Matthias Griese
#155,815
Most Influential Person Now
Researcher
Matthias Griese's AcademicInfluence.com Rankings
Matthias Griesecomputer-science Degrees
Computer Science
#8555
World Rank
#8993
Historical Rank
Machine Learning
#3533
World Rank
#3577
Historical Rank
Artificial Intelligence
#3842
World Rank
#3898
Historical Rank
Database
#5555
World Rank
#5764
Historical Rank
Download Badge
Computer Science
Why Is Matthias Griese Influential?
(Suggest an Edit or Addition)Matthias Griese's Published Works
Number of citations in a given year to any of this author's works
Total number of citations to an author for the works they published in a given year. This highlights publication of the most important work(s) by the author
Published Works
- A CFTR potentiator in patients with cystic fibrosis and the G551D mutation. (2011) (1829)
- Expression of therapeutic proteins after delivery of chemically modified mRNA in mice (2011) (591)
- Pulmonary surfactant in health and human lung diseases: state of the art. (1999) (484)
- Quantitative and functional impairment of pulmonary CD4+CD25hi regulatory T cells in pediatric asthma. (2007) (411)
- The Human Phenotype Ontology in 2021 (2020) (373)
- A Genome-wide Search for Linkage to Asthma (1999) (353)
- Cleavage of CXCR1 on neutrophils disables bacterial killing in cystic fibrosis lung disease (2007) (328)
- DNAH5 mutations are a common cause of primary ciliary dyskinesia with outer dynein arm defects. (2006) (304)
- DYX1C1 is required for axonemal dynein assembly and ciliary motility (2013) (252)
- An official American Thoracic Society research statement: noninfectious lung injury after hematopoietic stem cell transplantation: idiopathic pneumonia syndrome. (2011) (244)
- Mutations in CCNO result in congenital mucociliary clearance disorder with reduced generation of multiple motile cilia (2014) (217)
- CXCR2 mediates NADPH oxidase–independent neutrophil extracellular trap formation in cystic fibrosis airway inflammation (2010) (216)
- Infiltrated Neutrophils Acquire Novel Chemokine Receptor Expression and Chemokine Responsiveness in Chronic Inflammatory Lung Diseases (2008) (205)
- Long-term safety and efficacy of ivacaftor in patients with cystic fibrosis who have the Gly551Asp-CFTR mutation: a phase 3, open-label extension study (PERSIST). (2014) (193)
- Ultrastructural characterization of cystic fibrosis sputum using atomic force and scanning electron microscopy. (2012) (178)
- Effect of treatment with dornase alpha on airway inflammation in patients with cystic fibrosis. (2004) (170)
- European protocols for the diagnosis and initial treatment of interstitial lung disease in children (2015) (168)
- Pulmonary TH2 response in Pseudomonas aeruginosa–infected patients with cystic fibrosis (2006) (165)
- Changes of exhaled nitric oxide during steroid treatment of childhood asthma (1999) (163)
- α1-Antitrypsin inhalation reduces airway inflammation in cystic fibrosis patients (2006) (154)
- Interstitial lung disease in a baby with a de novo mutation in the SFTPC gene (2004) (144)
- Alteration of the pulmonary surfactant system in full-term infants with hereditary ABCA3 deficiency. (2006) (142)
- Pulmonary surfactant in cystic fibrosis. (1997) (136)
- Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del‐CFTR or F508del/G551D‐CFTR (2018) (135)
- A genome-wide search for linkage to asthma. German Asthma Genetics Group. (1999) (134)
- Mutations in SPAG1 cause primary ciliary dyskinesia associated with defective outer and inner dynein arms. (2013) (132)
- Pulmonary complications after bone marrow transplantation in children: Twenty‐four years of experience in a single pediatric center (2000) (129)
- Mutation of SFTPC in infantile pulmonary alveolar proteinosis with or without fibrosing lung disease (2004) (127)
- Surfactant protein D in human lung diseases (2006) (123)
- Pulmonary T(H)2 response in Pseudomonas aeruginosa-infected patients with cystic fibrosis. (2006) (119)
- Improvement of alveolar glutathione and lung function but not oxidative state in cystic fibrosis. (2004) (117)
- In vivo genome editing using nuclease-encoding mRNA corrects SP-B deficiency (2015) (111)
- Inhibition of airway proteases in cystic fibrosis lung disease (2008) (101)
- The role of matrix metalloproteinases in cystic fibrosis lung disease (2011) (99)
- Pulmonary alveolar proteinosis: new insights from a single-center cohort of 70 patients. (2011) (99)
- Incidence and classification of pediatric diffuse parenchymal lung diseases in Germany (2009) (99)
- Bronchoalveolar pepsin, bile acids, oxidation, and inflammation in children with gastroesophageal reflux disease. (2007) (96)
- Lung disease caused by ABCA3 mutations (2016) (95)
- Free DNA in Cystic Fibrosis Airway Fluids Correlates with Airflow Obstruction (2015) (92)
- TLR Expression on Neutrophils at the Pulmonary Site of Infection: TLR1/TLR2-Mediated Up-Regulation of TLR5 Expression in Cystic Fibrosis Lung Disease1 (2008) (91)
- Chemokines indicate allergic bronchopulmonary aspergillosis in patients with cystic fibrosis. (2006) (88)
