Charles L. Hoppel
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Charles L. Hoppelbiology Degrees
Biology
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Neuroscience
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Biochemistry
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Biology
Charles L. Hoppel's Degrees
- PhD Biochemistry University of California, San Diego
- Bachelors Chemistry University of California, San Diego
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(Suggest an Edit or Addition)Charles L. Hoppel's Published Works
Number of citations in a given year to any of this author's works
Total number of citations to an author for the works they published in a given year. This highlights publication of the most important work(s) by the author
Published Works
- Production of Reactive Oxygen Species by Mitochondria (2003) (1116)
- Biochemical properties of subsarcolemmal and interfibrillar mitochondria isolated from rat cardiac muscle. (1977) (798)
- Fatty acid import into mitochondria. (2000) (717)
- Effect of high-dose ibuprofen in patients with cystic fibrosis. (1995) (710)
- Mitochondrial dysfunction in cardiac disease: ischemia--reperfusion, aging, and heart failure. (2001) (702)
- Plasma acylcarnitine profiles suggest incomplete long-chain fatty acid beta-oxidation and altered tricarboxylic acid cycle activity in type 2 diabetic African-American women. (2009) (517)
- The Failing Heart Relies on Ketone Bodies as a Fuel (2016) (456)
- Direct Inhibition of Mitochondrial Respiratory Chain Complex III by Cell-permeable Ceramide* (1997) (438)
- Carnitine: a nutritional, biosynthetic, and functional perspective. (2004) (403)
- Plasma Metabolomic Profiles Reflective of Glucose Homeostasis in Non-Diabetic and Type 2 Diabetic Obese African-American Women (2010) (383)
- Cardiac mitochondria in heart failure: decrease in respirasomes and oxidative phosphorylation (2008) (352)
- Ischemic defects in the electron transport chain increase the production of reactive oxygen species from isolated rat heart mitochondria. (2008) (289)
- Carnitine metabolism in the fasting rat. (1978) (270)
- A mitochondrial enzyme degrades carotenoids and protects against oxidative stress (2011) (270)
- Modulation of electron transport protects cardiac mitochondria and decreases myocardial injury during ischemia and reperfusion. (2007) (267)
- Aging selectively decreases oxidative capacity in rat heart interfibrillar mitochondria. (1999) (252)
- The role of carnitine in normal and altered fatty acid metabolism. (2003) (245)
- Parkinson’s disease-associated mutant VPS35 causes mitochondrial dysfunction by recycling DLP1 complexes (2015) (243)
- Mitochondrial Dysfunction and Myocardial Ischemia-Reperfusion: Implications for Novel Therapies. (2017) (241)
- Myocardial ischemia decreases oxidative phosphorylation through cytochrome oxidase in subsarcolemmal mitochondria. (1997) (229)
- Urinary Excretion of l-Carnitine and Acylcarnitines by Patients with Disorders of Organic Acid Metabolism: Evidence for Secondary Insufficiency of l-Carnitine (1984) (225)
- HIF drives lipid deposition and cancer in ccRCC via repression of fatty acid metabolism (2017) (224)
- Involvement of All-trans-retinal in Acute Light-induced Retinopathy of Mice* (2009) (222)
- Mitochondria in heart failure. (2010) (221)
- Riboflavin and rat hepatic cell structure and function. Mitochondrial oxidative metabolism in deficiency states. (1979) (213)
- Blockade of Electron Transport during Ischemia Protects Cardiac Mitochondria* (2004) (211)
- Reversible Blockade of Electron Transport during Ischemia Protects Mitochondria and Decreases Myocardial Injury following Reperfusion (2006) (199)
- Mitochondrial Metabolism in Aging Heart. (2016) (199)
- Mitochondria in cardiac hypertrophy and heart failure. (2013) (196)
- Myocardial ischemia selectively depletes cardiolipin in rabbit heart subsarcolemmal mitochondria. (2001) (187)
- Bupivacaine Inhibits Acylcarnitine Exchange in Cardiac Mitochondria (2000) (184)
- Mitochondrial dysfunction in heart failure (2013) (183)
- Missense mutations in the BCS1L gene as a cause of the Björnstad syndrome. (2007) (182)
- Mitochondrial Carnitine Palmitoyltransferase 1a (CPT1a) Is Part of an Outer Membrane Fatty Acid Transfer Complex* (2011) (180)
- Improvements in lipoatrophy, mitochondrial DNA levels and fat apoptosis after replacing stavudine with abacavir or zidovudine (2005) (180)
- Decreased activities of ubiquinol:ferricytochrome c oxidoreductase (complex III) and ferrocytochrome c:oxygen oxidoreductase (complex IV) in liver mitochondria from rats with hydroxycobalamin[c-lactam]-induced methylmalonic aciduria. (1991) (175)
- Carnitine palmityltransferase. Location of two enzymatic activities in rat liver mitochondria. (1972) (168)
- Oxidative phosphorylation and aging (2006) (166)
- Aging decreases electron transport complex III activity in heart interfibrillar mitochondria by alteration of the cytochrome c binding site. (2001) (163)
- Ischemic injury to mitochondrial electron transport in the aging heart: damage to the iron-sulfur protein subunit of electron transport complex III. (2001) (161)
- Mitochondrial Expression and Function of GAS-1 in Caenorhabditis elegans (2001) (158)
- Deficiency of the reduced nicotinamide adenine dinucleotide dehydrogenase component of complex I of mitochondrial electron transport. Fatal infantile lactic acidosis and hypermetabolism with skeletal-cardiac myopathy and encephalopathy. (1987) (158)
- Dynamic organization of mitochondria in human heart and in myocardial disease. (2009) (153)
- Oxidation of Fatty Acids Is the Source of Increased Mitochondrial Reactive Oxygen Species Production in Kidney Cortical Tubules in Early Diabetes (2012) (152)
- Structural differences in two biochemically defined populations of cardiac mitochondria. (2005) (145)
- Relationship between acid-soluble carnitine and coenzyme A pools in vivo. (1980) (143)
- O6-benzylguanine: a clinical trial establishing the biochemical modulatory dose in tumor tissue for alkyltransferase-directed DNA repair. (1999) (139)
- Blockade of Electron Transport before Cardiac Ischemia with the Reversible Inhibitor Amobarbital Protects Rat Heart Mitochondria (2006) (137)
- Biochemical differences between subsarcolemmal and interfibrillar mitochondria from rat cardiac muscle: effects of procedural manipulations. (1985) (134)
- L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia. (1984) (133)
- Moderate severity heart failure does not involve a downregulation of myocardial fatty acid oxidation. (2004) (132)
- Development and evaluation of a spectrophotometric assay for complex III in isolated mitochondria, tissues and fibroblasts from rats and humans. (1994) (131)
- Mitochondrial defects and anesthetic sensitivity. (2002) (130)
- Ischemia-reperfusion injury in the aged heart: role of mitochondria. (2003) (127)
- Quantitative H2S-mediated protein sulfhydration reveals metabolic reprogramming during the integrated stress response (2015) (125)
- Mitochondrial long chain fatty acid beta-oxidation in man and mouse. (2009) (123)
