Kevin P Campbell

Q: What Schools Are Affiliated With Kevin P Campbell

Kevin P Campbell is affiliated with the following schools: University of Pennsylvania, Washington University in St. Louis, University of California, Berkeley, McGill University, Uppsala University, University of Minnesota, University of Pavia, Stanford University, Baylor College of Medicine, University of Toronto, University of Iowa

Kevin P Campbell's AcademicInfluence.com Rankings

Kevin P Campbell

Computer Science

#2677

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#2801

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Computational Linguistics

#47

World Rank

#48

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Machine Learning

#183

World Rank

#185

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Artificial Intelligence

#317

World Rank

#323

Historical Rank

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Computer Science

Kevin P Campbell's Degrees

PhD Computer Science Stanford University
Masters Computer Science Stanford University
Bachelors Computer Science University of California, Berkeley

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Kevin P Campbell's Published Works

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Total number of citations to an author for the works they published in a given year. This highlights publication of the most important work(s) by the author

Published Works

Primary structure of dystrophin-associated glycoproteins linking dystrophin to the extracellular matrix (1992) (1402)
A role for the dystrophin-glycoprotein complex as a transmembrane linker between laminin and actin (1993) (1354)
Membrane organization of the dystrophin-glycoprotein complex (1991) (1283)
Deficiency of a glycoprotein component of the dystrophin complex in dystrophic muscle (1990) (977)
Defective membrane repair in dysferlin-deficient muscular dystrophy (2003) (923)
Nomenclature of Voltage-Gated Calcium Channels (2000) (895)
Three muscular dystrophies: Loss of cytoskeleton-extracellular matrix linkage (1995) (852)
Post-translational disruption of dystroglycan–ligand interactions in congenital muscular dystrophies (2002) (782)
Structural evidence for direct interaction between the molecular components of the transverse tubule/sarcoplasmic reticulum junction in skeletal muscle (1988) (767)
Association of dystrophin and an integral membrane glycoprotein (1989) (713)
Identification of alpha-dystroglycan as a receptor for lymphocytic choriomeningitis virus and Lassa fever virus. (1998) (672)
Cell Therapy of α-Sarcoglycan Null Dystrophic Mice Through Intra-Arterial Delivery of Mesoangioblasts (2003) (645)
Calcium channel β-subunit binds to a conserved motif in the I–II cytoplasmic linker of the α1-subunit (1994) (587)
Enteroviral protease 2A cleaves dystrophin: Evidence of cytoskeletal disruption in an acquired cardiomyopathy (1999) (567)
Dystroglycan is essential for early embryonic development: disruption of Reichert's membrane in Dag1-null mice. (1997) (550)
Deletion of brain dystroglycan recapitulates aspects of congenital muscular dystrophy (2002) (548)
Dystroglycan: from biosynthesis to pathogenesis of human disease (2006) (531)
Sequence and expression of MRNAs encoding the α1 and α2 subunits of a DHP-sensitive calcium channel (1988) (524)
Auxiliary subunits: essential components of the voltage-gated calcium channel complex (2003) (511)
Association of dystrophin-related protein with dystrophin-associated proteins in mdx mouse muscle (1992) (510)
The mouse stargazer gene encodes a neuronal Ca2+-channel γ subunit (1998) (505)
Animal Models for Muscular Dystrophy Show Different Patterns of Sarcolemmal Disruption (1997) (500)
Molecular basis of muscular dystrophies (2000) (490)
Missense mutations in the adhalin gene linked to autosomal recessive muscular dystrophy (1994) (470)
Congenital muscular dystrophy with merosin deficiency. (1994) (461)
Direct binding of G-protein βλ complex to voltage-dependent calcium channels (1997) (453)
Purified ryanodine receptor from rabbit skeletal muscle is the calcium- release channel of sarcoplasmic reticulum (1988) (450)
Muscular dystrophies involving the dystrophin-glycoprotein complex: an overview of current mouse models. (2002) (445)
Dystrophin-associated proteins are greatly reduced in skeletal muscle from mdx mice (1991) (438)
Purified ryanodine receptor from skeletal muscle sarcoplasmic reticulum is the Ca2+-permeable pore of the calcium release channel. (1987) (434)
β–sarcoglycan: characterization and role in limb–girdle muscular dystrophy linked to 4q12 (1995) (427)
A stoichiometric complex of neurexins and dystroglycan in brain (2001) (425)
Dystrophin-Glycoprotein Complex: Post-translational Processing and Dystroglycan Function* 210 (2003) (422)
A Role for Dystroglycan in Basement Membrane Assembly (1998) (407)
Muscular dystrophies and the dystrophin-glycoprotein complex. (1997) (394)
The brain ryanodine receptor: A caffeine-sensitive calcium release channel (1991) (393)
Dystrophin-related protein is localized to neuromuscular junctions of adult skeletal muscle (1991) (388)
A role for dystrophin-associated glycoproteins and utrophin in agrin-induced AChR clustering (1994) (383)
Staining of the Ca2+-binding proteins, calsequestrin, calmodulin, troponin C, and S-100, with the cationic carbocyanine dye "Stains-all". (1983) (380)
The naming of voltage-gated calcium channels (1994) (371)
Disruption of the Sarcoglycan–Sarcospan Complex in Vascular Smooth Muscle A Novel Mechanism for Cardiomyopathy and Muscular Dystrophy (1999) (367)
The ryanodine receptor/Ca2+ release channel. (1993) (367)
Progressive Muscular Dystrophy in α-Sarcoglycan–deficient Mice (1998) (341)
Deficiency of merosin in dystrophic dy mice and genetic linkage of laminin M chain gene to dy locus. (1994) (327)
O-Mannosyl Phosphorylation of Alpha-Dystroglycan Is Required for Laminin Binding (2010) (323)
Dystrophin–glycoprotein complex: Its role in the molecular pathogenesis of muscular dystrophies (1994) (318)
Abnormal Coronary Function in Mice Deficient in α1H T-type Ca2+ Channels (2003) (308)
Immunosuppression and Resultant Viral Persistence by Specific Viral Targeting of Dendritic Cells (2000) (302)
Identification and Characterization of the Dystrophin Anchoring Site on β-Dystroglycan (*) (1995) (298)
PGC-1α regulates the neuromuscular junction program and ameliorates Duchenne muscular dystrophy (2007) (297)
Dystroglycan inside and out. (1999) (296)
Subcellular fractionation of dystrophin to the triads of skeletal muscle (1987) (296)
Overexpression of dystrophin in transgenic mdx mice eliminates dystrophic symptoms without toxicity (1993) (294)
Dual Function of the Voltage-Dependent Ca2+ Channel α2δ Subunit in Current Stimulation and Subunit Interaction (1996) (289)
Maturation and Maintenance of the Neuromuscular Synapse Genetic Evidence for Roles of the Dystrophin–Glycoprotein Complex (2000) (288)
Dystrophin-glycoprotein complex is highly enriched in isolated skeletal muscle sarcolemma (1991) (286)
Disruption of Dag1 in Differentiated Skeletal Muscle Reveals a Role for Dystroglycan in Muscle Regeneration (2002) (282)
Dysferlin and the plasma membrane repair in muscular dystrophy. (2004) (282)
Induction of calcium currents by the expression of the α1-subunit of the dihydropyridine receptor from skeletal muscle (1989) (282)
The biochemistry and molecular biology of the dihydropyridine-sensitive calcium channel (1988) (280)
The mouse stargazer gene encodes a neuronal Ca2+-channel gamma subunit. (1998) (279)
Dystroglycan: an extracellular matrix receptor linked to the cytoskeleton. (1996) (276)
SH3 Domain-mediated Interaction of Dystroglycan and Grb2(*) (1995) (272)
Unique Role of Dystroglycan in Peripheral Nerve Myelination, Nodal Structure, and Sodium Channel Stabilization (2003) (268)
Sarcolemma-localized nNOS is required to maintain activity after mild exercise (2008) (265)
LARGE can functionally bypass α-dystroglycan glycosylation defects in distinct congenital muscular dystrophies (2004) (262)
Primary structure of the gamma subunit of the DHP-sensitive calcium channel from skeletal muscle. (1990) (261)
Molecular Recognition by LARGE Is Essential for Expression of Functional Dystroglycan (2004) (260)
Dystroglycan Function Requires Xylosyl- and Glucuronyltransferase Activities of LARGE (2012) (260)
Deficiency of the 50K dystrophin-associated glycoprotein in severe childhood autosomal recessive muscular dystrophy (1992) (259)
Structural characterization of the dihydropyridine-sensitive calcium channel alpha 2-subunit and the associated delta peptides. (1991) (255)