- A large kindred of pulmonary fibrosis associated with a novel ABCA3 gene variant (2014) (88)
- Whole lung lavage therapy for pulmonary alveolar proteinosis: a global survey of current practices and procedures (2016) (85)
- The antimicrobial peptide cathelicidin interacts with airway mucus (2006) (83)
- Some ABCA3 mutations elevate ER stress and initiate apoptosis of lung epithelial cells (2011) (79)
- Pulmonary chemokines and their receptors differentiate children with asthma and chronic cough. (2005) (79)
- Inhalation treatment with glutathione in patients with cystic fibrosis. A randomized clinical trial. (2013) (78)
- Respiratory disease in Niemann‐Pick type C2 is caused by pulmonary alveolar proteinosis (2010) (77)
- TTC25 Deficiency Results in Defects of the Outer Dynein Arm Docking Machinery and Primary Ciliary Dyskinesia with Left-Right Body Asymmetry Randomization. (2016) (77)
- Pulmonary alveolar proteinosis. (2004) (76)
- Biallelic Mutations of Methionyl-tRNA Synthetase Cause a Specific Type of Pulmonary Alveolar Proteinosis Prevalent on Réunion Island. (2015) (76)
- Surfactant protein A and other bronchoalveolar lavage fluid proteins are altered in cystic fibrosis. (2001) (76)
- Pulmonary surfactant, lung function, and endobronchial inflammation in cystic fibrosis. (2004) (75)
- Interstitial lung disease in children – genetic background and associated phenotypes (2005) (73)
- The risk of hemophagocytic lymphohistiocytosis in Hermansky-Pudlak syndrome type 2. (2013) (72)
- Protein pattern of exhaled breath condensate and saliva (2002) (72)
- Surfactant protein A and D differently regulate the immune response to nonmucoid Pseudomonas aeruginosa and its lipopolysaccharide. (2003) (70)
- Bronchoalveolar lavage fluid findings in children with hypersensitivity pneumonitis (2003) (66)
- Comprehensive genotyping and clinical characterisation reveal 27 novel NKX2-1 mutations and expand the phenotypic spectrum (2014) (65)
- Microbial colonization and lung function in adolescents with cystic fibrosis. (2016) (63)
- Oxidative changes of bronchoalveolar proteins in cystic fibrosis. (2006) (60)
- GATA2 deficiency in children and adults with severe pulmonary alveolar proteinosis and hematologic disorders (2015) (60)
- Surfactant proteins A and D in children with pulmonary disease due to gastroesophageal reflux. (2002) (59)
- Genotype alone does not predict the clinical course of SFTPC deficiency in paediatric patients (2015) (58)
- Sequential genotyping of Pseudomonas aeruginosa from upper and lower airways of cystic fibrosis patients (2002) (57)
- Inhaled glutathione decreases PGE2 and increases lymphocytes in cystic fibrosis lungs. (2005) (57)
- Pulmonary alveolar proteinosis (2019) (55)
- Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor for 24 Weeks or Longer in People with Cystic Fibrosis and One or More F508del Alleles: Interim Results of an Open-Label Phase 3 Clinical Trial (2020) (53)
- Proteolysis of Surfactant Protein D by Cystic Fibrosis Relevant Proteases (2003) (53)
- Cardiopulmonary bypass reduces pulmonary surfactant activity in infants. (1999) (53)
- Biomarker discovery from body fluids using mass spectrometry. (2007) (52)
- Reduced proteolysis of surfactant protein A and changes of the bronchoalveolar lavage fluid proteome by inhaled α1‐protease inhibitor in cystic fibrosis (2001) (52)
- Clinical trials in cystic fibrosis. (2007) (52)
- International management platform for children’s interstitial lung disease (chILD-EU) (2017) (51)
- Characterization of CSF2RA mutation related juvenile pulmonary alveolar proteinosis (2014) (51)
- Hydroxychloroquine in children with interstitial (diffuse parenchymal) lung diseases (2015) (49)
- Expression, regulation and clinical significance of soluble and membrane CD14 receptors in pediatric inflammatory lung diseases (2010) (49)
- Analysis of 40 sporadic or familial neonatal and pediatric cases with severe unexplained respiratory distress: Relationship to SFTPB (2003) (49)
- Diagnostic and prognostic value of serum antibodies against Pseudomonas aeruginosa in cystic fibrosis (2006) (49)
- Compound SFTPB 1549C→GAA (121ins2) and 457delC heterozygosity in severe congenital lung disease and surfactant protein B (SP‐B) deficiency (1999) (48)
- Persistent Tachypnea of Infancy. Usual and Aberrant. (2016) (48)
- Anti-GM-CSF antibodies in paediatric pulmonary alveolar proteinosis (2004) (48)
- Phenotype characterisation of TBX4 mutation and deletion carriers with neonatal and paediatric pulmonary hypertension (2019) (48)
- Lung function in adults with cystic fibrosis at altitude: impact on air travel (2005) (48)
- Hypersensitivity pneumonitis: lessons for diagnosis and treatment of a rare entity in children (2013) (46)
- The Chitinase-Like Protein YKL-40 Modulates Cystic Fibrosis Lung Disease (2011) (46)
- A role for MCP-1/CCR2 in interstitial lung disease in children (2005) (45)
- Innate immune receptors on neutrophils and their role in chronic lung disease (2009) (44)
- Airway inflammation in children with tracheostomy (2004) (44)
- Surfactant protein D in serum from patients with allergic bronchopulmonary aspergillosis (2003) (43)