- Ischemia, rather than reperfusion, inhibits respiration through cytochrome oxidase in the isolated, perfused rabbit heart: role of cardiolipin. (2004) (122)
- Hamster cardiomyopathy. A defect in oxidative phosphorylation in the cardiac interfibrillar mitochondria. (1982) (117)
- Mutations in the MPV17 gene are responsible for rapidly progressive liver failure in infancy (2007) (117)
- Genetic disorders of carnitine metabolism and their nutritional management. (1998) (117)
- Aging defect at the QO site of complex III augments oxyradical production in rat heart interfibrillar mitochondria. (2003) (116)
- Metabolic response to carnitine in methylmalonic aciduria. An effective strategy for elimination of propionyl groups. (1983) (116)
- Skeletal muscle mitochondrial DNA injury in patients with unilateral peripheral arterial disease. (1999) (115)
- Heterogeneous response of subsarcolemmal heart mitochondria to calcium. (1986) (113)
- Urinary acylcarnitines are altered in human kidney cancer (2012) (113)
- Mitochondrial Oxidative Phosphorylation Is Defective in the Long-lived Mutant clk-1* (2004) (110)
- Aging skeletal muscle mitochondria in the rat: decreased uncoupling protein-3 content. (2001) (109)
- Carnitine metabolism in normal-weight and obese human subjects during fasting. (1980) (107)
- A Rostrocaudal Muscular Dystrophy Caused by a Defect in Choline Kinase Beta, the First Enzyme in Phosphatidylcholine Biosynthesis* (2006) (104)
- Kruppel-like Factor 15 Is a Critical Regulator of Cardiac Lipid Metabolism* (2014) (104)
- Kruppel-like factor 15 regulates skeletal muscle lipid flux and exercise adaptation (2012) (103)
- Ibuprofen in children with cystic fibrosis: pharmacokinetics and adverse effects. (1991) (101)
- Fumarase deficiency: a new cause of mitochondrial encephalomyopathy. (1986) (100)
- Development of β-Lapachone Prodrugs for Therapy Against Human Cancer Cells with Elevated NAD(P)H:Quinone Oxidoreductase 1 Levels (2005) (98)
- Homozygous carnitine palmitoyltransferase 1b (muscle isoform) deficiency is lethal in the mouse. (2005) (97)
- What is the functional significance of the unique location of glutaredoxin 1 (GRx1) in the intermembrane space of mitochondria? (2007) (93)
- Separation and quantitation of phospholipids and lysophospholipids by high-performance liquid chromatography. (2000) (92)
- Hyperammonaemia‐induced skeletal muscle mitochondrial dysfunction results in cataplerosis and oxidative stress (2016) (92)
- Sterol Regulatory Element-binding Protein-1 (SREBP-1) Is Required to Regulate Glycogen Synthesis and Gluconeogenic Gene Expression in Mouse Liver* (2014) (91)
- Leucine and Protein Metabolism in Obese Zucker Rats (2013) (88)
- Elevated hepatic mitochondrial and peroxisomal oxidative capacities in fed and starved adult obese (ob/ob) mice. (1985) (87)
- Studies on Giant Mitochondria (1986) (87)
- Inhibition of mitochondrial respiration by analogs of 4-phenylpyridine and 1-methyl-4-phenylpyridinium cation (MPP+), the neurotoxic metabolite of MPTP. (1987) (84)
- Effect of Ibuprofen on Neutrophil Migration in Vivo in Cystic Fibrosis and Healthy Subjects (2003) (84)
- Effect of intravenous L‐carnitine on carnitine homeostasis and fuel metabolism during exercise in humans (1994) (83)
- Effect of Maternal Obesity on Placental Lipid Metabolism (2017) (83)
- Lethal neonatal deficiency of carnitine palmitoyltransferase II associated with dysgenesis of the brain and kidneys. (1995) (83)
- Preservation of cardiolipin content during aging in rat heart interfibrillar mitochondria. (2002) (82)
- Cardiolipin as an oxidative target in cardiac mitochondria in the aged rat. (2008) (82)
- Improved Mitochondrial Function with Diet-Induced Increase in Either Docosahexaenoic Acid or Arachidonic Acid in Membrane Phospholipids (2012) (81)
- Mitochondria in the human heart (2009) (81)
- Mitochondria in the elderly: Is acetylcarnitine a rejuvenator? (2009) (80)
- Evidence for compartmentalization of mammalian carotenoid metabolism (2014) (79)
- Cardiac mitochondria in heart failure: normal cardiolipin profile and increased threonine phosphorylation of complex IV. (2011) (79)
- Kruppel-like factor 4 is critical for transcriptional control of cardiac mitochondrial homeostasis. (2015) (79)
- Biosynthesis of carnitine and 4-N-trimethylaminobutyrate from 6-N-trimethyl-lysine. (1973) (77)
- Novel isolation procedure for short-, medium-, and long-chain acyl-coenzyme A esters from tissue. (2008) (77)
- Decreased NADH dehydrogenase and ubiquinol-cytochrome c oxidoreductase in peripheral arterial disease. (2001) (76)
- Oxidative phosphorylation analysis: assessing the integrated functional activity of human skeletal muscle mitochondria--case studies. (2004) (75)
- Systemic Deficiency of the First Component of the Pyruvate Dehydrogenase Complex (1987) (75)
- Secondary carnitine insufficiency in disorders of organic acid metabolism: modulation of acyl-CoA/CoA ratios by l-carnitine in vivo (1983) (73)
- The Malonyl-CoA-sensitive Form of Carnitine Palmitoyltransferase Is Not Localized Exclusively in the Outer Membrane of Rat Liver Mitochondria* (1998) (73)
- Peroxisomal Fatty Acid Oxidation Is a Substantial Source of the Acetyl Moiety of Malonyl-CoA in Rat Heart* (2004) (72)
- Plasma and Urine Carnitine in Diabetic Ketosis (1979) (72)
- DIVISION OF GIANT MITOCHONDRIA DURING RECOVERY FROM CUPRIZONE INTOXICATION (1973) (71)
- Post-translational modifications of rat liver mitochondrial outer membrane proteins identified by mass spectrometry. (2007) (70)
- Quantification of carnitine and acylcarnitines in biological matrices by HPLC electrospray ionization-mass spectrometry. (2008) (69)
- Carnitine palmitoyltransferase in bovine fetal heart mitochondria. (1975) (68)
- Separation and characterization of cardiolipin molecular species by reverse-phase ion pair high-performance liquid chromatography-mass spectrometry1 (2010) (67)
- VDAC proteomics: post-translation modifications. (2012) (66)
- High-fat diet postinfarction enhances mitochondrial function and does not exacerbate left ventricular dysfunction. (2007) (66)
- Partial deficiency of muscle carnitine palmitoyltransferase with normal ketone production. (1978) (65)
- Reversal of mitochondrial defects before ischemia protects the aged heart (2006) (65)
- Characterization of D-3-hydroxybutyrylcarnitine (ketocarnitine): an identified ketosis-induced metabolite. (2012) (64)
- Phosphorylation of Rat Liver Mitochondrial Carnitine Palmitoyltransferase-I (2004) (64)
- Cardiolipin: characterization of distinct oxidized molecular species (2011) (63)
- Interfibrillar cardiac mitochondrial comples III defects in the aging rat heart (2004) (62)
- Glutaredoxin regulates apoptosis in cardiomyocytes via NFkappaB targets Bcl-2 and Bcl-xL: implications for cardiac aging. (2010) (60)
- Relationship between serum carnitine, acylcarnitines, and renal function in patients with chronic renal disease. (2006) (60)
- Homozygous carnitine palmitoyltransferase 1a (liver isoform) deficiency is lethal in the mouse. (2005) (60)
- Enhanced modification of cardiolipin during ischemia in the aged heart. (2009) (60)
- Hepatic mitochondrial function in ketogenic states. Diabetes, starvation, and after growth hormone administration. (1975) (59)