The unfolded protein response mediates adaptation to exercise in skeletal muscle through a PGC-1α/ATF6α complex. (2011) (254)
Structural Analysis of the Voltage-Dependent Calcium Channel β Subunit Functional Core and Its Complex with the α1 Interaction Domain (2004) (251)
Ca2+ channel regulation by a conserved β subunit domain (1994) (244)
RIM1 confers sustained activity and neurotransmitter vesicle anchoring to presynaptic Ca2+ channels (2007) (242)
Association of Triadin with the Ryanodine Receptor and Calsequestrin in the Lumen of the Sarcoplasmic Reticulum (*) (1995) (241)
A dystroglycan mutation associated with limb-girdle muscular dystrophy. (2011) (240)
Human dystroglycan: skeletal muscle cDNA, genomic structure, origin of tissue specific isoforms and chromosomal localization. (1993) (239)
Dysferlin and muscle membrane repair. (2007) (237)
A neuronal ryanodine receptor mediates light-induced phase delays of the circadian clock (1998) (236)
Subunit identification and reconstitution of the N-type Ca2+ channel complex purified from brain. (1993) (227)
Isolation, characterization, and localization of the inositol 1,4,5-trisphosphate receptor protein in Xenopus laevis oocytes. (1992) (223)
Ryanodine receptor of skeletal muscle is a gap junction-type channel. (1988) (218)
ISPD loss-of-function mutations disrupt dystroglycan O-mannosylation and cause Walker-Warburg syndrome (2012) (216)
Role of α-Dystroglycan as a Schwann Cell Receptor for Mycobacterium leprae (1998) (215)
Assembly of the Dystrophin-Associated Protein Complex Does Not Require the Dystrophin Cooh-Terminal Domain (2000) (215)
C‐terminal titin deletions cause a novel early‐onset myopathy with fatal cardiomyopathy (2007) (215)
Attenuated pain responses in mice lacking CaV3.2 T‐type channels (2007) (214)
Duchenne muscular dystrophy (1988) (211)
In vivo muscle gene transfer of full-length dystrophin with an adenoviral vector that lacks all viral genes. (1996) (209)
Rapsyn may function as a link between the acetylcholine receptor and the agrin-binding dystrophin-associated glycoprotein complex (1995) (207)
Disruption of the beta-sarcoglycan gene reveals pathogenetic complexity of limb-girdle muscular dystrophy type 2E. (2000) (206)
Non-muscle alpha-dystroglycan is involved in epithelial development (1995) (205)
Sarcospan, the 25-kDa Transmembrane Component of the Dystrophin-Glycoprotein Complex* (1997) (202)
Minimum Requirements for Efficient Transduction of Dividing and Nondividing Cells by Feline Immunodeficiency Virus Vectors (1999) (201)
Distribution of Dystroglycan in Normal Adult Mouse Tissues (1998) (199)
Abnormal coronary function in mice deficient in alpha1H T-type Ca2+ channels. (2003) (199)
Mutations in GDP-mannose pyrophosphorylase B cause congenital and limb-girdle muscular dystrophies associated with hypoglycosylation of α-dystroglycan. (2013) (194)
PGC-1alpha regulates the neuromuscular junction program and ameliorates Duchenne muscular dystrophy. (2007) (191)
Transcriptional Upregulation of Cav3.2 Mediates Epileptogenesis in the Pilocarpine Model of Epilepsy (2008) (191)
Structural characterization of the 1,4-dihydropyridine receptor of the voltage-dependent Ca2+ channel from rabbit skeletal muscle. Evidence for two distinct high molecular weight subunits. (1987) (190)
Primary adhalinopathy: a common cause of autosomal recessive muscular dystrophy of variable severity (1995) (189)
Identification of a novel mutant transcript of laminin alpha 2 chain gene responsible for muscular dystrophy and dysmyelination in dy2J mice. (1995) (187)
SGK196 Is a Glycosylation-Specific O-Mannose Kinase Required for Dystroglycan Function (2013) (184)
Biosynthesis of dystroglycan: processing of a precursor propeptide (2000) (178)
Forced expression of dystrophin deletion constructs reveals structure- function correlations (1996) (177)
Subunit regulation of the neuronal alpha 1A Ca2+ channel expressed in Xenopus oocytes. (1995) (176)
Dystroglycan Is Selectively Associated with Inhibitory GABAergic Synapses But Is Dispensable for Their Differentiation (2002) (176)
Cloning and tissue‐specific expression of the brain calcium channel β‐subunit (1991) (175)
Identification and characterization of the high affinity [3H]ryanodine receptor of the junctional sarcoplasmic reticulum Ca2+ release channel. (1987) (174)
Compositional differences between infant and adult human corneal basement membranes. (2007) (172)
Calcium channel beta-subunit binds to a conserved motif in the I-II cytoplasmic linker of the alpha 1-subunit. (1994) (171)
Primary structure and muscle-specific expression of the 50-kDa dystrophin-associated glycoprotein (adhalin). (1993) (170)
Purification of dystrophin from skeletal muscle. (1991) (170)
New World Arenavirus Clade C, but Not Clade A and B Viruses, Utilizes α-Dystroglycan as Its Major Receptor (2002) (168)
Dp71 can restore the dystrophin-associated glycoprotein complex in muscle but fails to prevent dystrophy (1994) (168)
Dystrophin and the membrane skeleton. (1993) (167)
Differences in Affinity of Binding of Lymphocytic Choriomeningitis Virus Strains to the Cellular Receptor α-Dystroglycan Correlate with Viral Tropism and Disease Kinetics (2001) (167)
Identification of Three Subunits of the High Affinity ω-Conotoxin MVIIC-sensitive Ca2+ Channel* (1996) (166)
Mutations in B3GALNT2 cause congenital muscular dystrophy and hypoglycosylation of α-dystroglycan. (2013) (164)
Matriglycan: a novel polysaccharide that links dystroglycan to the basement membrane (2015) (163)
Dysferlin-mediated membrane repair protects the heart from stress-induced left ventricular injury. (2007) (162)
Dissection of Functional Domains of the Voltage-Dependent Ca2+ Channel α2δ Subunit (1997) (161)
Dystroglycan in development and disease. (1998) (159)
A role for dystroglycan in epithelial polarization: loss of function in breast tumor cells. (2002) (158)
A β4 Isoform-specific Interaction Site in the Carboxyl-terminal Region of the Voltage-dependent Ca2+ Channel α1A Subunit* (1998) (158)
Distinct roles for dystroglycan, beta1 integrin and perlecan in cell surface laminin organization. (2001) (158)
Molecular analysis of the interaction of LCMV with its cellular receptor α-dystroglycan (2001) (157)
Dystroglycan is a binding protein of laminin and merosin in peripheral nerve (1994) (156)
Expression of human full-length and minidystrophin in transgenic mdx mice: implications for gene therapy of Duchenne muscular dystrophy. (1995) (154)
Purification and characterization of calsequestrin from canine cardiac sarcoplasmic reticulum and identification of the 53,000 dalton glycoprotein. (1983) (154)
Membrane Targeting and Stabilization of Sarcospan Is Mediated by the Sarcoglycan Subcomplex (1999) (153)
Limb-Girdle Muscular Dystrophy in the United States (2006) (152)
Subunit Heterogeneity in N-type Ca Channels (*) (1996) (150)
The CaV3.2 T-Type Ca2+ Channel Is Required for Pressure Overload–Induced Cardiac Hypertrophy in Mice (2009) (150)
Animal models for muscular dystrophy: valuable tools for the development of therapies. (2000) (150)
Structural and functional diversity of voltage-activated calcium channels. (1996) (149)
Dystroglycan in the Cerebellum is a Laminin α2‐chain Binding Protein at the Glial‐Vascular Interface and is Expressed in Purkinje cells (1996) (149)
An HMGA2-IGF2BP2 axis regulates myoblast proliferation and myogenesis. (2012) (148)
The sarcoglycan complex in limb-girdle muscular dystrophy. (1998) (144)
The effects of ryanodine on passive calcium fluxes across sarcoplasmic reticulum membranes. (1987) (144)
Properties of the - Anchoring Site in Voltage-dependent Ca Channels (*) (1995) (143)
Posttranslational Modification of α-Dystroglycan, the Cellular Receptor for Arenaviruses, by the Glycosyltransferase LARGE Is Critical for Virus Binding (2005) (140)
Further characterization of light and heavy sarcoplasmic reticulum vesicles. Identification of the 'sarcoplasmic reticulum feet' associated with heavy sarcoplasmic reticulum vesicles. (1980) (138)
A founder mutation in the gamma-sarcoglycan gene of gypsies possibly predating their migration out of India. (1996) (136)
Specific absence of the alpha 1 subunit of the dihydropyridine receptor in mice with muscular dysgenesis. (1989) (134)
Basal lamina strengthens cell membrane integrity via the laminin G domain-binding motif of α-dystroglycan (2009) (134)
Disruption of the dystrophin-glycoprotein complex in the cardiomyopathic hamster. (1993) (133)
Mild congenital muscular dystrophy in two patients with an internally deleted laminin alpha2-chain. (1997) (132)
Identification and characterization of the dihydropyridine-binding subunit of the skeletal muscle dihydropyridine receptor. (1987) (132)