- Respiratory syncytial virus and pulmonary surfactant. (2002) (43)
- A noninvasive method to collect nasally exhaled air condensate in humans of all ages (2001) (42)
- Exhaled nitric oxide in healthy children: variability and a lack of correlation with atopy. (2002) (42)
- Anti-inflammatory cytokines in cystic fibrosis lung disease (2006) (42)
- Pharmacokinetics of bovine surfactant in neonatal respiratory distress syndrome. (1995) (41)
- Optimum peripheral drug deposition in patients with cystic fibrosis. (2005) (41)
- Pathogenesis, imaging and clinical characteristics of CF and non-CF bronchiectasis (2018) (40)
- Feasibility and Variability of Measuring the Lung Clearance Index in a Multi‐Center Setting (2012) (40)
- Acid and non-acid gastro-esophageal refluxes in children with chronic pulmonary diseases. (2007) (39)
- Eradication of initial Pseudomonas aeruginosa colonization in patients with cystic fibrosis. (2002) (39)
- Fatal neonatal respiratory failure in an infant with congenital hypothyroidism due to haploinsufficiency of the NKX2-1 gene: alteration of pulmonary surfactant homeostasis (2010) (38)
- Diversity of the basic defect of homozygous CFTR mutation genotypes in humans (2007) (38)
- Categorizing diffuse parenchymal lung disease in children (2015) (37)
- Fractional analysis of bronchoalveolar lavage fluid cytology in cystic fibrosis patients with normal lung function. Bronchoalveolar lavage for the evaluation of anti-inflammatory treatment (BEAT) study group. (2000) (37)
- Limited proteolysis of surfactant protein D causes a loss of its calcium-dependent lectin functions. (2003) (36)
- Oxidative stress in cystic fibrosis lung disease: an early event, but worth targeting? (2014) (36)
- ATP-stimulated inositol phospholipid metabolism and surfactant secretion in rat type II pneumocytes. (1991) (36)
- Pulmonary Alveolar Proteinosis: A Comprehensive Clinical Perspective (2017) (35)
- Surfactant Lipidomics in Healthy Children and Childhood Interstitial Lung Disease (2015) (35)
- Myocardial performance and free energy of ATP-hydrolysis in isolated rat hearts during graded hypoxia, reoxygenation and high Ke+-perfusion. (1988) (35)
- Therapeutic lung lavages in children and adults (2005) (35)
- Long-term follow-up and treatment of congenital alveolar proteinosis (2011) (34)
- Niemann-Pick Type C-2 Disease: Identification by Analysis of Plasma Cholestane-3β,5α,6β-Triol and Further Insight into the Clinical Phenotype. (2015) (34)
- Serum KL-6 is a predictor of outcome in pulmonary alveolar proteinosis (2013) (34)
- Exhaled breath condensate (2004) (34)
- WS7.3 VX-661, an investigational CFTR corrector, in combination with ivacaftor, a CFTR potentiator, in patients with CF and homozygous for the F508Del-CFTR mutation: Interim analysis (2013) (34)
- Ontogeny of surfactant secretion in type II pneumocytes from fetal, newborn, and adult rats. (1992) (34)
- Early onset children's interstitial lung diseases: Discrete entities or manifestations of pulmonary dysmaturity? (2019) (33)
- Status of plasma and erythrocyte fatty acids and vitamin A and E in young children with cystic fibrosis. (1988) (33)
- Serum YKL-40 as predictor of outcome in hypersensitivity pneumonitis (2017) (33)
- Surfactant protein D regulates chemotaxis and degranulation of human eosinophils (2006) (32)
- A non-BRICHOS surfactant protein c mutation disrupts epithelial cell function and intercellular signaling (2010) (32)
- Assessment of the multiplex PCR-based assay Unyvero pneumonia application for detection of bacterial pathogens and antibiotic resistance genes in children and neonates (2017) (31)
- The surfactant lipid transporter ABCA3 is N‐terminally cleaved inside LAMP3‐positive vesicles (2010) (31)
- Efficacy and safety of intravenous meropenem and tobramycin versus ceftazidime and tobramycin in cystic fibrosis. (2008) (31)
- Management of children with interstitial lung diseases: the difficult issue of acute exacerbations (2016) (31)
- Bi-allelic Mutations in Phe-tRNA Synthetase Associated with a Multi-system Pulmonary Disease Support Non-translational Function (2018) (31)
- Exhaled hydrogen peroxide, nitrite and nitric oxide in healthy children: decrease of hydrogen peroxide by atmospheric nitric oxide. (2002) (30)
- Oxidative damage to surfactant protein D in pulmonary diseases (2006) (30)
- Eradication of methicillin resistant Staphylococcus aureus detected for the first time in cystic fibrosis: A single center observational study (2016) (30)
- Chitinase activation in patients with fungus-associated cystic fibrosis lung disease. (2016) (30)
- Signal-transduction mechanisms of ATP-stimulated phosphatidylcholine secretion in rat type II pneumocytes: interactions between ATP and other surfactant secretagogues. (1993) (30)
- Clonal analysis of Inquilinus limosus isolates from six cystic fibrosis patients and specific serum antibody response. (2006) (30)
- A2 and P2 purine receptor interactions and surfactant secretion in primary cultures of type II cells. (1991) (30)
- SFTPC mutations cause SP‐C degradation and aggregate formation without increasing ER stress (2013) (29)