- Biosynthesis of carnitine and 4-N-trimethylaminobutyrate from lysine. (1973) (58)
- Proteomics of mitochondrial inner and outer membranes (2008) (56)
- Autosomal dominant acute necrotizing encephalopathy (2003) (55)
- Carnitine and trimethylaminobutyrate synthesis in rat tissues. (1974) (55)
- Quantification of free carnitine, individual short- and medium-chain acylcarnitines, and total carnitine in plasma by high-performance liquid chromatography. (1993) (53)
- New aspects of impaired mitochondrial function in heart failure (2009) (53)
- ATAD3A oligomerization causes neurodegeneration by coupling mitochondrial fragmentation and bioenergetics defects (2019) (51)
- Fatty acid oxidation in cardiac and skeletal muscle mitochondria is unaffected by deletion of CD36. (2007) (50)
- Prolonged exposure to high dietary lipids is not associated with lipotoxicity in heart failure. (2009) (50)
- Peroxisomal and Mitochondrial Oxidation of Fatty Acids in the Heart, Assessed from the 13C Labeling of Malonyl-CoA and the Acetyl Moiety of Citrate* (2005) (50)
- Elevated Plasma Carnitine in Hepatic Cirrhosis (2007) (49)
- A targeted proteomic approach for the analysis of rat liver mitochondrial outer membrane proteins with extensive sequence coverage. (2006) (49)
- Quantification of carnitine, acetylcarnitine, and total carnitine in tissues by high-performance liquid chromatography: the effect of exercise on carnitine homeostasis in man. (1995) (48)
- Inflammatory Breast Cancer as a Model Disease to Study Tumor Angiogenesis: Results of a Phase IB Trial of Combination SU5416 and Doxorubicin (2007) (47)
- Strategy for the isolation, derivatization, chromatographic separation, and detection of carnitine and acylcarnitines. (2005) (47)
- Assessing the Reversibility of the Anaplerotic Reactions of the Propionyl-CoA Pathway in Heart and Liver* (2003) (47)
- Decreased cytochrome c mediates an age-related decline of oxidative phosphorylation in rat kidney mitochondria. (2010) (47)
- Derivatization of carboxylic acids by reaction with 4'-bromophenacyl trifluoromethanesulfonate prior to determination by high-performance liquid chromatography. (1984) (46)
- Mitochondrial dysfunction in heart failure: potential for therapeutic interventions? (2000) (46)
- Measuring oxidative phosphorylation in human skin fibroblasts. (2013) (46)
- Enhanced acyl-CoA dehydrogenase activity is associated with improved mitochondrial and contractile function in heart failure. (2008) (45)
- Method for isolation of non-esterified fatty acids and several other classes of plasma lipids by column chromatography on silica gel. (1993) (45)
- Quantification of malonyl-coenzyme A in tissue specimens by high-performance liquid chromatography/mass spectrometry. (2006) (45)
- Diabetes or peroxisome proliferator-activated receptor alpha agonist increases mitochondrial thioesterase I activity in heart. (2007) (45)
- A phase IB clinical and pharmacokinetic study of the angiogenesis inhibitor SU5416 and paclitaxel in recurrent or metastatic carcinoma of the head and neck (2005) (44)
- Plasma levels and renal excretion of phenytoin and its metabolites in patients with renal failure (1979) (44)
- Impact on carnitine homeostasis of short‐term treatment with the pivalate prodrug cefditoren pivoxil (2003) (44)
- Possible division of cardiac mitochondria (1972) (43)
- Structure of cristae in cardiac mitochondria of aged rat (2006) (43)
- Mitochondrial respiratory chain complex I deficiency with clinical and biochemical features of long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency. (2000) (43)
- Decrease in mitochondrial function in rat cardiac permeabilized fibers correlates with the aging phenotype. (2010) (42)
- Oxidative stress mediates ethanol-induced skeletal muscle mitochondrial dysfunction and dysregulated protein synthesis and autophagy. (2019) (42)
- Functional redundancy of mitochondrial enoyl‐CoA isomerases in the oxidation of unsaturated fatty acids (2012) (41)
- Mitochondrial Division in Rat Cardiomyocytes: An Electron Microscope Study (2011) (41)
- Biochemical effects of cuprizone on mouse liver and heart mitochondria. (1973) (41)
- Multiple-dose pharmacokinetics and bioequivalence of L-carnitine 330-mg tablet versus 1-g chewable tablet versus enteral solution in healthy adult male volunteers. (1995) (40)
- Inter-tissue relationships in the synthesis and distribution of carnitine. (1986) (40)
- Comprehensive approach to the quantitative analysis of mitochondrial phospholipids by HPLC-MS. (2013) (40)
- Probing peroxisomal β-oxidation and the labelling of acetyl-CoA proxies with [1-13C]octanoate and [3-13C]octanoate in the perfused rat liver (2005) (40)
- Dopaminergic Neurotoxicity In Vivo and Inhibition of Mitochondrial Respiration In Vitro by Possible Endogenous Pyridinium‐Like Substances (1991) (40)
- Carnitine biosynthesis. Hydroxylation of N6-trimethyl-lysine to 3-hydroxy-N6-trimethyl-lysine. (1980) (40)
- Furosemide kinetics in patients with hepatic cirrhosis with ascites (1981) (40)
- Altered expression of the adenine nucleotide translocase isoforms and decreased ATP synthase activity in skeletal muscle mitochondria in heart failure. (2009) (39)
- Acylcarnitines as markers of exercise‐associated fuel partitioning, xenometabolism, and potential signals to muscle afferent neurons (2017) (38)
- Improved Metabolic Health Alters Host Metabolism in Parallel with Changes in Systemic Xeno-Metabolites of Gut Origin (2014) (38)
- Effect of starvation on the disposition of free and peptide-linked trimethyllysine in the rat. (1986) (38)
- Validated method for the quantification of free and total carnitine, butyrobetaine, and acylcarnitines in biological samples. (2015) (38)
- A phase II and pharmacokinetic study of weekly 72-h topotecan infusion in patients with platinum-resistant and paclitaxel-resistant ovarian carcinoma. (2000) (38)
- Mitofusin 2 Regulates Axonal Transport of Calpastatin to Prevent Neuromuscular Synaptic Elimination in Skeletal Muscles. (2018) (38)
- Giant Mitochondria in a Cardiomyopathic Heart (2002) (37)
- Increased Mitochondrial Oxidative Phosphorylation in the Liver Is Associated With Obesity and Insulin Resistance (2011) (37)
- Carnitine and carnitine palmitoyltransferase in fatty acid oxidation and ketosis. (1982) (37)
- Hepatic mitochondrial inner membrane properties and carnitine palmitoyltransferase A and B. Effect of diabetes and starvation. (1985) (37)
- Quantitative assessment of anaplerosis from propionate in pig heart in vivo. (2003) (37)
- Urinary excretion of acetylcarnitine during human diabetic and fasting ketosis. (1982) (36)
- L-Carnitine insufficiency in disorders of organic acid metabolism: response to L-carnitine by patients with methylmalonic aciduria and 3-hydroxy-3-methylglutaric aciduria. (1984) (36)
- Pc 4 photodynamic therapy of U87‐derived human glioma in the nude rat (2005) (35)
- Quantitative acylcarnitine determination by UHPLC-MS/MS--Going beyond tandem MS acylcarnitine "profiles". (2015) (34)
- Phase I clinical and pharmacokinetic study of rebeccamycin analog NSC 655649 given daily for five consecutive days. (2001) (34)