Primary adhalinopathy (alpha-sarcoglycanopathy): clinical, pathologic, and genetic correlation in 20 patients with autosomal recessive muscular dystrophy. (1997) (132)
Functional rescue of the sarcoglycan complex in the BIO 14.6 hamster using delta-sarcoglycan gene transfer. (1998) (130)
Exogenous Dp71 restores the levels of dystrophin associated proteins but does not alleviate muscle damage in mdx mice (1994) (130)
The Ca2+-release channel/ryanodine receptor is localized in junctional and corbular sarcoplasmic reticulum in cardiac muscle (1993) (129)
Merosin‐negative congenital muscular dystrophy associated with extensive brain abnormalities (1995) (127)
Dystrophin-glycoprotein complex and laminin colocalize to the sarcolemma and transverse tubules of cardiac muscle. (1993) (127)
Intracellular accumulation and reduced sarcolemmal expression of dysferlin in limb–girdle muscular dystrophies (2000) (126)
Primary structure and topological analysis of a skeletal muscle-specific junctional sarcoplasmic reticulum glycoprotein (triadin). (1993) (123)
Fukutin gene mutations cause dilated cardiomyopathy with minimal muscle weakness (2006) (123)
A Comparative Study of α‐Dystroglycan Glycosylation in Dystroglycanopathies Suggests that the Hypoglycosylation of α‐Dystroglycan Does Not Consistently Correlate with Clinical Severity (2009) (121)
mdx muscle pathology is independent of nNOS perturbation. (1998) (121)
Biochemical Characterization of the Epithelial Dystroglycan Complex* (1999) (121)
ε-Sarcoglycan Replaces α-Sarcoglycan in Smooth Muscle to Form a Unique Dystrophin-Glycoprotein Complex* (1999) (120)
Subcellular distribution of the 1,4-dihydropyridine receptor in rabbit skeletal muscle in situ: an immunofluorescence and immunocolloidal gold- labeling study (1989) (119)
Cortical localization of a calcium release channel in sea urchin eggs (1992) (119)
Biochemical and Biophysical Evidence for γ2 Subunit Association with Neuronal Voltage-activated Ca2+Channels* (2001) (119)
A β-subunit normalizes the electrophysiological properties of a cloned N-type CA2+ channel α1-subunit (1993) (118)
Distinct Functions of Glial and Neuronal Dystroglycan in the Developing and Adult Mouse Brain (2010) (117)
Heterogeneity of the 59-kDa dystrophin-associated protein revealed by cDNA cloning and expression. (1994) (117)
Characterization of Dystroglycan‐Laminin Interaction in Peripheral Nerve (1996) (117)
Prevention of cardiomyopathy in mouse models lacking the smooth muscle sarcoglycan-sarcospan complex. (2001) (115)
Mutational diversity and hot spots in the alpha-sarcoglycan gene in autosomal recessive muscular dystrophy (LGMD2D). (1997) (115)
Both Laminin and Schwann Cell Dystroglycan Are Necessary for Proper Clustering of Sodium Channels at Nodes of Ranvier (2005) (114)
Identification and characterization of the dystrophin anchoring site on beta-dystroglycan. (1995) (112)
Structural analysis of the voltage-dependent calcium channel beta subunit functional core and its complex with the alpha 1 interaction domain. (2004) (111)
Proteolytic Enzymes and Altered Glycosylation Modulate Dystroglycan Function in Carcinoma Cells (2004) (111)
Identification of α-Syntrophin Binding to Syntrophin Triplet, Dystrophin, and Utrophin (*) (1995) (111)
Expression and Subunit Interaction of Voltage-Dependent Ca2+ Channels in PC12 Cells (1996) (110)
Biochemical Characterization and Molecular Cloning of Cardiac Triadin (*) (1996) (109)
Clustering and immobilization of acetylcholine receptors by the 43-kD protein: a possible role for dystrophin-related protein (1993) (109)
Biochemical and ultrastructural characterization of the 1,4-dihydropyridine receptor from rabbit skeletal muscle. Evidence for a 52,000 Da subunit. (1988) (107)
Ultrastructural localization of calsequestrin in adult rat atrial and ventricular muscle cells (1985) (107)
Direct binding of G-protein betagamma complex to voltage-dependent calcium channels. (1997) (106)
Molecular Pathogenesis of Muscle Degeneration in the δ-Sarcoglycan-Deficient Hamster (1998) (106)
LARGE glycans on dystroglycan function as a tunable matrix scaffold to prevent dystrophy (2013) (106)
Localization of the high affinity calcium binding protein and an intrinsic glycoprotein in sarcoplasmic reticulum membranes. (1980) (106)
Centronuclear myopathy in mice lacking a novel muscle-specific protein kinase transcriptionally regulated by MEF2. (2005) (105)
Extracellular Interaction of the Voltage-dependent Ca2+ Channel α2δ and α1 Subunits* (1997) (105)
A biochemical, genetic, and clinical survey of autosomal recessive limb girdle muscular dystrophies in Turkey (1997) (103)
Reduced expression of dystroglycan in breast and prostate cancer. (2001) (103)
Like-acetylglucosaminyltransferase (LARGE)-dependent modification of dystroglycan at Thr-317/319 is required for laminin binding and arenavirus infection (2011) (103)
A calmodulin-dependent protein kinase system from skeletal muscle sarcoplasmic reticulum. Phosphorylation of a 60,000-dalton protein. (1982) (102)
Dystroglycan loss disrupts polarity and β-casein induction in mammary epithelial cells by perturbing laminin anchoring (2006) (101)
Identification of critical amino acids involved in α 1‐β interaction in voltage‐dependent Ca2+ channels (1996) (101)
Point mutation in the glycoprotein of lymphocytic choriomeningitis virus is necessary for receptor binding, dendritic cell infection, and long-term persistence (2011) (101)
Characterization of the major brain form of the ryanodine receptor/Ca2+ release channel. (1993) (101)
β Subunit Reshuffling Modifies N- and P/Q-Type Ca2+Channel Subunit Compositions in Lethargic Mouse Brain (1999) (100)
Congenital muscular dystrophy with rigid spine syndrome: A clinical, pathological, radiological, and genetic study (2000) (100)
Assembly of the Sarcoglycan Complex (1998) (100)
Molecular and genetic characterization of sarcospan: insights into sarcoglycan-sarcospan interactions. (2000) (99)
Sequence and expression of mRNAs encoding the alpha 1 and alpha 2 subunits of a DHP-sensitive calcium channel. (1988) (99)
A Role of Dystroglycan in Schwannoma Cell Adhesion to Laminin* (1997) (99)
Association of Native Ca Channel Subunits with the Subunit Interaction Domain (*) (1995) (98)
Ultrastructural localization of calsequestrin in rat skeletal muscle by immunoferritin labeling of ultrathin frozen sections (1983) (95)
Dystroglycan expression in the wild type and mdx mouse neural retina: Synaptic colocalization with dystrophin, dystrophin‐related protein but not laminin (1995) (95)
Subunit Stoichiometry of Human Muscle Chloride Channels (1997) (94)
A monoclonal antibody to the Ca2+-ATPase of cardiac sarcoplasmic reticulum cross-reacts with slow type I but not with fast type II canine skeletal muscle fibers: an immunocytochemical and immunochemical study. (1988) (93)
CaV3.2 is the major molecular substrate for redox regulation of T‐type Ca2+ channels in the rat and mouse thalamus (2006) (91)
The glucuronyltransferase B4GAT1 is required for initiation of LARGE-mediated α-dystroglycan functional glycosylation (2014) (91)
Evidence for a role of dystroglycan regulating the membrane architecture of astroglial endfeet (2011) (91)
Loss of sarcolemma nNOS in sarcoglycan‐deficient muscle (2002) (91)
Biochemical characterization of ultrastructural localization of a major junctional sarcoplasmic reticulum glycoprotein (triadin). (1993) (90)
Loss of α-Dystroglycan Laminin Binding in Epithelium-derived Cancers Is Caused by Silencing of LARGE*S⃞♦ (2009) (90)
POMT1 mutation results in defective glycosylation and loss of laminin-binding activity in α-DG (2004) (90)
Characterization of δ-Sarcoglycan, a Novel Component of the Oligomeric Sarcoglycan Complex Involved in Limb-Girdle Muscular Dystrophy* (1996) (90)
Caveolin‐3 is not an integral component of the dystrophin glycoprotein complex (1998) (87)
Role of alpha-dystroglycan as a Schwann cell receptor for Mycobacterium leprae. (1998) (86)
Purification, calcium binding properties, and ultrastructural localization of the 53,000- and 160,000 (sarcalumenin)-dalton glycoproteins of the sarcoplasmic reticulum. (1990) (86)
The Voltage-dependent Calcium Channel β Subunit Contains Two Stable Interacting Domains* (2003) (86)
Dual function of the voltage-dependent Ca2+ channel alpha 2 delta subunit in current stimulation and subunit interaction. (1996) (86)
Solubilization and biochemical characterization of the high affinity [3H]ryanodine receptor from rabbit brain membranes. (1990) (85)
The functional O-mannose glycan on α-dystroglycan contains a phospho-ribitol primed for matriglycan addition (2016) (85)