- Whole‐lung lavage in infants and children with pulmonary alveolar proteinosis (2010) (29)
- Chronic interstitial lung disease in children (2018) (28)
- Respiratory syncytial virus potentiates ABCA3 mutation-induced loss of lung epithelial cell differentiation. (2012) (28)
- Fractional analysis of bronchoalveolar lavage fluid cytology in cystic fibrosis patients with normal lung function. Bronchoalveolar lavage for the evaluation of anti-inflammatory treatment (BEAT) study group (2000) (28)
- Research in progress: put the orphanage out of business (2013) (28)
- Hermansky-Pudlak syndrome type 2 manifests with fibrosing lung disease early in childhood (2018) (28)
- Sequential analysis of surfactant, lung function and inflammation in cystic fibrosis patients (2005) (27)
- Nebulization of a bovine surfactant in cystic fibrosis: a pilot study. (1997) (27)
- Functional rescue of misfolding ABCA3 mutations by small molecular correctors (2018) (27)
- Children with absent surfactant protein D in bronchoalveolar lavage have more frequently pneumonia (2008) (27)
- CXCR1 and CXCR2 haplotypes synergistically modulate cystic fibrosis lung disease (2011) (27)
- De Novo and Inherited Pathogenic Variants in KDM3B Cause Intellectual Disability, Short Stature, and Facial Dysmorphism. (2019) (27)
- Novel Method to Process Cystic Fibrosis Sputum for Determination of Oxidative State (2009) (27)
- Asthma severity, recommended changes of inhaled therapy and exhaled nitric oxide in children: a prospective, blinded trial. (2000) (26)
- Surfactant proteins SP-B and SP-C and their precursors in bronchoalveolar lavages from children with acute and chronic inflammatory airway disease (2008) (26)
- Severe Variant of X-linked Dyskeratosis Congenita (Hoyeraal-Hreidarsson Syndrome) Causes Significant Enterocolitis in Early Infancy (2009) (26)
- Postinfectious Bronchiolitis Obliterans in Children: Diagnostic Workup and Therapeutic Options: A Workshop Report (2020) (26)
- Wash-out kinetics and efficacy of a modified lavage technique for alveolar proteinosis (2012) (26)
- Surfactant protein A--from genes to human lung diseases. (2006) (26)
- Expression profiles of hydrophobic surfactant proteins in children with diffuse chronic lung disease (2005) (26)
- Multisystem Inflammation and Susceptibility to Viral infections in Human ZNFX1 Deficiency. (2021) (26)
- Delivery of Alpha-1 Antitrypsin to Airways. (2016) (25)
- Long-Term Inhaled Granulocyte Macrophage–Colony-Stimulating Factor in Autoimmune Pulmonary Alveolar Proteinosis: Effectiveness, Safety, and Lowest Effective Dose (2014) (25)
- Elemental and ion composition of exhaled air condensate in cystic fibrosis. (2003) (25)
- Protein Oxidation by Chronic Pulmonary Diseases in Children (2006) (25)
- The basidiomycetous yeast Trichosporon may cause severe lung exacerbation in cystic fibrosis patients – clinical analysis of Trichosporon positive patients in a Munich cohort (2013) (25)
- Cathepsin H and napsin A are active in the alveoli and increased in alveolar proteinosis (2008) (25)
- Clinical characteristics of patients with familial idiopathic pulmonary fibrosis (f-IPF) (2019) (25)
- The surfactant protein C mutation A116D alters cellular processing, stress tolerance, surfactant lipid composition, and immune cell activation (2012) (25)
- Long‐term pulmonary outcome after meconium ileus in cystic fibrosis (2009) (25)
- Recombinant human DNase (rhDNase) influences phospholipid composition, surface activity, rheology and consecutively clearance indices of cystic fibrosis sputum. (1997) (24)
- Pulmonary alveolar proteinosis in children on La Réunion Island: a new inherited disorder? (2014) (24)
- Bronchoalveolar lavage protein patterns in children with malignancies, immunosuppression, fever and pulmonary infiltrates (2002) (23)
- Pulmonary interstitial glycogenosis - A systematic analysis of new cases. (2018) (23)
- Amphotericin B and pulmonary surfactant. (1998) (23)
- Smaller sized particles are preferentially taken up by alveolar type II pneumocytes. (1998) (23)
- ABCA3 missense mutations causing surfactant dysfunction disorders have distinct cellular phenotypes (2018) (23)
- Surfactant proteins in pediatric interstitial lung disease (2016) (23)
- Ursodeoxycholic acid therapy in cystic fibrosis liver disease – a retrospective long‐term follow‐up case‐control study (2012) (22)
- Histamine release test in comparison to standard tests in diagnosis of childhood allergic asthma. (1990) (22)
- Pulmonary alveolar proteinosis: time to shift? (2015) (22)
- Prospective study on nontuberculous mycobacteria in patients with and without cystic fibrosis (2004) (22)
- Quantitative Lipidomics in Pulmonary Alveolar Proteinosis. (2019) (21)
- rhKGF stimulates lung surfactant production in neonatal rats in vivo (2011) (21)
- Development and validation of a health‐related quality of life questionnaire for pediatric patients with interstitial lung disease (2018) (20)
- Heterozygous OAS1 gain-of-function variants cause an autoinflammatory immunodeficiency (2021) (19)
- ABCA3 protects alveolar epithelial cells against free cholesterol induced cell death. (2015) (19)