- Riboflavin and mouse hepatic cell structure and function. Mitochondrial oxidative metabolism in severe deficiency states. (1975) (34)
- Parkinson's disease-associated pathogenic VPS35 mutation causes complex I deficits. (2017) (33)
- Isolation of hepatic mitochondrial contact sites: previously unrecognized inner membrane components. (2002) (33)
- Quantification of carnitine and specific acylcarnitines by high-performance liquid chromatography: application to normal human urine and urine from patients with methylmalonic aciduria, isovaleric acidemia or medium-chain acyl-CoA dehydrogenase deficiency. (1993) (33)
- Neurofibromin colocalizes with mitochondria in cultured cells. (1997) (33)
- Incomplete fatty acid oxidation. The production and epimerization of 3-hydroxy fatty acids. (1992) (32)
- Radiochemical malonyl-CoA decarboxylase assay: activity and subcellular distribution in heart and skeletal muscle. (2002) (32)
- Lethal neonatal case and review of primary short-chain enoyl-CoA hydratase (SCEH) deficiency associated with secondary lymphocyte pyruvate dehydrogenase complex (PDC) deficiency. (2017) (32)
- Mitochondrial Dysfunction in Cardiovascular Aging. (2017) (32)
- Aging-dependent changes in rat heart mitochondrial glutaredoxins—Implications for redox regulation☆ (2013) (31)
- Rat liver mitochondrial contact sites and carnitine palmitoyltransferase-I. (2001) (31)
- Mutations in the mitochondrial ribosomal protein MRPS22 lead to primary ovarian insufficiency (2018) (31)
- BAM15‐mediated mitochondrial uncoupling protects against obesity and improves glycemic control (2020) (31)
- Carnitine Palmitoyltransferase and Transport of Fatty Acids (1976) (30)
- Acute hormonal effects on carnitine metabolism in thin and obese subjects: responses to somatostatin, glucagon, and insulin. (1981) (30)
- Plasma concentrations of 5‐(4‐hydroxyphenyl)‐5‐phenylhydantoin in phenytoin‐treated patients (1977) (30)
- Effect of carnitine on mitochondrial oxidation of palmitoylearnitine. (1980) (29)
- A mutation in mitochondrial complex I increases ethanol sensitivity in Caenorhabditis elegans. (2003) (29)
- Mass fragmentographic determination of diphenylhydantoin and its main metabolite, 5-(4-hydroxyphenyl)-5-phenylhydantoin, in human plasma. (1976) (29)
- Determination of carnitine, butyrobetaine, and betaine as 4'-bromophenacyl ester derivatives by high-performance liquid chromatography. (1984) (29)
- Quantitation of long-chain acylcarnitines by HPLC/fluorescence detection: application to plasma and tissue specimens from patients with carnitine palmitoyltransferase-II deficiency. (2005) (28)
- Combined partial deficiency of muscle carnitine palmitoyltransferase and carnitine with autosomal dominant inheritance. (1980) (28)
- N6-Trimethyl-lysine metabolism. 3-Hydroxy-N6-trimethyl-lysine and carnitine biosynthesis. (1980) (27)
- Phase I study of the EGFR tyrosine kinase inhibitor erlotinib in combination with docetaxel and radiation in locally advanced squamous cell cancer of the head and neck (SCCHN). (2006) (27)
- Mitochondrial Dysfunction in a Patient with Crohn Disease: Possible Role in Pathogenesis (2004) (27)
- A novel mutation in the mitochondrial tRNASer(AGY) gene associated with mitochondrial myopathy, encephalopathy, and complex I deficiency (2006) (27)
- Tetraphenylborate potentiates the respiratory inhibition by the dopaminergic neurotoxin MPP+ in both electron transport particles and intact mitochondria. (1989) (27)
- Partial muscle carnitine palmitoyltransferase-A deficiency. Rhabdomyolysis associated with transiently decreased muscle carnitine content after ibuprofen therapy. (1987) (26)
- Defects in skeletal muscle subsarcolemmal mitochondria in a non-obese model of type 2 diabetes mellitus (2017) (26)
- Phase II and pharmacokinetic/pharmacodynamic trial of sequential topoisomerase I and II inhibition with topotecan and etoposide in advanced non-small-cell lung cancer (2000) (26)
- A 22 kDa polyanion inhibits carnitine‐dependent fatty acid oxidation in rat liver mitochondria (1999) (25)
- A Phase I and Pharmacodynamic Study of Fludarabine, Carboplatin, and Topotecan in Patients With Relapsed, Refractory, or High-Risk Acute Leukemia (2004) (25)
- Preliminary Clinical and Pharmacologic Investigation of Photodynamic Therapy with the Silicon Phthalocyanine Photosensitizer Pc 4 for Primary or Metastatic Cutaneous Cancers (2011) (25)
- Fatty Acid Chain Elongation in Palmitate-perfused Working Rat Heart (2014) (25)
- Urinary 3-hydroxydicarboxylic acids in pathophysiology of metabolic disorders with dicarboxylic aciduria. (1991) (25)
- Determination of plasma non-esterified fatty acids and triglyceride fatty acids by gas chromatography of their methyl esters after isolation by column chromatography on silica gel. (1995) (25)
- Management of 3-aminopyridine-2-carboxaldehyde thiosemicarbazone-induced methemoglobinemia. (2012) (24)
- A phase I trial of radiotherapy and simultaneous 24-hour paclitaxel in patients with locally advanced head and neck squamous cell carcinoma. (1997) (24)
- Pharmacologic action of L-carnitine on hypertriglyceridemia in obese Zucker rats. (1986) (24)
- Acyl-CoA dehydrogenase activity in the riboflavin-deficient rat. Effects of starvation. (1987) (24)
- Synthesis of radioactively methyl-labelled (l)-carnitine (1982) (23)
- Enhanced resistance to permeability transition in interfibrillar cardiac mitochondria in dogs: effects of aging and long-term aldosterone infusion. (2013) (23)
- Analyzing mitochondrial function in human peripheral blood mononuclear cells. (2018) (23)
- Lipids activate skeletal muscle mitochondrial fission and quality control networks to induce insulin resistance in humans. (2021) (23)
- An enzymatic method for the determination of butyrobetaine via conversion to carnitine after isolation by high performance liquid chromatography. (1988) (23)
- cis-3,4-Methylene-heptanoylcarnitine: characterization and verification of the C8:1 acylcarnitine in human urine. (2007) (23)
- Exercise plasma metabolomics and xenometabolomics in obese, sedentary, insulin-resistant women: impact of a fitness and weight loss intervention. (2019) (23)
- Long-term L-carnitine treatment in isovaleric acidemia. (1991) (22)
- Hepatic mitochondrial function in lean and obese Zucker rats. (1983) (22)
- A radiochemical pyruvate dehydrogenase assay: activity in heart. (2003) (22)
- Decreased carnitine biosynthesis in rats with secondary biliary cirrhosis (2000) (21)
- Quality improvement of mitochondrial respiratory chain complex enzyme assays using Caenorhabditis elegans (2011) (21)
- Acetyl-l-carnitine increases mitochondrial protein acetylation in the aged rat heart (2015) (21)
- Spiropentaneacetic acid as a specific inhibitor of medium-chain acyl-CoA dehydrogenase. (1991) (20)
- Determination of free carnitine and 'total' carnitine in human urine: derivatization with 4'-bromophenacyl trifluoromethanesulfonate and high performance liquid chromatography. (1992) (20)
- Effect of starvation in the rat on trimethyllysine in peptide linkage. (1983) (20)
- Ultrastructural effects of riboflavin deficiency on rat hepatic mitochondria (1980) (20)