Prevention of dystrophic pathology in mdx mice by a truncated dystrophin isoform. (1994) (84)
Dystrophin-glycoprotein complex: molecular organization and critical roles in skeletal muscle. (1995) (84)
ISPD gene mutations are a common cause of congenital and limb-girdle muscular dystrophies (2013) (84)
Residual laminin-binding activity and enhanced dystroglycan glycosylation by LARGE in novel model mice to dystroglycanopathy (2008) (81)
Evidence for the presence of calsequestrin in two structurally different regions of myocardial sarcoplasmic reticulum (1984) (81)
Genetic ablation of complement C3 attenuates muscle pathology in dysferlin-deficient mice. (2010) (80)
γ Subunit of Voltage-activated Calcium Channels* (2003) (79)
Dystroglycan binding to laminin alpha1LG4 module influences epithelial morphogenesis of salivary gland and lung in vitro. (2001) (79)
Sarcospan-Deficient Mice Maintain Normal Muscle Function (2000) (79)
Dissection of functional domains of the voltage-dependent Ca2+ channel alpha2delta subunit. (1997) (79)
Brief report: deficiency of a dystrophin-associated glycoprotein (adhalin) in a patient with muscular dystrophy and cardiomyopathy. (1996) (79)
Differential expression of dystrophin, utrophin and dystrophin‐associated proteins in peripheral nerve (1993) (79)
Are voltage-dependent ion channels involved in the endothelial cell control of vasomotor tone? (2007) (79)
Brain and Eye Malformations Resembling Walker–Warburg Syndrome Are Recapitulated in Mice by Dystroglycan Deletion in the Epiblast (2008) (78)
Presence of inositol 1,4,5-trisphosphate receptor, calreticulin, and calsequestrin in eggs of sea urchins and Xenopus laevis. (1994) (78)
Characterization of the 1,4-dihydropyridine receptor using subunit-specific polyclonal antibodies. Evidence for a 32,000-Da subunit. (1989) (77)
Common pathological mechanisms in mouse models for muscular dystrophies (2006) (77)
α6β4 Integrin and Dystroglycan Cooperate to Stabilize the Myelin Sheath (2008) (77)
Structural basis of laminin binding to the LARGE glycans on dystroglycan (2016) (76)
Abnormal expression of dystrophin-associated proteins in Fukuyama-type congenital muscular dystrophy (1993) (75)
A neural correlate of response bias in monkey caudate nucleus (75)
Interactions of intermediate filament protein synemin with dystrophin and utrophin. (2006) (75)
Skeletal Muscle Basement Membrane-Sarcolemma-Cytoskeleton Interaction Minireview Series* (2003) (75)
Congenital disorder of glycosylation due to DPM1 mutations presenting with dystroglycanopathy-type congenital muscular dystrophy. (2013) (75)
Glycomic Analyses of Mouse Models of Congenital Muscular Dystrophy* (2011) (74)
Purification and characterization of the 53,000-dalton glycoprotein from the sarcoplasmic reticulum. (1981) (74)
The calcium signal and neutrophil activation. (1990) (73)
Dystrophic phenotype induced in vitro by antibody blockade of muscle alpha-dystroglycan-laminin interaction. (1999) (72)
Decoding arenavirus pathogenesis: essential roles for alpha-dystroglycan-virus interactions and the immune response. (2011) (71)
Opposing roles of integrin alpha6Abeta1 and dystroglycan in laminin-mediated extracellular signal-regulated kinase activation. (2003) (70)
Transmembrane Auxiliary Subunits of Voltage-dependent Ion Channels* (1996) (70)
Deficiency of dystrophin-associated proteins: A common mechanism leading to muscle cell necrosis in severe childhood muscular dystrophies (1993) (69)
Ca2+ channel regulation by a conserved beta subunit domain. (1994) (69)
Contrast agent‐enhanced magnetic resonance imaging of skeletal muscle damage in animal models of muscular dystrophy (2000) (68)
Dystroglycan on radial glia end feet is required for pial basement membrane integrity and columnar organization of the developing cerebral cortex. (2012) (68)
Proteomic analysis of plasma membrane and secretory vesicles from human neutrophils (2007) (67)
Specific association of calmodulin-dependent protein kinase and related substrates with the junctional sarcoplasmic reticulum of skeletal muscle. (1990) (67)
Old World and Clade C New World Arenaviruses Mimic the Molecular Mechanism of Receptor Recognition Used by α-Dystroglycan's Host-Derived Ligands (2007) (66)
Ca‐ATPase isozyme expression in sarcoplasmic reticulum is altered by chronic stimulation of skeletal muscle (1990) (66)
Welcome to Skeletal Muscle (2011) (64)
Quercetin inhibits Ca2+ uptake but not Ca2+ release by sarcoplasmic reticulum in skinned muscle fibers. (1980) (64)
Absence of the Skeletal Muscle Sarcolemma Chloride Channel ClC-1 in Myotonic Mice (*) (1995) (64)
Evidence for the association of dystrophin with the transverse tubular system in skeletal muscle. (1988) (63)
Distribution of alpha-dystroglycan during embryonic nerve-muscle synaptogenesis (1995) (63)
A common missense mutation in the adhalin gene in three unrelated Brazilian families with a relatively mild form of autosomal recessive limb-girdle muscular dystrophy. (1995) (63)
Proteoglycan synthesis by fibroblast cultures initiated from regions of adult bovine tendon subjected to different mechanical forces. (1986) (63)
Laminin-6 assembles into multimolecular fibrillar complexes with perlecan and participates in mechanical-signal transduction via a dystroglycan-dependent, integrin-independent mechanism (2005) (62)
Dystrophin-associated glycoproteins: their possible roles in the pathogenesis of Duchenne muscular dystrophy. (1993) (61)
Neuronal Dystroglycan Is Necessary for Formation and Maintenance of Functional CCK-Positive Basket Cell Terminals on Pyramidal Cells (2016) (60)
Visual Impairment in the Absence of Dystroglycan (2009) (59)
Analysis of excitation-contraction-coupling components in chronically stimulated canine skeletal muscle. (1991) (58)
A monoclonal antibody to the beta subunit of the skeletal muscle dihydropyridine receptor immunoprecipitates the brain omega-conotoxin GVIA receptor. (1991) (58)
Disruption of perlecan binding and matrix assembly by post‐translational or genetic disruption of dystroglycan function (2005) (58)
Photoaffinity labeling of the ryanodine receptor/Ca2+ release channel with an azido derivative of ryanodine. (1994) (57)
Loss of basement membrane, receptor and cytoskeletal lattices in a laminin-deficient muscular dystrophy (2004) (57)
Newly synthesized calsequestrin, destined for the sarcoplasmic reticulum, is contained in early/intermediate Golgi-derived clathrin-coated vesicles. (1989) (55)
Dystrophin deficiency exacerbates skeletal muscle pathology in dysferlin-null mice (2011) (54)
Characterization of the purified N-type Ca2+ channel and the cation sensitivity of ω-conotoxin GVIA binding (1993) (54)
Mouse fukutin deletion impairs dystroglycan processing and recapitulates muscular dystrophy. (2012) (54)
Insulin Resistance in Striated Muscle-specific Integrin Receptor β1-deficient Mice* (2009) (54)
Expression of γ-Sarcoglycan in Smooth Muscle and Its Interaction with the Smooth Muscle Sarcoglycan-Sarcospan Complex* (2000) (54)
The role of the dystrophin-glycoprotein complex in the molecular pathogenesis of muscular dystrophies (1993) (53)
Modified Cardiovascular L-type Channels in Mice Lacking the Voltage-dependent Ca2+ Channel β3 Subunit* (2003) (53)
Phosphorylation of the 1,4-dihydropyridine receptor of the voltage-dependent Ca2+ channel by an intrinsic protein kinase in isolated triads from rabbit skeletal muscle. (1987) (53)
Absence of γ‐sarcoglycan (35 DAG) in autosomal recessive muscular dystrophy linked to chromosome 13q12 (1996) (53)
Long-term skeletal muscle protection after gene transfer in a mouse model of LGMD-2D. (2007) (51)
Old World arenavirus infection interferes with the expression of functional alpha-dystroglycan in the host cell. (2007) (51)
A 5' dystrophin duplication mutation causes membrane deficiency of alpha-dystroglycan in a family with X-linked cardiomyopathy. (1997) (51)
Genetic heterogeneity for Duchenne-like muscular dystrophy (DLMD) based on linkage and 50 DAG analysis. (1993) (50)
Characterization of aquaporin‐4 in muscle and muscular dystrophy (2002) (50)
Xylosyl- and glucuronyltransferase functions of LARGE in α-dystroglycan modification are conserved in LARGE2 (2012) (50)
Congenital muscular dystrophy type 1D (MDC1D) due to a large intragenic insertion/deletion, involving intron 10 of the LARGE gene (2011) (49)
Cav3.2 T-type calcium channel is required for the NFAT-dependent Sox9 expression in tracheal cartilage (2014) (49)
Evidence for a 95 kDa Short Form of the α1A Subunit Associated with the ω-Conotoxin MVIIC Receptor of the P/Q-type Ca2+ Channels (1998) (49)