- Serum Levels of Surfactant Proteins in Patients with Combined Pulmonary Fibrosis and Emphysema (CPFE) (2015) (19)
- Density and agonist‐promoted high and low affinity states of the β‐adrenoceptor on human B‐ and T‐cells (1988) (19)
- Adequate Patient Characterization in COPD: Reasons to Go Beyond GOLD Classification. (2010) (18)
- Influence of salinity on energy metabolism in juvenile turbot, Psetta maxima (L.) (2013) (18)
- Increased Risk of Interstitial Lung Disease in Children with a Single R288K Variant of ABCA3 (2016) (18)
- Lung clearance index for monitoring early lung disease in alpha-1-antitrypsin deficiency. (2016) (18)
- Sternal fracture with fatal outcome in cystic fibrosis (2005) (18)
- Comparison of exhaled breath condensate from nasal and oral collection. (2003) (17)
- Surfactant lipid uptake and secretion in type II cells in response to lectins and secretagogues. (1991) (17)
- Clinical Biological and Genetic Heterogeneity of the Inborn Errors of Pulmonary Surfactant Metabolism (2001) (17)
- In-vivo data support equivalent therapeutic efficacy of a new tobramycin inhalation solution (150 mg/1.5 ml) administered by the eFlow® electronic nebuliser compared to TOBI® in the PARI LC PLUS® (2010) (17)
- Tools to explore ABCA3 mutations causing interstitial lung disease (2016) (17)
- Celiac disease and pulmonary hemosiderosis in a patient with chronic granulomatous disease (2004) (17)
- Potentiation of ABCA3 lipid transport function by ivacaftor and genistein (2019) (17)
- Surfactant subfractions during nosocomial infection in ventilated preterm human neonates. (1996) (16)
- Expression and regulation of interferon-related development regulator-1 in cystic fibrosis neutrophils. (2013) (16)
- Exhaled carbon monoxide is not flow dependent in children with cystic fibrosis and asthma. (2004) (16)
- Aberrant Processing Forms of Lung Surfactant Proteins SP–B and SP–C Revealed by High-Resolution Mass Spectrometry (2008) (15)
- Fatty acid composition of phospholipids of plasma and of mononuclear blood cells in children with allergic asthma and the influence of glucocorticoids (1990) (15)
- Neonatal Respiratory Insufficiency Caused by an (Homozygous) ABCA3-Stop Mutation: a Systematic Evaluation of Therapeutic Options (2014) (15)
- Adenosine A2-receptor-mediated phosphatidylcholine secretion in type II pneumocytes. (1991) (15)
- Surfactant in children with malignancies, immunosuppression, fever and pulmonary infiltrates (2002) (15)
- Successful treatment of neonatal respiratory failure caused by a novel surfactant protein C p.Cys121Gly mutation with hydroxychloroquine (2013) (15)
- Agglutination of Pseudomonas aeruginosa by Surfactant Protein D (2005) (15)
- Retraction: CXCR2 mediates NADPH oxidase–independent neutrophil extracellular trap formation in cystic fibrosis airway inflammation (2011) (15)
- CYTOKINE STIMULATION BY PSEUDOMONAS AERUGINOSA—STRAIN VARIATION AND MODULATION BY PULMONARY SURFACTANT (2004) (14)
- Quantification of volume and lipid filling of intracellular vesicles carrying the ABCA3 transporter. (2017) (14)
- MUC1 gene polymorphisms are associated with serum KL-6 levels and pulmonary dysfunction in pulmonary alveolar proteinosis (2013) (14)
- Serum YKL‐40 is a reliable biomarker for pulmonary alveolar proteinosis (2017) (14)
- Deleted in Malignant Brain Tumors 1 (DMBT1) is present in hyaline membranes and modulates surface tension of surfactant (2007) (14)
- Lung alveolar proteomics of bronchoalveolar lavage from a pulmonary alveolar proteinosis patient using high-resolution FTICR mass spectrometry (2007) (13)
- Health effects of sulfur-related environmental air pollution. II. Cellular and molecular parameters of injury. (1999) (13)
- The chemokine CCL18 characterises Pseudomonas infections in cystic fibrosis lung disease (2014) (13)
- Surfactant protein B deficiency caused by a novel mutation involving multiple exons of the SP-B gene. (2008) (13)
- Bi-allelic missense ABCA3 mutations in a patient with childhood ILD who reached adulthood (2019) (13)
- Surfactant function in children with chronic airway inflammation. (2004) (12)
- Lymphocytic interstitial pneumonia and follicular bronchiolitis in children: A registry‐based case series (2020) (12)
- 8-Isoprostane in nasally exhaled breath condensate in different pediatric lung diseases. (2007) (12)
- Study design of a randomised, placebo-controlled trial of nintedanib in children and adolescents with fibrosing interstitial lung disease (2021) (12)
- A Global Survey on Whole Lung Lavage in Pulmonary Alveolar Proteinosis. (2016) (12)
- Lung disease in STAT3 hyper‐IgE syndrome requires intense therapy (2019) (11)
- Glucocorticoid receptors in mononuclear blood cells and their correlation to endogenous and exogenous corticoids in healthy and asthmatic children (1988) (11)
- Inhalation of alpha(1)-protease inhibitor in cystic fibrosis does not affect surfactant convertase and surface activity. (2001) (11)
- Successful weaning from mechanical ventilation in a patient with surfactant protein C deficiency presenting with severe neonatal respiratory distress (2014) (11)