- Abnormal fatty acid utilization during prolonged fasting in chronic uremia. (1987) (20)
- Cited2, a Transcriptional Modulator Protein, Regulates Metabolism in Murine Embryonic Stem Cells* (2013) (19)
- High-performance liquid chromatographic separation of acylcarnitines following derivatization with 4′-bromophenacyl trifluromethanesulfonate (1990) (19)
- Design and implementation of the first randomized controlled trial of coenzyme CoQ₁₀ in children with primary mitochondrial diseases. (2012) (19)
- Probing peroxisomal beta-oxidation and the labelling of acetyl-CoA proxies with [1-(13C)]octanoate and [3-(13C)]octanoate in the perfused rat liver. (2005) (19)
- Inhibition of mitochondrial respiration by analogues of the dopaminergic neurotoxin 1-methyl-4-phenylpyridinium: structural requirements for accumulation-dependent enhanced inhibitory potency on intact mitochondria. (1990) (19)
- Succinyl-CoA synthetase (SUCLA2) deficiency in two siblings with impaired activity of other mitochondrial oxidative enzymes in skeletal muscle without mitochondrial DNA depletion. (2017) (19)
- Morphological Pathways of Mitochondrial Division (2018) (18)
- Butyrobetaine availability in liver is a regulatory factor for carnitine biosynthesis in rat. Flux through butyrobetaine hydroxylase in fasting state. (1989) (18)
- Pharmacokinetics of O6‐Benzylguanine (NSC637037) and Its Metabolite, 8‐Oxo‐O6‐Benzylguanine (2003) (18)
- Determination of ibuprofen in human plasma by high-performance liquid chromatography. (1988) (18)
- Abnormal urinary excretion of unsaturated dicarboxylic acids in patients with medium-chain acyl-CoA dehydrogenase deficiency. (1990) (18)
- Novel ETF dehydrogenase mutations in a patient with mild glutaric aciduria type II and complex II-III deficiency in liver and muscle (2010) (18)
- Ultrastructural effects of dietary galactoflavin on mouse hepatocytes. (1974) (17)
- Post-translational modifications of mitochondrial outer membrane proteins. (2009) (17)
- CARNITINE AND CARNITINE PALMITOYLTRANSFERASE IN METABOLIC STUDIES1 (1980) (17)
- Plasma carnitine in alcoholism. (1988) (17)
- Determination of free trimethyllysine in plasma and tissue specimens by high-performance liquid chromatography. (1984) (17)
- Investigating the link of ACAD10 deficiency to type 2 diabetes mellitus (2018) (17)
- Metabolic Studies of Carnitine in a Child with Propionic Acidemia (1989) (16)
- Altered carnitine metabolism in dialysis patients with reduced physical function may be due to dysfunctional fatty acid oxidation. (2012) (16)
- Decreased Cytochrome c Oxidase Subunit VIIa in Aged Rat Heart Mitochondria: Immunocytochemistry (2011) (16)
- Isolation of mitochondrial subpopulations from skeletal muscle: Optimizing recovery and preserving integrity (2018) (16)
- Carnitine biosynthesis in rat liver slices. (1974) (16)
- Operating Room Scheduling by Computer (1977) (16)
- Atypical urinary opiate excretion pattern. (1997) (16)
- Determination of ibuprofen and its major metabolites in human urine by high-performance liquid chromatography. (1988) (15)
- Effect of diet and starvation on hepatic mitochondrial function in the rat. (1983) (15)
- A phase I pharmacokinetic and pharmacodynamic study of SU5416 and Adriamycin in inflammatory breast cancer (2001) (15)
- Post-translational modifications of mitochondrial outer membrane proteins (2011) (14)
- Selective and accurate C5 acylcarnitine quantitation by UHPLC-MS/MS: Distinguishing true isovaleric acidemia from pivalate derived interference. (2017) (14)
- Successful long-term treatment of hepatic carnitine palmitoyltransferase I deficiency and a novel mutation (2004) (14)
- Determination of total carnitine in human urine by high-performance liquid chromatography. (1987) (14)
- Comparison of L-carnitine pharmacokinetics with and without baseline correction following administration of single 20-mg/kg intravenous dose. (1995) (14)
- Carnitine deficiency associated with ornithine transcarbamylase deficiency. (1991) (14)
- Competition between acetate and oleate for the formation of malonyl-CoA and mitochondrial acetyl-CoA in the perfused rat heart. (2006) (14)
- Hepatic peroxisomal and mitochondrial fatty acid oxidation in the riboflavin-deficient rat. (1985) (13)
- Determination of ibuprofen in human plasma by high-performance liquid chromatography. (1984) (13)
- Subsurface cisterns in mouse hepatocytes (1974) (13)
- Hepatic mitochondrial inner-membrane properties, beta-oxidation and carnitine palmitoyltransferases A and B. Effects of genetic obesity and starvation. (1986) (13)
- Carnitine metabolism in lean and obese Zucker rats during starvation. (1986) (12)
- Derivatization of isolated endogenous butyrobetaine with 4'-bromophenacyl trifluoromethanesulfonate followed by high-performance liquid chromatography. (1992) (12)
- Urinary 3-hydroxyadipic acid 3,6-lactone: structural identification and effect of fasting in adults and children. (1989) (12)
- A phase I and pharmacodynamic study of sequential topotecan and etoposide in patients with relapsed or refractory acute myelogenous and lymphoblastic leukemia. (2003) (12)
- Disassociation between acidinsoluble acylcarnitines and ketogenesis following carnitine administration in vivo. (1978) (11)
- Peroxisomal palmitoyl-CoA oxidation in the Zucker rat. (1983) (11)
- Peroxisome Proliferator-activated Receptor γ (PPARγ) Mediates a Ski Oncogene-induced Shift from Glycolysis to Oxidative Energy Metabolism*♦ (2011) (11)
- Monolysocardiolipin: improved preparation with high yield (2011) (11)
- Phase I clinical and pharmacokinetic study of oxaliplatin, irinotecan and capecitabine (2009) (11)
- The M405V allele of the glutaryl-CoA dehydrogenase gene is an important marker for glutaric aciduria type I (GA-I) low excretors. (2016) (10)
- In vivo studies of carnitine and fatty acid metabolism: problems with use of anesthetics. (1981) (10)
- Isolation and identification of two isomeric forms of malonyl-coenzyme A in commercial malonyl-coenzyme A. (2004) (10)
- Inhibition of mitochondrial respiration by neutral, monocationic, and dicationic bis-pyridines related to the dopaminergic neurotoxin 1-methyl-4-phenylpyridinium cation (MPP+). (1991) (10)
- N6-Trimethyl-lysine metabolism. Structural identification of the metabolite 3-hydroxy-N6-trimethyl-lysine. (1980) (10)
- Cardiac mitochondrial structure and function in tafazzin-knockdown mice. (2018) (10)
- Phase II and pharmacokinetic trial of rebeccamycin analog in advanced biliary cancers (2009) (10)
- Blocked O-GlcNAc cycling alters mitochondrial morphology, function, and mass (2021) (10)
- Separation of acylcarnitines from biological samples using high-performance liquid chromatography. (1986) (9)
- Relationships between expression of BCS1L, mitochondrial bioenergetics, and fatigue among patients with prostate cancer (2019) (9)
- Improved high-performance liquid chromatographic method for the determination of 6-N,N,N-trimethyllysine in plasma and urine: biomedical application of chromatographic figures of merit and amine mobile phase modifiers. (1986) (9)