Direct photoaffinity labeling of the high affinity nitrendipine-binding site in subcellular membrane fractions isolated from canine myocardium. (1984) (49)
Intramembrane charge movements and excitation– contraction coupling expressed by two-domain fragments of the Ca2+ channel (2001) (48)
γ1 Subunit Interactions within the Skeletal Muscle L-type Voltage-gated Calcium Channels* (2003) (48)
Neural Regulation of α‐Dystroglycan Biosynthesis and Glycosylation in Skeletal Muscle (2000) (48)
β-Sarcoglycan: genomic analysis and identification of a novel missense mutation in the LGMD2E Amish isolate (1998) (47)
Identification of alpha-syntrophin binding to syntrophin triplet, dystrophin, and utrophin. (1995) (47)
Identification of novel proteins unique to either transverse tubules (TS28) or the sarcolemma (SL50) in rabbit skeletal muscle (1990) (47)
Plant cells contain calsequestrin. (1989) (47)
Extracellular interaction of the voltage-dependent Ca2+ channel alpha2delta and alpha1 subunits. (1997) (47)
Molecular pathogenesis of muscle degeneration in the delta-sarcoglycan-deficient hamster. (1998) (46)
Early adenovirus-mediated gene transfer effectively prevents muscular dystrophy in alpha-sarcoglycan-deficient mice (2000) (46)
Expression, localization and functions in acrosome reaction and sperm motility of CaV3.1 and CaV3.2 channels in sperm cells: An evaluation from CaV3.1 and CaV3.2 deficient mice (2007) (45)
Cell stiffness and receptors: evidence for cytoskeletal subnetworks. (2005) (45)
Rab3-interacting Molecule γ Isoforms Lacking the Rab3-binding Domain Induce Long Lasting Currents but Block Neurotransmitter Vesicle Anchoring in Voltage-dependent P/Q-type Ca2+ Channels* (2010) (45)
Long‐term regulation of voltage‐gated Ca2+ channels by gabapentin (2002) (44)
Sarcolemmal-restricted localization of functional ClC-1 channels in mouse skeletal muscle (2010) (44)
Three Muscular Dystrophies: Review Loss of Cytoskeleton-Extracellular (1995) (44)
Laminin isoforms differentially regulate adhesion, spreading, proliferation, and ERK activation of beta1 integrin-null cells. (2004) (44)
Expression of dystrophin-associated glycoproteins during human fetal muscle development: A preliminary immunocytochemical study (1994) (43)
Sequence similarity of calreticulin with a Ca2(+)-binding protein that co-purifies with an Ins(1,4,5)P3-sensitive Ca2+ store in HL-60 cells. (1990) (43)
Congenital muscular dystrophy with glycosylation defects of α-dystroglycan in Japan (2005) (41)
Dystroglycan Matrix Receptor Function in Cardiac Myocytes Is Important for Limiting Activity-Induced Myocardial Damage (2009) (41)
GMPPB‐Associated Dystroglycanopathy: Emerging Common Variants with Phenotype Correlation (2015) (40)
ION PATHWAYS IN PROTEINS OF THE SARCOPLASMIC RETICULUM * (1980) (39)
Fukutin-related Protein Associates with the Sarcolemmal Dystrophin-Glycoprotein Complex* (2007) (39)
Combined deficiency of alpha and epsilon sarcoglycan disrupts the cardiac dystrophin complex (2011) (39)
Gamma subunit of voltage-activated calcium channels. (2003) (38)
Endpoint measures in the mdx mouse relevant for muscular dystrophy pre-clinical studies (2012) (38)
Distinct immunopeptide maps of the sarcoplasmic reticulum Ca2+ release channel in malignant hyperthermia. (1990) (38)
Transient expression of Dp140, a product of the Duchenne muscular dystrophy locus, during kidney tubulogenesis. (1997) (38)
Genetic heterogeneity of severe childhood autosomal recessive muscular dystrophy with adhalin (50 kDa dystrophin-associated glycoprotein) deficiency. (1994) (37)
Restoration of dystrophin‐associated proteins in skeletal muscle of mdx mice transgenic for dystrophin gene (1993) (35)
Mild deficiency of dystrophin-associated proteins in Becker muscular dystrophy patients having in-frame deletions in the rod domain of dystrophin. (1993) (35)
Aberrant glycosylation of α‐dystroglycan causes defective binding of laminin in the muscle of chicken muscular dystrophy (2005) (34)
Deficiency of the 50 kDa dystrophin associated glycoprotein (adhalin) in severe autosomal recessive muscular dystrophies in children native from European countries. (1993) (34)
Gene transfer establishes primacy of striated vs. smooth muscle sarcoglycan complex in limb-girdle muscular dystrophy (2003) (34)
Purification of dystrophin‐related protein (utrophin) from lung and its identification in pulmonary artery endothelial cells (1993) (34)
Expression of dystrophin-associated proteins in dystrophin-positive muscle fibers (revertants) in Duchenne muscular dystrophy (1994) (34)
Characterization and ultrastructural localization of a novel 90-kDa protein unique to skeletal muscle junctional sarcoplasmic reticulum. (1994) (34)
Myoglobinuria and muscle pain are common in patients with limb-girdle muscular dystrophy 2I (2011) (34)
Binding of Lassa virus perturbs extracellular matrix‐induced signal transduction via dystroglycan (2012) (33)
Modulation of L-type Ca2+ current but not activation of Ca2+ release by the gamma1 subunit of the dihydropyridine receptor of skeletal muscle (2001) (33)
A beta-subunit normalizes the electrophysiological properties of a cloned N-type Ca2+ channel alpha 1-subunit. (1993) (33)
The Unfolded Protein Response Mediates Adaptation to Exercise in Skeletal Muscle through a PGC-1 a / ATF 6 a Complex (2011) (33)
Abnormal expression of laminin suggests disturbance of sarcolemma-extracellular matrix interaction in Japanese patients with autosomal recessive muscular dystrophy deficient in adhalin. (1994) (33)
Utrophin to the rescue (1996) (33)
Cloning and tissue-specific expression of the brain calcium channel beta-subunit. (1991) (32)
Loss of LARGE2 Disrupts Functional Glycosylation of α-Dystroglycan in Prostate Cancer* (2012) (32)
A common disease-associated missense mutation in alpha-sarcoglycan fails to cause muscular dystrophy in mice. (2008) (32)
Characterization of delta-sarcoglycan, a novel component of the oligomeric sarcoglycan complex involved in limb-girdle muscular dystrophy. (1996) (31)
Further evidence of Fukutin mutations as a cause of childhood onset limb-girdle muscular dystrophy without mental retardation (2009) (31)
Triadin, a linker for calsequestrin and the ryanodine receptor. (1996) (31)
in Xenopus oocytes (1995) (31)
Phenotypic heterogeneity in the stargazin allelic series (2003) (31)
A calmodulin-dependent protein kinase system from skeletal muscle sarcoplasmic reticulum. (1984) (30)
Structure of protein O-mannose kinase reveals a unique active site architecture (2016) (30)
The alpha(2)delta subunit augments functional expression and modifies the pharmacology of Ca(V)1.3 L-type channels. (2009) (30)
Involvement of Ca2+ Channel Synprint Site in Synaptic Vesicle Endocytosis (2010) (30)
Ultrastructural localization of adhalin, α‐dystroglycan and merosin in normal and dystrophic muscle (1996) (30)
Inhibition of Recombinant N-Type CaV Channels by the γ2 Subunit Involves Unfolded Protein Response (UPR)-Dependent and UPR-Independent Mechanisms (2007) (29)
Dystroglycan Maintains Inner Limiting Membrane Integrity to Coordinate Retinal Development (2017) (29)
Cell entry of Lassa virus induces tyrosine phosphorylation of dystroglycan (2013) (29)
Targeting Schwann cells by nonlytic arenaviral infection selectively inhibits myelination (2003) (29)
Labeling of high affinity ATP binding sites on the 53,000- and 160,000-dalton glycoproteins of the sarcoplasmic reticulum with the photoaffinity probe 8-N3-[alpha-32P]ATP. (1983) (28)
Anti-epileptic drugs delay age-related loss of spiral ganglion neurons via T-type calcium channel (2011) (28)
Dystroglycan controls signaling of multiple hormones through modulation of STAT5 activity (2010) (28)
114th ENMC International Workshop on Congenital Muscular Dystrophy (CMD) 17–19 January 2003, Naarden, The Netherlands: (8th Workshop of the International Consortium on CMD; 3rd Workshop of the MYO-CLUSTER project GENRE) (2003) (28)
An investigation of functional similarities between the sarcoplasmic reticulum and platelet calcium-dependent adenosinetriphosphatases with the inhibitors quercetin and calmidazolium. (1987) (28)
Biallelic Mutations in TMTC3, Encoding a Transmembrane and TPR-Containing Protein, Lead to Cobblestone Lissencephaly. (2016) (27)
Mutation Associated with an Autosomal Dominant Cone-Rod Dystrophy CORD7 Modifies RIM1-Mediated Modulation of Voltage-Dependent Ca2+ Channels (2007) (27)
Role of dystroglycan in limiting contraction-induced injury to the sarcomeric cytoskeleton of mature skeletal muscle (2016) (27)
Expression of dystrophin-associated glycoproteins and utrophin in carriers of Duchenne muscular dystrophy (1994) (27)