- Predictive values of antibodies against Pseudomonas aeruginosa in patients with cystic fibrosis one year after early eradication treatment. (2014) (11)
- Surfactant Function in Neonates with Respiratory Distress Syndrome (1998) (11)
- Increasing Total Serum IgE, Allergic Bronchopulmonary Aspergillosis, and Lung Function in Cystic Fibrosis. (2017) (11)
- Randomized controlled phase 2 trial of hydroxychloroquine in childhood interstitial lung disease (2022) (10)
- Persistent tachypnea of infancy: Follow up at school age (2020) (10)
- Some ABCA 3 mutations elevate ER stress and initiate apoptosis of lung epithelial cells (2011) (10)
- FARS1‐related disorders caused by bi‐allelic mutations in cytosolic phenylalanyl‐tRNA synthetase genes: Look beyond the lungs! (2020) (10)
- Rescue of respiratory failure in pulmonary alveolar proteinosis due to pathogenic MARS1 variants (2020) (10)
- Lavage lipidomics signatures in children with cystic fibrosis and protracted bacterial bronchitis. (2019) (10)
- Inhibitors of elastase in airway lavage samples from ventilated preterm human neonates. (1998) (9)
- Prospective evaluation of hydroxychloroquine in pediatric interstitial lung diseases: Study protocol for an investigator-initiated, randomized controlled, parallel-group clinical trial (2020) (9)
- Incidence and Prevalence of Children's Diffuse Lung Disease in Spain. (2021) (9)
- An informative intragenic microsatellite marker suggests the IL-1 receptor as a genetic modifier in cystic fibrosis (2017) (9)
- One-year outcomes in a multicentre cohort study of incident rare diffuse parenchymal lung disease in children (ChILD) (2019) (9)
- Endobronchial Lesions Caused by Nontuberculous Mycobacteria in Apparently Healthy Pediatric Patients (2015) (9)
- Calcium, potassium, urea and total protein are not reliable dilutional markers of bronchoalveolar small volume-lavages in ventilated preterm human neonates. (1996) (9)
- CXCR4+ granulocytes reflect fungal cystic fibrosis lung disease (2015) (8)
- Analysis of the Proteolytic Processing of ABCA3: Identification of Cleavage Site and Involved Proteases (2016) (8)
- [Cystic fibrosis care in transition from adolescence to adult age]. (2009) (8)
- Instructions for infection control in outpatient care of patients with cystic fibrosis. (2005) (8)
- Rehabilitation Programs for Cystic Fibrosis – View from a CF Center (2010) (8)
- Etiologic Classification of Diffuse Parenchymal (Interstitial) Lung Diseases (2022) (8)
- Surfactant proteins D and A in sputum. (2001) (8)
- Variation in the bombesin staining of pulmonary neuroendocrine cells in pediatric pulmonary disorders—A useful marker for airway maturity (2020) (8)
- Characteristics of flow dependency of nitric oxide in exhaled air in children with cystic fibrosis and asthma. (1999) (8)
- Pott's disease: a major issue for an unaccompanied refugee minor (2016) (8)
- Pulmonary alveolar proteinosis in a cat (2015) (8)
- Treating allergic bronchopulmonary aspergillosis with short-term prednisone and itraconazole in cystic fibrosis. (2020) (8)
- Tracheobronchial surface active material in cystic fibrosis. (1997) (8)
- Nintedanib in children and adolescents with fibrosing interstitial lung diseases (2022) (8)
- Adherence pattern to study drugs in clinical trials by patients with cystic fibrosis (2016) (7)
- Impaired Formation of the Second Messenger cAMP in Mononuclear Blood Cells of Children with Pertussis (1989) (7)
- Characterization of CSF 2 RA mutation related juvenile pulmonary alveolar proteinosis (2014) (7)
- In Vitro Inhibition of Neutrophil Elastase Activity by Inhaled Anti-Pseudomonas Antibiotics Used in Cystic Fibrosis Patients (2010) (7)
- Inhaled sargramostim and whole lung lavage (WLL) as therapy of autoimmune pulmonary alveolar proteinosis (aPAP) (2016) (7)
- Hepatopulmonary syndrome after allogeneic bone marrow transplantation (1999) (7)
- Increasing sputum levels of gamma-glutamyltransferase may identify cystic fibrosis patients who do not benefit from inhaled glutathione. (2017) (7)
- Respiratory support, surface activity and protein content during nosocomial infection in preterm neonates. (1996) (7)
- Surfactant lipid uptake and metabolism by neonatal and adult type II pneumocytes. (1999) (7)
- Quantitation of surfactant protein B by HPLC in bronchoalveolar lavage fluid. (2005) (6)
- Metabolic labelling of choline phospholipids probes ABCA3 transport in lamellar bodies. (2019) (6)
- European idiopathic pulmonary fibrosis Patient Charter: a missed opportunity (2016) (6)
- Intravenous α1-antitrypsin in a child with deficiency and severe lung disease (2009) (6)
- Skin Prick Test Reactivity to Supplemental Enzymes in Cystic Fibrosis and Pancreatic Insufficiency (2005) (6)
- Surfactant Protein A in Cystic Fibrosis: Supratrimeric Structure and Pulmonary Outcome (2012) (6)
- Signal Transduction Mechanisms Mediating Surfactant Phospholipid Secretion in Isolated Type II Cells1 (1994) (6)
- A pharmacokinetics and safety comparison of a highly concentrated tobramycin solution with TOBI. (2014) (6)
- Pulmonary function testing in children's interstitial lung disease (2020) (6)