- Simultaneous determination of O6-benzylguanine and 8-oxo-O6-benzylguanine in human plasma by reversed-phase high-performance liquid chromatography. (1997) (9)
- Association between Mitochondrial Bioenergetics and Radiation- Related Fatigue: A Possible Mechanism and Novel Target (2015) (9)
- Integrated mitochondrial function and cancer-related fatigue in men with prostate cancer undergoing radiation therapy (2018) (9)
- Kinetics of placentally transferred phenytoin and its p-hydroxylated metabolites in newborn infants. (1979) (9)
- Relationship between hepatic mitochondrial oxidative metabolism and morphology during riboflavin deficiency and recovery in mice. (1976) (8)
- Fatty acid chain‐elongation in perfused rat heart: Synthesis of stearoylcarnitine from perfused palmitate (2007) (8)
- Metabolic reprogramming during hyperammonemia targets mitochondrial function and postmitotic senescence (2021) (8)
- Partial muscle carnitine palmitoyltransferase-A deficiency (1987) (8)
- Rat liver mitochondrial carnitine palmitoyltransferase-I, hepatic carnitine, and malonyl-CoA: Effect of starvation (2008) (8)
- Carnitine Palmitoyltransferase-I and Regulation of Mitochondrial Fatty Acid Oxidation (2005) (8)
- Correcting false positive medium-chain acyl-CoA dehydrogenase deficiency results from newborn screening; synthesis, purification, and standardization of branched-chain C8 acylcarnitines for use in their selective and accurate absolute quantitation by UHPLC-MS/MS. (2017) (8)
- Exercise training and diet-induced weight loss increase markers of hepatic bile acid (BA) synthesis and reduce serum total BA concentrations in obese women. (2021) (8)
- Bioenergetic functions in subpopulations of heart mitochondria are preserved in a non-obese type 2 diabetes rat model (Goto-Kakizaki) (2020) (8)
- Hypercarnitinemia in cirrhosis (1985) (8)
- Multiple Mitochondrial Alterations in a Case of Myopathy (2014) (8)
- Impact of a weight loss and fitness intervention on exercise‐associated plasma oxylipin patterns in obese, insulin‐resistant, sedentary women (2020) (7)
- Giant Mitochondria (Megamitochondria) (2013) (7)
- Ultrastructural and biochemical effects of D‐penicillamine on mouse hepatocytes (1980) (7)
- Determination of 6-N-trimethyllysine in urine by high-performance liquid chromatography. (1983) (7)
- DIABETES, STARVATION, AND AFTER GROWTH HORMONE ADMINISTRATION (1975) (7)
- Multiple Muscle Cell Alterations in a Case of Encephalomyopathy (2014) (7)
- Mass spectrometric demonstration of the presence of liver carnitine palmitoyltransferase-I (CPT-I) in heart mitochondria of adult rats. (2009) (7)
- The failure of supplemental dietary copper to prevent cuprizone-induced alterations in mouse hepatocytes. (1975) (7)
- Rapid high-performance liquid chromatography of 3-methylhistidine in human urine. (1987) (7)
- Megamitochondria in Cardiomyocytes of a Knockout (Klf15−/−) Mouse (2015) (6)
- Mitochondrial uncoupling attenuates sarcopenic obesity by enhancing skeletal muscle mitophagy and quality control (2022) (6)
- A novel null mutation in the pyruvate dehydrogenase phosphatase catalytic subunit gene (PDP1) causing pyruvate dehydrogenase complex deficiency (2019) (6)
- Determination of O6-benzylguanine in human plasma by reversed-phase high-performance liquid chromatography. (1996) (6)
- Discovery of a redox-thiol switch regulating cellular energy metabolism (2019) (5)
- Dynamin-related protein 1 regulates substrate oxidation in skeletal muscle by stabilizing cellular and mitochondrial calcium dynamics (2021) (5)
- Quinol type compound in cytochrome c preparations leads to non-enzymatic reduction of cytochrome c during the measurement of complex III activity. (2007) (5)
- Rat liver mitochondrial carnitine palmitoyltransferase-I, hepatic carnitine, and malonyl-CoA: effect of starvation. (2008) (5)
- High-performance liquid chromatographic separation of acylcarnitines following derivatization with 4'-bromophenacyl trifluoromethanesulfonate. (1990) (5)
- Plasma Citrate and Succinate Are Associated with Neurocognitive Impairment in Older People with HIV. (2021) (5)
- Mitochondrial electron transport and aging in the heart (2002) (5)
- 1143 METABOLIC EFFECTS OF TREATMENT OF SYSTEMIC CARNITINE DEFICIENCY (1981) (5)
- Anesthesia and bariatric surgery gut preparation alter plasma acylcarnitines reflective of mitochondrial fat and branched-chain amino acid oxidation. (2017) (4)
- Understanding physiologic phospholipid maintenance in the context of brain mitochondrial phospholipid alterations after cardiac arrest. (2021) (4)
- String mitochondria in mouse soleus muscle (2013) (4)
- Mitochondrial Utilization of Competing Fuels Is Altered in Insulin Resistant Skeletal Muscle of Non-obese Rats (Goto-Kakizaki) (2020) (4)
- Peroxisome-desmosome complexes in mouse hepatic cells (1970) (4)
- Isolation of rat adrenocortical mitochondria. (2012) (4)
- MITOCHONDRIA DYSFUNCTION IN CARDIAC DISEASE: ISCHEMIAREPERFUSION, AGING AND HEART FAILURE (2001) (4)
- Anesthetic Hypersensitivity in a Case-Controlled Series of Patients With Mitochondrial Disease (2021) (4)
- Synthesis of carboxy-labelled l-carnitine (1982) (4)
- Pharmacokinetic interaction between diltiazem and nortriptyline (1996) (4)
- Breast cancer growth and proliferation is suppressed by the mitochondrial targeted furazano[3,4-b]pyrazine BAM15 (2021) (4)
- Carnitine palmitoyltransferase activity in the rabbit choroid plexus: Its possible function in fatty acid metabolism and transport (1992) (3)
- Anaplerosis from heptanoate ‐a propionyl‐CoA precursor‐ in mouse brain (2007) (3)
- A Clinical Trial Establishing the Biochemical Modulatory Dose in Tumor Tissue for Alkyltransferase-directed DNA Repair 1 (1999) (3)
- Identification of unusual phospholipids from bovine heart mitochondria by HPLC-MS/MS (2020) (3)
- Identification of unusual phospholipids from bovine heart mitochondria by HPLC-MS/MS. (2020) (3)
- Reassessment of the mechanisms by which aminooxyacetate (AOA) inhibits gluconeogenesis (GNG) from lactate (2007) (3)
- Dosing Colistimethate Every 8 h Results in Higher Plasma Concentrations of Active Colistin Than Every 12-Hourly Dosing without Increase in Nephrotoxicity: A Phase 1 Pharmacokinetics Trial in Healthy Adult Volunteers (2022) (3)
- Diabetes or peroxisome proliferator-activated receptor α agonist increases mitochondrial thioesterase I activity in heart Published, JLR Papers in Press, April 16, 2007. (2007) (3)
- Synthesis and characterization of cis-4-decenoyl-CoA, 3-phenylpropionyl-CoA, and 2,6-dimethylheptanoyl-CoA. (2010) (3)
- Carnitine and β-Oxidation (2013) (3)
- Author response: Quantitative H2S-mediated protein sulfhydration reveals metabolic reprogramming during the integrated stress response (2015) (2)
- Is carnitine palmitoyltransferase I (CPT-I) exclusively in the mitochondrial outer membrane? (1997) (2)
- RIBOFLAVIN DEFICIENCY (1942) (2)
- MALIGNANT MELANOMA OF THE STOMACH (1965) (2)
- Comments on quantitation of carnitine esters by high performance liquid chromatography: Reply to E. Schmidt-Sommerfeld and D. Penn (1994) (2)
- Impaired mitochondrial oxidative metabolism in heart failure (2002) (2)
- Alterations of skeletal muscle bioenergetics in a mouse with F508del mutation leading to a cystic fibrosis-like condition. (2019) (2)