Glial scaffold required for cerebellar granule cell migration is dependent on dystroglycan function as a receptor for basement membrane proteins (2013) (27)
Structure, function and biosynthesis of sarcoplasmic reticulum proteins (1979) (27)
Basolateral Entry and Release of New and Old World Arenaviruses from Human Airway Epithelia (2008) (26)
Training the next generation of biomedical investigators in glycosciences. (2016) (26)
A functional AMPA receptor-calcium channel complex in the postsynaptic membrane. (2006) (25)
Gamma 1 subunit interactions within the skeletal muscle L-type voltage-gated calcium channels. (2003) (25)
Identification and characterization of proteins in sarcoplasmic reticulum from normal and failing human left ventricles. (1990) (25)
The Expression of Dystrophin‐associated Glycoproteins During Skeletal Muscle Degeneration and Regeneration. An Immunofluorescence Study (1995) (24)
Molecular analysis of the interaction of LCMV with its cellular receptor (cid:2) -dystroglycan (2001) (24)
DIDS INHIBITION OF SARCOPLASMIC RETICULUM ANION EFFLUX AND CALCIUM TRANSPORT (1980) (24)
Subunit regulation of the neuronal α 1 A Ca 2 + channel expressed in Xenopus oocytes (2005) (24)
Structural and functional correlates of a mutation in the malignant hyperthermia‐susceptible pig ryanodine receptor (1992) (24)
Mechanism of action of "ruthenium red" compounds on Ca2+ ionophore from sarcoplasmic reticulum (Ca2+ + Mg2+)- adenosine triphosphatase and lipid bilayer. (1975) (24)
Functional properties of the purified N-type Ca2+ channel from rabbit brain. (1994) (24)
Neural regulation of alpha-dystroglycan biosynthesis and glycosylation in skeletal muscle. (2000) (23)
A novel form of familial congenital muscular dystrophy in two adolescents. (1998) (22)
β-sarcoglycan : Characterization and role in limb-girdle muscular dystrophy linked to 4q12 (1996) (22)
Reactive oxygen species deglycosilate glomerular α-dystroglycan (2006) (22)
P-sarcoglycan : characterization and role in limb-girdle muscular dystrophy linked to 4 q 12 (2006) (21)
Deficiency of the 50 kDa dystrophin-associated glycoprotein and abnormal expression of utrophin in two South Asian cousins with variable expression of severe childhood autosomal recessive muscular dystrophy (1994) (21)
Congenital muscular dystrophy with glycosylation defects of alpha-dystroglycan in Japan. (2005) (21)
Opposing Roles of Integrin 6 A 1 and Dystroglycan in Laminin-mediated Extracellular Signal-regulated Kinase Activation (2003) (20)
Calcium transport by sarcoplasmic reticulum of skeletal muscle is inhibited by antibodies against the 53-kilodalton glycoprotein of the sarcoplasmic reticulum membrane. (1989) (20)
Identification of critical amino acids involved in alpha1-beta interaction in voltage-dependent Ca2+ channels. (1996) (20)
Molecular Signatures of Membrane Protein Complexes Underlying Muscular Dystrophy* (2016) (19)
Endogenous Glucuronyltransferase Activity of LARGE or LARGE2 Required for Functional Modification of α-Dystroglycan in Cells and Tissues* (2014) (19)
Albumin is a major protein component of transverse tubule vesicles isolated from skeletal muscle. (1989) (19)
212th ENMC International Workshop:: Animal models of congenital muscular dystrophies, Naarden, The Netherlands, 29–31 May 2015 (2016) (19)
Caveolin 3 Is Associated with the Calcium Release Complex and Is Modified via in Vivo Triadin Modification (2010) (19)
Disruption of the b-Sarcoglycan Gene Reveals Pathogenetic Complexity of Limb-Girdle Muscular Dystrophy Type 2 (2000) (19)
Skeletal muscle junctional membrane protein content in pigs with different ryanodine receptor genotypes. (1994) (18)
Dystroglycan overexpression in vivo alters acetylcholine receptor aggregation at the neuromuscular junction. (2000) (18)
Lethal congenital muscular dystrophy in two sibs with arthrogryposis multiplex: new entity or variant of cobblestone lissencephaly syndrome? (1996) (18)
Molecular characterization of a two‐domain form of the neuronal voltage‐gated P/Q‐type calcium channel α12.1 subunit (2002) (18)
α-Dystroglycan can mediate arenavirus infection in the absence of β-dystroglycan (2003) (18)
Biochemical and pathological changes result from mutated Caveolin-3 in muscle (2018) (18)
Evidence for a 95 kDa short form of the alpha1A subunit associated with the omega-conotoxin MVIIC receptor of the P/Q-type Ca2+ channels. (1998) (18)
α‐Dystroglycan deficiency correlates with elevated serum creatine kinase and decreased muscle contraction tension in golden retriever muscular dystrophy (1994) (17)
CLINICAL AND MOLECULAR PATHOLOGICAL FEATURES OF SEVERE CHILDHOOD AUTOSOMAL RECESSIVE MUSCULAR DYSTROPHY IN SAUDI ARABIA (1996) (17)
Localization of α-Dystroglycan on the Podocyte: from Top to Toe (2005) (17)
The dystroglycan receptor maintains glioma stem cells in the vascular niche (2019) (17)
Role of the Ryanodine Receptor of Skeletal Muscle in Excitation‐Contraction Coupling (1989) (17)
Two separate Ni2+-sensitive voltage-gated Ca2+channels modulate transretinal signalling in the isolated murine retina (2011) (16)
Assessment of the 50-kDa dystrophin-associated glycoprotein in Brazilian patients with severe childhood autosomal recessive muscular dystrophy (1994) (16)
Sarcoglycan Complex (2009) (16)
Muscular dystrophy associated with β‐dystroglycan deficiency (1996) (16)
Association of native Ca2+ channel beta subunits with the alpha 1 subunit interaction domain. (1995) (16)
From adhalinopathies to alpha-sarcoglycanopathies: An overview (1996) (16)
Uniparental disomy unveils a novel recessive mutation in POMT2 (2018) (15)
Purification and reconstitution of N-type calcium channel complex from rabbit brain. (1994) (15)
Expression of sialidase and dystroglycan in human glomerular diseases. (2010) (15)
Muscles of mice deficient in alpha-sarcoglycan maintain large masses and near control force values throughout the life span. (2005) (15)
Clinical heterogeneity of adhalin deficiency (1996) (15)
Localization of alpha-dystroglycan on the podocyte: from top to toe. (2005) (14)
γ1-Dependent Down-regulation of Recombinant Voltage-gated Ca2+ Channels (2007) (14)
216th ENMC international workshop: Clinical readiness in FKRP related myopathies January 15–17, 2016 Naarden, The Netherlands (2016) (14)
Collagen VI deficiency reduces muscle pathology, but does not improve muscle function, in the γ-sarcoglycan-null mouse (2016) (14)
Animal Model Molecular Pathogenesis of Muscle Degeneration in the d-Sarcoglycan-Deficient Hamster (1998) (14)
Analysis of the Role of Dystroglycan in Early Postimplantation Mouse Development a (1998) (14)
Dissection of Functional Domains of the Voltage-Dependent Ca 2 1 Channel a 2 d Subunit (1997) (14)
Evidence that platelet and skeletal sarcoplasmic reticulum Ca2+-ATPase are structurally distinct. (1985) (14)
Dystroglycan is involved in laminin‐1‐stimulated motility of Müller glial cells: Combined velocity and directionality analysis (2005) (14)
Adhalin gene mutations and autosomal recessive limb‐girdle muscular dystrophy (1995) (13)
A novel POMT2 mutation causes mild congenital muscular dystrophy with normal brain MRI (2009) (13)
A novel missense mutation in POMT1 modulates the severe congenital muscular dystrophy phenotype associated with POMT1 nonsense mutations (2014) (13)
Evidence for the Presence of Calsequestrin in Both Peripheral and Interior Regions of Sheep Purkinje Fibers (1984) (13)
Frog cardiac calsequestrin. Identification, characterization, and subcellular distribution in two structurally distinct regions of peripheral sarcoplasmic reticulum in frog ventricular myocardium. (1991) (12)
LARGE2-dependent glycosylation confers laminin-binding ability on proteoglycans (2016) (12)
Biosynthesis of intrinsic sarcoplasmic reticulum proteins during differentiation of the myogenic cell line L6. (1983) (12)
Partial deficiency of dystrophin‐associated proteins in a young girl with sporadic myopathy and normal karyotype (1993) (12)
Adenosine A(3) receptor stimulation induces protection of skeletal muscle from eccentric exercise-mediated injury. (2010) (12)
Non-neural agrin codistributes with acetylcholine receptors during early differentiation of Torpedo electrocytes. (1996) (11)
POMK regulates dystroglycan function via LARGE1-mediated elongation of matriglycan (2020) (11)
Neurosensory hearing loss in secondary adhalinopathy. (1996) (11)
Alpha-dystroglycan can mediate arenavirus infection in the absence of beta-dystroglycan. (2003) (11)
Exercise-induced left ventricular systolic dysfunction in women heterozygous for dystrophinopathy. (2010) (11)
Expression of Deletion-Containing Dystrophins in mdx Muscle: Implications for Gene Therapy and Dystrophin Function (1995) (11)