- Inhibitory effects of pertussis toxin on the cAMP generating system in human mononuclear leucocytes (1990) (5)
- Health effects of sulfur-related environmental air pollution: the pulmonary surfactant system is not disturbed by exposure to acidic sulfate and neutral sulfite aerosols. (1999) (5)
- β-Adrenoceptor density and resolution of high and low affinity state on B- and T-cells in asthmatic and non-asthmatic children (1988) (5)
- High-content Screen Identifies Cyclosporin A as a Novel ABCA3-specific Molecular Corrector. (2021) (5)
- Life‐threatening, giant pneumatoceles in the course of surfactant protein C deficiency (2015) (5)
- Assessment of Surfactant Protein A (SP-A) dependent agglutination (2010) (5)
- Genetic testing in interstitial lung disease: An international survey (2022) (5)
- Early‐onset, fatal interstitial lung disease in STAT3 gain‐of‐function patients (2021) (4)
- Mutations in CCNO and MCIDAS lead to a mucociliary clearance disorder due to reduced generation of multiple motile cilia (2015) (4)
- European Respiratory Society statement on familial pulmonary fibrosis (2022) (4)
- WS5.1 Inhaled glutathione in cystic fibrosis (2012) (4)
- e-Flow rapid®: improved lung function and patient satisfaction with more volume delivered to the lungs during inhalation therapy in cystic fibrosis (2008) (4)
- Expanding the phenotypic spectrum of FINCA syndrome beyond infancy. (2021) (4)
- Eradication of methicillin resistant Staphylococcus aureus in cystic fibrosis (2009) (4)
- Expanding the phenotypic spectrum of FINCA (fibrosis, neurodegeneration, and cerebral angiomatosis) syndrome beyond infancy (2021) (4)
- Case Report: Unilateral Sixth Cranial Nerve Palsy Associated With COVID-19 in a 2-year-old Child (2021) (4)
- Risk of interstitial Lung Disease in Children with a Single R 288 K Variant of aBCa 3 (2016) (4)
- Influence of blood constituents on uptake of a lipid-extracted natural surfactant by alveolar type II cells. (1997) (4)
- 44 Pulmonary exacerbations in a Phase 3 trial of ivacaftor in subjects with cystic fibrosis who have the G551D-CFTR mutation (2012) (4)
- The risk of hemophagocytic lymphohistiocytosis in Hermansky (2016) (4)
- Respiratory Bronchiolitis–Associated Interstitial Lung Disease in Childhood: New Sequela of Smoking (2015) (4)
- Medication for childhood interstitial lung diseases differs internationally (2018) (4)
- Homooligomerization of ABCA3 and its functional significance. (2016) (4)
- Lung ultrasound—a new diagnostic modality in persistent tachypnea of infancy (2020) (4)
- Whole Lung Lavage Followed By Inhaled Sargramostim As Therapy Of Autoimmune Pulmonary Alveolar ProteINOSis (2016) (4)
- Analysis and optimisation of dynamic facility ventilation in recirculation aquacultural systems (2018) (4)
- The improved clinical course of persistent tachypnea of infancy with inhaled bronchodilators and corticosteroids (2021) (4)
- Airways glutathione S-transferase omega-1 and its A140D polymorphism are associated with severity of inflammation and respiratory dysfunction in cystic fibrosis. (2021) (4)
- Case Report: Pediatric Renal Sarcoidosis and Prognostic Factors in Reviewed Cases (2021) (4)
- Effects of the antiallergic drug ketotifen on bronchial resistance and beta-adrenoceptor density of lymphocytes in children with exercise-induced asthma. (1988) (4)
- Insights Into Patient Variability During Ivacaftor-Lumacaftor Therapy in Cystic Fibrosis (2021) (3)
- Cibacron blue stimulation of surfactant secretion in rat type II pneumocytes (1992) (3)
- Patient education for children with interstitial lung diseases and their caregivers: A pilot study. (2019) (3)
- Respiratory distress syndrome due to a novel homozygous ABCA3 mutation in a term neonate (2011) (3)
- ABCA3-related interstitial lung disease beyond infancy (2023) (3)
- [Pulmonary surfactant and the immune system]. (1992) (3)
- Interstitial lung disease in infancy and early childhood: a clinicopathological primer (2022) (3)
- Multicentre feasibility and variability of measuring the lung clearance index in healthy volunteers (2011) (2)
- Glucocorticoids in childhood. (1989) (2)
- COVID-19 in patients with pulmonary alveolar proteinosis: a European multicentre study (2022) (2)
- [Clinical, biological and genetic heterogeneity of the inborn errors of pulmonary surfactant metabolism: SP-B deficiency and alveolar proteinosis]. (2001) (2)
- Acute exacerbations in children’s interstitial lung disease (2022) (2)
- The adrenergic system in lymphocytes from children with cystic fibrosis (1989) (2)
- Pushing chILD Forward: The Bright Future of Children's Interstitial Lung Diseases. (2015) (2)
- Effective improvement of cystic fibrosis care by application of elementary measures: essential lessons not only for developing countries. (2008) (2)
- Pulmonary alveolar proteinosis due to heterozygous mutation in OAS1: Whole lung lavages for long‐term bridging to hematopoietic stem cell transplantation (2021) (2)
- Early pulmonary phenotype in Hermansky-Pudlak syndrome: Analysis of the chILD-EU registry (2016) (2)
- Potentiation of A2 purinoceptor-stimulated surfactant phospholipid secretion in primary cultures of rat type II pneumocytes (2004) (2)