- Effect of theophylline on urinary excretion of 3-methylhistidine in patients with lung disease. (1991) (2)
- Quantification of acylcarnitines. (1985) (2)
- Rapid and sensitive method for the determination of salicylic acid in serum by reversed-phase ion-pair high-performance liquid chromatography. (1983) (2)
- Picolinyl ester fragmentation mechanism studies with application to the identification of acylcarnitine acyl groups following transesterification (2006) (2)
- Corrigendum to 'design and implementation of the first randomized controlled trial of coenzyme q10 in children with primary mitochondrial diseases' [Mitochondrion 12/6 (2012) 623-629] (2013) (1)
- Abstract 1296: Diabetes and Activation of Peroxisome Proliferator Activated Receptor {alpha} Increases Mitochondrial Thioesterase I Protein Expression and Activity in the Heart (2006) (1)
- Great Britain Carnitine Biosynthesis HYDROXYLATION OF N 6-TRIMETHYL-LYSINE TO 3-HYDROXY-N 6-TRIMETHYL-LYSINE (2005) (1)
- Pc 4 photodynamic therapy of U87 (human glioma) orthotopic tumor in nude rat brain (2005) (1)
- Reperfusion with preserved mitochondrial function decreases mitochondrial hydrogen peroxide production and infarct size (2006) (1)
- Time to harmonize mitochondrial syndrome nomenclature and classification: A consensus from the North American Mitochondrial Disease Consortium (NAMDC). (2022) (1)
- Carnitine palmitoyltransferase deficiency. (1990) (1)
- Phase I study of oxaliplatin (Ox), irinotecan (Irino), and capecitabine (Cape) in patients with solid tumors. (2004) (1)
- Erratum: Increased mitochondrial oxidative phosphorylation in the liver is associated with obesity and insulin resistance (Obesity 19 (917-924) DOI: 10.1038/oby.2010.214) (2011) (1)
- Mitochondrial Disorders: Metabolic and Genetic Basis (2014) (1)
- P001 Phase 1 Study of Erlotinib, Docetaxel, and Radiation in Locally Advanced Squamous Cell Cancer of the Head and Neck (2006) (1)
- Time to Harmonize Mitochondrial Syndrome Nomenclature and Classification: A Consensus from the North American Mitochondrial Disease Consortium (Namdc) (2022) (1)
- ACAD10 protein expression and Neurobehavioral assessment of Acad10-deficient mice (2020) (1)
- Comprehensive plasma acylcarnitine profiles of type 2 diabetic and non‐diabetic subjects with or without an uncoupling protein 3 (UCP3) missense polymorphism (2008) (1)
- Pharmacology and pharmacokinetics of aging (1997) (1)
- Pharmacokinetics of furosemide in hepatic ascites (1980) (1)
- Mitochondrial Bioenergetics in the Heart (2014) (1)
- Possible Bioenergetic Biomarker for Chronic Cancer-Related Fatigue. (2021) (0)
- A liver mitochondrial outer membrane (MOM) fatty acid transfer complex (2010) (0)
- The influence of anesthetic agents on fatty acid and carnitine metabolism in fed and starved rat (1982) (0)
- Abstract 851: High Saturated Fat Feeding Prevents Left Ventricular Dysfunction and Enhances Mitochondrial Function in Heart Failure (2006) (0)
- Erratum: Carnitine palmitoyltransferase activity in the rabbit choroid plexus: Its possible function in fatty acid metabolism and transport (Neuroscience Letters, 140 (1992) 13-15) (1992) (0)
- Hepatic metabolism of the dicarboxylate azelate: production of malonyl‐CoA and of anaplerotic methylmalonyl‐CoA (2006) (0)
- 171 The metabolic phenotype in moderate severity heart failure includes reductions in pyruvate dehydrogenase activity and malonyl CoA (2003) (0)
- Skeletal muscle mitochondrial dysfunction in pacing‐induced heart failure in dogs (2006) (0)
- dysfunctionand does not exacerbate left ventricular High-fat diet postinfarction enhances mitochondrial (2016) (0)
- Post‐translational Modifications of the Mitochondrial Outer Membrane Proteins: Carnitine Palmitoyltransferase‐I, Long‐chain acyl‐CoA synthetase, and Voltage Dependent Anion Channel (2006) (0)
- Aging effects on oxidative phosphorylation in rat adrenocortical mitochondria (2014) (0)
- Diffuse Cortical Gliosis Is Associated with Decreased Mitochondrial Electron Transport Chain Complex IV Activity in Epileptogenic Brain Resected from Children with Intractable Epilepsy (PD3.003) (2012) (0)
- HPLC-MS/MS Analysis of Carnitine and Acylcarnitines in Clinical Samples (2013) (0)
- 55. Respirosome supercomplexes in patients with defects in mitochondrial oxidative phosphorylation (2009) (0)
- Decrease in oxidative phosphorylation with aging correlates with the aging phenotype (2009) (0)
- Heart mitochondrial abnormalities in a canine model of pacing‐induced heart failure (2006) (0)
- Energy metabolism in human skeletal muscle mitochondria (2011) (0)
- 237: Markers of mitochondrial fatty acid oxidation are lower in placentas of obese mothers (2016) (0)
- Elevated acylcarnitine (AC) concentrations are associated with lower physical composite scores (PCS) in hemodialysis (HD) patients (2007) (0)
- KINETICS OFPLACENTALLY TRANSFERREDPHENYTOINAND ITS P-HYDROXYLATEDMETABOLITESINNEWBORN INFANTS (1979) (0)
- Selective, Accurate, and Precise Quantitation of Glutarylcarnitine in Human Urine from a Patient with Glutaric Acidemia Type I. (2017) (0)
- Abstract 18250: Tafazzin-Knockdown Mice: Heart Mitochondrial Structure and Function (2013) (0)
- Abstract 1328: Selective Glutaredoxin (GRx1) Knockdown in H9c2 Cells Provides a Model for Age-Related Decreases in GRx1 in Rat Heart, and Increases Susceptibility to Oxidant Induced Apoptosis (2007) (0)
- A121. Post infarction saturated fat feeding enhances mitochondrial function but does not exacerbate LV dysfunction (2006) (0)
- Elevated Leptin and Triglyceride are Associated with Enhanced Mitochondrial Function Despite Ceramide Accumulation (2007) (0)
- Carnitine metabolism in hepatic cirrhosis. (1980) (0)
- Pharmacologic 1-carnitine action and hypertriglyceridemia in the Zucker rat (1985) (0)
- Enhanced Mitochondrial Function in High Fat Fed Heart Failure Animals is Due to Increased Activation of Medium‐Chain Acyl‐CoA Dehydrogenase (2007) (0)
- Limited Fatty Acid Oxidation (FAO) in CPT2 Knockout Myocytes Associates with Insulin Resistance and Cell Stress: possible role of acylcarnitine lipotoxicity (2019) (0)
- Singlet Oxygen in Intact Heart Mitochondria Decreases Supercomplexes (2012) (0)
- Effect Of Age, Anesthesia, And Ischemia/Reperfusion With Palmitate On Myocardial Acylcarnitines (2007) (0)
- Effects of Halothane on Mitochondrial Function in C. Elegans: [2002][A-115] (2002) (0)
- Mitochondrial Uncoupling Decreases Sarcopenic Obesity By Activation of Skeletal Muscle Mitochondrial Quality Control and Attenuated ER Stress (2022) (0)
- BIOSYNTHESIS OF VALPROYLCARNITINE (2009) (0)
- Isolation and mass spectrometric analysis of native protein complexes in rat liver mitochondrial contact sites (2012) (0)
- Post Infarction High Saturated Fat Feeding Does Not Exacerbate LV Dysfunction but Enhances Mitochondrial Function (2006) (0)
- Identification of cis‐3,4‐cyclopropane‐heptanoylcarnitine in human urine and its synthesis (2006) (0)
- Proteomics approach to protein complexes in rat liver mitochondrial contact sites (2011) (0)
- Diagnostic application of measuring oxidative phosphorylation in permeabilized skin fibroblasts (2012) (0)