Variability in proteoglycan synthesis among six strains of normal human adult skin fibroblasts. (1986) (10)
Chloride-induced release of actively loaded calcium from light and heavy sarcoplasmic reticulum vesicles (2005) (10)
Adhalin mRNA and cDNA sequence are normal in the cardiomyopathic hamster (1995) (10)
Clinical utility of RNA sequencing to resolve unusual GNE myopathy with a novel promoter deletion (2019) (10)
Protective role for the N-terminal domain of α-dystroglycan in Influenza A virus proliferation (2019) (10)
MG53′s new identity (2013) (10)
Muscular dystrophy associated with beta-Dystroglycan deficiency. (1996) (10)
Cell surface glycan engineering reveals that matriglycan alone can recapitulate dystroglycan binding and function (2021) (9)
Molecular characterization of a two-domain form of the neuronal voltage-gated P/Q-type calcium channel alpha(1)2.1 subunit. (2002) (9)
Exogenous expression of the glycosyltransferase LARGE1 restores α-dystroglycan matriglycan and laminin binding in rhabdomyosarcoma (2019) (9)
Antibodies against the Calcium-Binding Protein: Calsequestrin from Streptanthus tortuosus (Brassicaceae). (1989) (9)
The α 2 δ subunit augments functional expression and modifies the pharmacology of CaV1.3 L-type channels (2010) (9)
Adhalin gene polymorphism. (1994) (9)
Variable disease severity in Saudi Arabian and Sudanese families with c.3924 + 2 T > C mutation of LAMA2 (2011) (9)
Phosphorylation of heavy sarcoplasmic reticulum vesicles: Identification and characterization of three phosphorylated proteins (1980) (9)
Exome sequencing reveals independent SGCD deletions causing limb girdle muscular dystrophy in Boston terriers (2017) (9)
Reactive oxygen species deglycosilate glomerular alpha-dystroglycan. (2006) (9)
Specific Absence of the a1 Subunit of the Dihydropyridine Receptor in Mice with Muscular (1989) (8)
220th ENMC workshop: Dystroglycan and the dystroglycanopathies Naarden, The Netherlands, 27–29 May 2016 (2017) (8)
dystroglycan modification are conserved in LARGE2 (2012) (8)
Functional Glycosylation of Dystroglycan Is Crucial for Thymocyte Development in the Mouse (2010) (8)
Limb-girdle muscular dystrophies. (2002) (8)
Skeletal Muscle - one year on (2012) (8)
Radioimmunoassay for the calcium release channel agonist ryanodine. (1994) (8)
Muscular dystrophy. Utrophin to the rescue. (1996) (8)
HNK-1 Sulfotransferase modulates α-dystroglycan glycosylation by 3-O-sulfation of glucuronic acid on matriglycan. (2020) (8)
Identification of muscle-specific calpain and β-sarcoglycan genes in progressive autosomal recessive muscular dystrophies (1996) (7)
Exome sequencing reveals independent SGCD deletions causing limb girdle muscular dystrophy in Boston terriers (2017) (7)
Dynamic Dystroglycan Complexes Mediate Cell Entry of Lassa Virus (2019) (7)
Affinity Purification of Antibodies Specific for 1,4‐Dihydropyridine Ca2+ Channel Blockers (1987) (6)
The dystrophin-glycoprotein complex: identification and biochemical characterization (1991) (6)
The 'sniffer-patch' technique for detection of neurotransmitter release (1997) (6)
227th ENMC International Workshop: Finalizing a plan to guarantee quality in translational research for neuromuscular diseases Heemskerk, Netherlands, 10–11 February 2017 (2017) (5)
32,000‐Dalton Subunit of the 1,4‐Dihydropyridine Receptor a (1989) (5)
Ca2+ Channel Antibodies: Subunit-Specific Antibodies as Probes for Structure and Function (1988) (5)
Distribution of ot-Dystroglycan during Embryonic Nerve-Muscle Synaptogenesis (2003) (5)
Improved genotyping of the dysferlin null mouse (2011) (5)
High-affinity antibodies to the 1,4-dihydropyridine Ca2+-channel blockers. (1986) (5)
Structural characterization of the nitrendipine receptor of the voltage-dependent Ca2+ channel: evidence for a 52,000 dalton subunit. (1988) (4)
Structure and mechanism of LARGE1 matriglycan polymerase (2022) (4)
Single base polymorphism in the DAG1 gene detected by DGGE and mismatch PCR. (1993) (4)
Primary adhalinopathy (α‐sarcoglycanopathy) (1997) (4)
Lassa Fever Virus Binds Matriglycan—A Polymer of Alternating Xylose and Glucuronate—On α-Dystroglycan (2021) (4)
Dystroglycan: Extracellular Matrix Receptor that Links to Cytoskeleton (2015) (4)
PROTEIN COMPONENTS AND THEIR ROLES IN SARCOPLASMIC RETICULUM FUNCTION (2005) (4)
Flickery block of the purified ryanodine receptor by ruthenium red tetraammine palladium and tetraammine platinum (1989) (3)
Muscular dystrophy-dystroglycanopathy in a family of Labrador retrievers with a LARGE1 mutation (2021) (3)
Characterisation of Antibody Models of the Ryanodine Receptor for Use in High-Throughput Screening (1998) (2)
Evidence for a 95 kDa Short Form of the a 1 A Subunit Associated with the v-Conotoxin MVIIC Receptor of the P / Q-type Ca 2 1 Channels (1997) (2)
A novel missense mutation in POMT 1 modulates the severe congenital muscular dystrophy phenotype associated with POMT 1 nonsense mutations (2014) (2)
BRIEF REPORT A Dystroglycan Mutation Associated with Limb-Girdle Muscular Dystrophy (2011) (2)
A unique variant of lymphocytic choriomeningitis virus that induces pheromone binding protein MUP: Critical role for CTL (2019) (2)
Program and abstracts for the 2012 Joint Meeting of the Society for Glycobiology & American Society for Matrix Biology (2012) (2)
Program and abstracts for the 2012 Joint Meeting of the Society for Glycobiology & American Society for Matrix Biology (2012) (2)
Third International Workshop for Glycosylation Defects in Muscular Dystrophies, 18–19 April 2013, Charlotte, USA (2014) (2)
Genetic characterization and improved genotyping of the dysferlin-deficient mouse strain Dysftm1Kcam (2015) (2)
release by the gamma 1 subunit of the dihydropyridine receptor of skeletal muscle (2001) (2)
LATE BREAKING NEWS E-POSTER PRESENTATION (2020) (1)
Tubules of Cardiac Muscle (2005) (1)
(cid:1) 1 Subunit Interactions within the Skeletal Muscle L-type Voltage-gated Calcium Channels* (2002) (1)
Illuminating regeneration: noninvasive imaging of disease progression in muscular dystrophy. (2013) (1)
Unraveling the ribbon synapse (2008) (1)
chapter 17 – Molecular Pathways for Dilated Cardiomyopathy (2004) (1)
Identification of Two Intrinsic Proteins Uniquely Associated with the Terminal Cisternae of the Sarcoplasmic Reticulum (2005) (1)
Monoclonal Antibody Characterization of the 1,4‐Dihydropyridine Receptor of Rabbit Skeletal Muscle (1988) (1)
Structural Analysis of the Voltage-Dependent Calcium Channel Beta Subunit Functional Core in Complex with Alpha1 Interaction Domain (2004) (1)
Investigations of an inducible intact dystrophin gene excision system in cardiac and skeletal muscle in vivo (2020) (1)
Overlay and Bead Assay (1998) (1)
The identification of sarcoplasmic reticulum terminal cisternae proteins in platelets. (1989) (1)
Report: Fourth International Workshop for Glycosylation Defects inMuscular Dystrophies (2016) (1)
Dystrophin and nnos double knockout mice maintain dystrophic phenotype (1997) (1)
O.1 Novel O-mannosyl phosphorylation of alpha-dystroglycan is required for laminin binding: implications for congenital muscular dystrophy (2010) (1)
A syntrophin gene maps to mouse Chromosome 8 and is not the myodystrophy gene (1995) (1)
Glial scaffold required for cerebellar granule cell migration is dependent on dystroglycan function as a receptor for basement membrane proteins (2013) (1)
G.P.2 Mutations in the human isoprenoid synthase domain containing gene are a common cause of congenital and limb girdle muscular dystrophies (2012) (1)
Chapter 66 – Skeletal Muscle Dystrophin-Glycoprotein Complex and Muscular Dystrophy (2012) (1)
Congenital Muscular Dystrophy and Hypoglycosylation of a-Dystroglycan (2013) (1)
Old World and Clade C New World Arenaviruses Mimic the Molecular Mechanism of Receptor Recognition Used by (cid:2) -Dystroglycan’s Host-Derived Ligands (cid:1) (2007) (1)
Overlay and bead assay. Determination of calcium channel subunit interaction domains. (1998) (1)
Anti‐dihydropyridine Antibodies Exhibit [3H]Nitrendipine Binding Properties Similar to the Membrane Receptor for the 1,4‐Dihydropyridine Ca2+ Channel Antagonists (1987) (1)
United States Patent ( 19 ) Campbell et al . 54 MEASURING NON-DYSTROPHIN PROTEINS AND DAGNOSING MUSCULAR DYSTROPHY 75 ) Inventors : (2017) (0)
Chapter 4 Calsequestrin (2005) (0)
LARGE repression in epithelium-derived cancer (2009) (0)
Reciprocal roles of T-type calcium channel subtypes in processing nociceptive signals (2004) (0)
Molecular cloning of the 53000 dalton glycoprotein of the sarcoplasmic reticulum (1988) (0)