- Phase I pharmacokinetic trial of docetaxel and thalidomide: A regimen based on anti-angiogenic therapeutic principles (2004) (0)
- 71 Ischemic damage to the electron transport chain increases the production of reactive oxygen species from isolated rat heart mitochondria (2007) (0)
- Phase I pharmacokinetic trial of docetaxel and thalidomide: A regimen based on anti-angiogenic therapeutic principles. (2004) (0)
- Proficiency testing for mitochondrial electron transport chain (ETC) enzyme assays using C. elegans (2011) (0)
- Acetylcarnitine treatment increases mitochondrial protein‐lysine acetylation and protein expression (2010) (0)
- Misplaced mitochondria in a human myopathy (2012) (0)
- HIF drives lipid deposition and cancer in ccRCC via repression of fatty acid metabolism (2017) (0)
- Dependence of hepatic mitochondrial β-oxidation on carnitine palmitoyltransferase-A: Effect of starvation and diabetes (1984) (0)
- The dependence of hepatic mitochondrial β-oxidation on carnitine palmitoyltransferase-A: Effect of obesity and starvation (1984) (0)
- Effect of somatostatin on carnitine metabolism (1979) (0)
- Trimethyllysine metabolism in lean and obese zucker rats during fasting (1987) (0)
- Trimethyllysine metabolism in lean and obese zucker rats during fasting (1987) (0)
- Study on Integrated Mitochondrial Function and Cancer-Related Fatigue in Men with Prostate Cancer Undergoing Radiation Therapy (2022) (0)
- Effects of PPARalpha activation on mitochondrial function in the heart (2006) (0)
- Metabolite signatures reflective of muscle metabolism and insulin sensitivity following a diet and fitness intervention in obese, sedentary, insulin‐resistant women (2012) (0)
- A137. Effects of PPARα activation on mitochondrial function in the heart (2006) (0)
- Bispectral index and mitochondrial myopathies. Authors' reply (2003) (0)
- Fatty acid oxidation in the aged heart (2011) (0)
- Age-related changes in human skeletal muscle mitochondrial energy metabolism (2006) (0)
- Potential Consequences of Age‐Dependent Changes in Glutaredoxin in Cardiomyocytes (2007) (0)
- Pacing‐induced heart failure causes specific defects in the phosphorylation apparatus in skeletal muscle mitochondria (2007) (0)
- Age-associated Compositional Changes in Cardiolipin and Monolysocardilipin (2010) (0)
- Dependence of fatty acid oxidation on short-chain acyl-CoA dehydrogenase activity in riboflavin deficient rat (1984) (0)
- 4 Cytochrome c: A recurring nightmare in mitochondrial diagnostic assays (2010) (0)
- Bispectral Index and Mitochondrial Myopathies (2003) (0)
- Selective age-associated defect of respiratory complex III in interfibrillar heart mitochondria (1997) (0)
- Liver Gluconeogenic Gene Expression in Mouse Regulate Glycogen Synthesis and Protein-1 ( SREBP-1 ) Is Required to Sterol Regulatory Element-binding Gene Regulation : (2014) (0)
- Diabetes causes kidney cell‐specific mitochondrial phenotypes and increased generation of superoxide (2007) (0)
- 65 Fatty acid oxidation in human skeletal muscle mitochondria determined by oxidative phosphorylation as a function of age (2007) (0)
- Aged rat heart: Modulation of age-related respiratory defects decreases ischemic-reflow injury (2013) (0)
- Cardiolipin Biosynthesis: Hydrolysis on Cardiolipin Detected by HPLC-MS (2011) (0)
- Acylcarnitines: Distinguishing acylcarnitine isomeric forms by HPLC/ESI/MS (2006) (0)
- Inhibition of oleate oxidation in rat heart by acetate and propionate: A mass isotopomer study (2006) (0)
- Defects in mitochondrial oxidative phosphorylation: Role of supercomplexes (2010) (0)
- Breast cancer growth and proliferation is suppressed by the mitochondrial targeted furazano[3,4-b]pyrazine BAM15 (2021) (0)
- Autosomal dominant acute necrotizing encephalopathy associated with uncoupling of mitochondrial oxidative phosphorylation (2001) (0)
- Skeletal Muscle Mitochondria in Microembolism‐induced Heart Failure (2009) (0)
- CHOLESTEROL LOWERING EFFECT OF PROPIONATE MAY BE RELATED TO LOW CARNITINE INTAKE AND GLUCAGON-RESPONSE (1993) (0)
- 68A myopathy with retiform mitochondria (2012) (0)
- Weight loss and fitness intervention increase markers of hepatic bile acid (BA) synthesis, while reducing serum total BA concentrations in sedentary, obese insulin resistant women (2019) (0)
- A304 BUPIVACAINE INHIBITS CARDIAC MITOCHONDRIAL RESPIRATION DEPENDANT ON ACYLCARNITINE SUBSTRATES (1997) (0)
- Bioenergetic functions in subpopulations of heart mitochondria are preserved in a non-obese type 2 diabetes rat model (Goto-Kakizaki) (2020) (0)
- Bispectral index and mitochondrial myopathies [4] (multiple letters) (2003) (0)
- Mitochondrial disruption in cardiovascular diseases (2018) (0)
- Skeletal Muscle Mitochondrial Fission Is Increased after an Overnight Lipid Infusion in Healthy Humans (2018) (0)
- Development of B -Lapachone Prodrugs forTherapyAgainst Human Cancer Cells with Elevated NAD(P)H:Quinone Oxidoreductase 1Levels Cancer Therapy: Preclinical (2005) (0)
- 133 Detection of mitochondrial defects in patients with mitochondrial diseases: A case study (2010) (0)
- Mitochondrial Adaptation in Insulin Resistant Human Skeletal Muscle (2018) (0)
- Great Britain N 6-Trimethyl-lysine Metabolism 3-HYDROXY-N 6-TRIMETHYL-LYSINE AND CARNITINE BIOSYNTHESIS (0)
- 134 Permeabilized fibers or isolated mitochondria for the detection of oxidative phosphorylation defects in patients with mitochondrial diseases (2010) (0)
- Identification of unusual phospholipids from bovine heart mitochondria by HPLC-MS/MS. (2020) (0)
- Is there a single malonyl‐CoA pool in the heart for regulation of carnitine palmitoyltransferase‐I and fatty acid chain elongation (2006) (0)
- Deficiency oftheReducedNicotinamide AdenineDinucleotide Dehydrogenase ComponentofComplexIofMitochondrial Electron Transport (1987) (0)
- ATAD3A oligomerization causes neurodegeneration by coupling mitochondrial fragmentation and bioenergetics defects (2019) (0)
- Mitochondrial electron transport dissections of sequentially isolated lung cells: Rotenone-sensitive respiration burst during phagocytosis (1982) (0)
- Measurements of the kinetics of the pentose phosphate pathway (PPP) in perfused hearts and livers, using [U‐13C6]gluconolactone (2007) (0)
- Partial beta‐oxidation of gamma‐hydroxybutyrate (GHB) in perfused rat livers (2007) (0)
- Measurement of the turnover of glutathione by labeling from 2H‐enriched water and LC‐MS‐MS analysis (2007) (0)
- Fatty acid beta oxidation is the source of malonyl‐CoA for fatty acid chain elongation in rat heart (2009) (0)
- Dysregulated cellular redox status during hyperammonemia causes mitochondrial dysfunction and senescence by inhibiting sirtuin-mediated deacetylation. (2023) (0)
- Analysis of elderly (>= 65 yrs) patients' participation on early phase I clinical trials at two NCI-designated Comprehensive Cancer Centers (2005) (0)
- Heart mitochondrial fatty acid oxidation is not affected by deletion of the fatty acid transporter CD36/FAT (2011) (0)
- Effect of propionylcarnitine on mitochondrial energy metabolism in elderly rat heart (2012) (0)
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