Immunogold localization of adhalin, alpha-dystroglycan and laminin in normal and dystrophic skeletal muscle. (1996) (0)
Exogenous expression of the glycosyltransferase LARGE1 restores α-dystroglycan matriglycan and laminin binding in rhabdomyosarcoma (2019) (0)
P01.07 The Dystroglycan Complex Promotes Mesenchymal-Like Glioblastoma through Interaction with EphA Receptor Tyrosine Kinases (2017) (0)
Structural Basis of Dystroglycan Function and the Pathogenesis of Muscular Dystrophy (2020) (0)
Abstracts of the 8th Meeting of the Italian Peripheral Nerve Study Group: 23 (2003) (0)
Molecular Physiology and Biophysics (2017) (0)
Defining Dystrophin-Specific T Cells in DMD Population (S15.001) (2012) (0)
Investigations of an inducible intact dystrophin gene excision system in cardiac and skeletal muscle in vivo (2020) (0)
Inamori Activities of LARGE Dystroglycan Function Requires Xylosyl-and Glucuronyltransferase (2013) (0)
Isolation of the ω-conotoxin receptor from rabbit brain using affinity chromatography with a monoclonal antibody (1992) (0)
251. rAAV-Mediated Gene Therapy To Treat Limb Girdle Muscular Dystrophy Type 2D (LGMD-2D) (2004) (0)
N-terminal domain on dystroglycan enables LARGE1 to extend matriglycan on α-dystroglycan and prevents muscular dystrophy (2023) (0)
Author response: The glucuronyltransferase B4GAT1 is required for initiation of LARGE-mediated α-dystroglycan functional glycosylation (2014) (0)
Laminin A2LG45 C-form, G6/7 bound. (2016) (0)
Rate of force recovery immediately following lengthening contractions for various mouse models of muscular dystrophy (2012) (0)
Contractile properties of mice deficient in dystrophin and the NADPH subunit p47phox (2012) (0)
Isolation of a cellular receptor for lymphocytic choriomeningitis virus and Lassa fever virus (1999) (0)
Monoclonal antibodies against the dihydropyridine receptor from rabbit skeletal muscle (1987) (0)
The bioclemistry and molecular biology of the di sensiti've aldum dlamel (1988) (0)
Mouse fukutin deletion recapitulates dystroglycanopathy phenotypic variability and impairs dystroglycan processing downstream of O-mannose phosphorylation (2012) (0)
Evidence forthe Presence ofCalsequestrin inTwo StructurallyDifferentRegionsof Myocardial SarcoplasmicReticulum (2005) (0)
TMIC-01. THE DYSTROGLYCAN RECEPTOR MAINTAINS GLIOMA STEM CELLS IN THE VASCULAR NICHE (2019) (0)
Deficiency of merosin in dystrophic dy mouse homologue of congenital muscular dystrophy (1994) (0)
POMK regulates dystroglycan function via LARGE-mediated elongation of matriglycan (2020) (0)
Effects of CaMKII activity on cardiac and skeletal muscle pathology in a mouse model of Duchenne muscular dystrophy (1102.3) (2014) (0)
Biochemical and pathological changes result from mutated Caveolin-3 in muscle (2018) (0)
Mutational diversity andhotspotsinthe u-sarcoglycan gene inautosomal recessive muscular dystrophy (LGMD2D) (2011) (0)
Modulation of Nociceptive Signals by α1G and α1H T-Type Calcium Channels (2004) (0)
CorrectionAn HMGA2-IGF2BP2 Axis Regulates Myoblast Proliferation and Myogenesis (2013) (0)
Author response: The functional O-mannose glycan on α-dystroglycan contains a phospho-ribitol primed for matriglycan addition (2016) (0)
Molecular Basis for Dystroglycan Binding to Laminin‐G Domain‐Containing Ligands (2013) (0)
Frog Cardiac Calsequestrin (2005) (0)
MP21-13 A SURVEY OF FERTILITY AND FATHERHOOD AMONG US MALE SURGEONS: AN UNDERREPRESENTED AND UNDERSTUDIED COHORT (2021) (0)
Response to the letter: “On the localization of ClC-1 in skeletal muscle fibers” (2011) (0)
POSSIBLE SITES OF ION FLOW IN THE SARCOPLASMIC RETICULUM MEMBRANE (2005) (0)
Laminin A2LG45 C-form, Apo. (2016) (0)
Sarcoglycan Complex IMPLICATIONSFORMETABOLICDEFECTS INMUSCULARDYSTROPHIES (2009) (0)
EM.O.2 Residual laminin-binding activity and enhanced dystroglycan glycosylation by LARGE in novel model mice to dystroglycanopathy (2009) (0)
D.I.4 Patient fibroblast functional complementation studies: A valuable tool in the identification of novel Walker–Warburg syndrome disease genes (2012) (0)
Abstract 996: Loss of alpha-dystroglycan laminin binding in epithelium-derived cancers is caused by silencing ofLARGE (2010) (0)
High-affinity antibodies to the 1 , 4-dihydropyridine Ca 2 +-channel blockers ( nitrendipine / nifedipine / nisoldipIne / Ca 2 ' antgonsts / dihydropyridlne receptor ) (2003) (0)
Abstract 421: Dystroglycan glycosylation status predicts Gleason grade and influences prostate tumor growth (2010) (0)
Genetic characterization and improved genotyping of the dysferlin-deficient mouse strain Dysftm1Kcam (2015) (0)
Dystroglycan N-terminal domain enables LARGE1 to extend matriglycan on α-dystroglycan and prevents muscular dystrophy (2022) (0)
Genetic, allelic and phenotypic heterogeneity of muscular dystrophies with primary and secondary involvement of adhalin (alpha-sarcoglycan) (1996) (0)
C.I.1 Congenital muscular dystrophy and dystroglycan glycosylation (2007) (0)
MP21-02 TESTICULAR CORE BIOPSY: A NEW PARADIGM FOR THE DIFFERENTIAL DIAGNOSIS OF AZOOSPERMIA (2021) (0)
Channel Antibodies : Subunit-Specific Antibodies as Probes for Structure and Function (2005) (0)
CONGENITAL MYOPATHIES: NEMALINE AND TITINOPATHIES P.227Unraveling muscle slowness in NEM6 myopathy: a key role for the skeletal muscle thin filament (2018) (0)
Biochemical and Morphological Characterization of Light and Heavy Sarcoplasmic Reticulum Vesicles (1978) (0)
Author response: POMK regulates dystroglycan function via LARGE1-mediated elongation of matriglycan (2020) (0)
Like-Glycosyltransferase; Glycosyltransferase-Like 1B (LARGE, GYLTL1B) (2014) (0)
Progressive Muscular Dystrophy in (cid:97) -Sarcoglycan–deficient Mice (1998) (0)
G.P.276 Clinical summary of eight unrelated individuals with GMPPB mutations (2015) (0)
SEVERE MUSCULAR DYSTROPHY AND CARDIOMYOPATHY IN MICE DEFICIENT IN DELTA-SARCOGLYCAN (1999) (0)
Alpha-Dystroglycan Supports Platelet Aggregation and Thrombus Formation. (2019) (0)
Structural Basis of Dystroglycan Function and the Pathogenesis of Muscular Dystrophy (2020) (0)
491. Improved Apical Airway Epithelia Targeting Properties of FIV Vector Pseudotyped with Envelopes from LCMV (2004) (0)
Skeletal muscle’s 3rd year anniversary (2014) (0)
Abnormal tracheal cartilage formation in mice lacking Cav3.2 T‐type Ca2+ channels (540.3) (2014) (0)
Skeletal muscle’s 3rd year anniversary (2014) (0)
Molecular Basis of Muscular Dystrophy and Approaches to Therapy (2007) (0)
MG53′s new identity (2013) (0)
Peripheral nerve dystroglycan : its function and potential role in the molecular pathogenesis of neuromuscular diseases (2006) (0)
LATE BREAKING NEWS E-POSTER PRESENTATION LBP 11 Congenital Muscular Dystrophy Type 1D (α-Dystroglycanopathy) in a Family of Labrador Retrievers with a Stop Codon Mutation in LARGE1 Gene (2020) (0)
P.162Novel Kbtbd13 R408C-knockin mouse model phenocopies NEM6 myopathy (2019) (0)
PNAS Plus Significance Statements (2014) (0)
[Function of dystroglycan in the nervous system]. (2004) (0)
Functional Consequences of Large1 Overexpression in Two Distinct Forms of Muscular Dystrophy (2010) (0)
Large1 gene transfer in older myd mice with severe muscular dystrophy restores muscle function and greatly improves survival (2021) (0)
[Complete deficiency of adhalin (50 kDa DAG) in skeletal muscle of malignant limb-girdle muscular dystrophy]. (1995) (0)
This Week in The Journal F Cellular / Molecular Calcium Channels Interact With Endocytic Proteins (2010) (0)
Functional O‐Mannosylation of α‐Dystroglycan: Trisaccharide‐phospho‐ribitol Primed for Matriglycan Addition (2016) (0)
United States Patent ( 19 ) Campbell et al . 54 DIHYDROPYRIDINE RECEPTOR AND ANTBODES THERETO (2017) (0)
Dystroglycan function at CCK-positive terminals (0)
Vectors Cells by Feline Immunodeficiency Virus Transduction of Dividing and Nondividing Minimum Requirements for Efficient (2013) (0)
MP21-11 A FELLOW'S FATE: OUTCOMES OF ANDROLOGY FELLOWSHIP TRAINING (2021) (0)
Linkage analysis offamilies withsevere childhood autosomal recessive muscular dystrophy inMoroccoindicates genetic homogeneity ofthedisease inNorthAfrica (1994) (0)
LARGE1 Processively Polymerizes Matriglycan Using Active Sites on Alternate Protomers (2022) (0)
MP21-18 IT'S NOT ABOUT TIME: DOES ABSTINENCE ALTER SEMINAL OXIDATIVE STRESS OR DNA FRAGMENTATION RATES? (2021) (0)
Abstract 2289: Dystroglycan Function in Cardiac Myocytes is Required for Prevention of Cardiac Myocyte Sarcolemma Damage (2009) (0)
Heterogeneity of A d h h Deficiency (2006) (0)
44. Development of AAV-Mediated Gene Therapy for Murine Models of Genetic Diseases Affecting the Heart (2005) (0)

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