- Uptake of a natural surfactant and increased delivery of small organic anions into type II pneumocytes. (2001) (2)
- Inhaled GM-CSF for Pulmonary Alveolar Proteinosis. (2020) (2)
- [Chronic recurrent pneumonias in ossifying bronchial carcinoid tumor]. (1987) (2)
- Chemokines indicate allergic bronchopulmonary aspergillosis in cystic fibrosis patients (2006) (2)
- Cellular association of antiproteases in lavages from ventilated preterm human neonates. (1997) (2)
- International consensus statement on quality standards for managing children/adolescents with bronchiectasis from the ERS CRC Child-BEAR-Net (2022) (2)
- Cardiovascular risk in pulmonary alveolar proteinosis (2016) (2)
- [Leprosy - An overview from a pediatric perspective]. (2001) (2)
- [Leukotriene blockade in asthma--a new anti-inflammatory therapeutic principle]. (2008) (1)
- Diffuse pulmonary development disorders- Molecular definable causes of pulmonary hypertension in the mature newborn (2015) (1)
- Diffuse alveolar haemorrhage in children: an international multicentre study (2023) (1)
- [Cellular association of antiproteases]. (1998) (1)
- 356* Use of patient monitoring systems in clinical trials to generate objective information on patients' drug adherence of inhaled medications (2011) (1)
- 815 Lung Transplantation for Children in Europe: A 10-Year Multi-Center Austrian-German Experience (2012) (1)
- Nutritional supplements in cystic fibrosis (2006) (1)
- Interventional Bronchus Occlusion Using Amplatzer Devices – A Promising Treatment Option for Children with Persistent Air Leak (2022) (1)
- WS2.9 Expression and regulation of IFRD1 in neutrophils of cystic fibrosis patients (2012) (1)
- Diagnostic workup of childhood interstitial lung disease (2023) (1)
- CR3/108--Congenital alveolar capillary dysplasia with familiary microphthalmia. (2006) (1)
- Healthcare resource utilisation and medical costs for children with interstitial lung diseases (chILD) in Europe (2022) (1)
- Identifying obstacles hindering the conduct of academic-sponsored trials for drug repurposing on rare-diseases: an analysis of six use cases (2022) (1)
- Meconium ileus—it is time to act now! (2010) (1)
- Do Not Miss Acute Diffuse Panbronchiolitis for Tree-in-Bud: Case Series of a Rare Lung Disease (2022) (1)
- Genetics in Idiopathic Pulmonary Fibrosis: A Clinical Perspective (2022) (1)
- Progressive lung disease caused by ABCA3 mutation (2020) (1)
- Histamine release from basophils in childhood: Age dependency and inhibition by pertussis infection and pertussis toxin (1993) (1)
- [The beta adrenergic system of lymphocytes in children with atopic dermatitis]. (1990) (1)
- Hypersensitivity pneumonitis: Lessons from a randomized controlled trial in children (2021) (1)
- Nintedanib in children and adolescents with fibrosing interstitial lung disease: the InPedILD trial (2022) (1)
- A survey of children’s interstitial lung disease (ChILD) databases across the EU and an ability to identify pan-registry clinical trial cohorts (2019) (1)
- Diffuse lung disease and pulmonary hypertension related to TBX4 mutation in 5 children (2019) (1)
- Minimal important difference in childhood interstitial lung diseases (2022) (1)
- The interaction of phosphatidylcholine with alveolar type II pneumocytes is dependent on its physical state. (1999) (1)
- Diffuse alveolar hemorrhage in children with interstitial lung disease: Determine etiologies! (2023) (1)
- Abandoning developmental silos: what can paediatricians and adult interstitial lung disease physicians learn from each other? (2019) (1)
- Guideline adherence in febrile children below 3 months visiting European Emergency Departments: an observational multicenter study (2022) (1)
- Interstitial lung disease caused by filamin A gene mutations: Clinical course of three paediatric cases (2016) (1)
- Molecular Epidemiology of Nontuberculous Mycobacteria in a German CF Center and Clinical Course of NTM Positive Patients (2013) (1)
- Comorbidity and long‐term clinical outcome of laryngotracheal clefts types III and IV: Systematic analysis of new cases (2020) (1)
- Abandoning developmental silos: what can paediatricians and adult interstitial lung disease physicians learn from each other? (2019) (1)
- Classification of different ABCA3 mutations causing interstitial lung disease (2015) (1)
- [IgG subclasses in healthy children and in children with frequent respiratory tract infections]. (1990) (1)
- Surfactanthomöpstase : Grundlagen für die Surfactantsubstitutions-therapie (1992) (1)
- IMPAIRED β-ADRENERGIC FUNCTION IN LYMPHOCYTES OF CHILDREN WITH PERTUSSIS (P) (1987) (1)
- Congenital Vertical Tracheal Septum Misdiagnosed as Laryngomalacia. (2019) (1)
- Multiple breath washout for monitoring alpha-1-antitrypsin deficiency related lung disease (2013) (1)
- Healthcare utilisation in childhood interstitial lung diseases: Analysis of chILD-EU registry data (2016) (1)
- International Experience in Pediatric Extracorporeal Membrane Oxygenation (ECMO) Bridge to Lung Transplantation (2015) (1)
- Pulmonary hypertension presenting with apnea, cyanosis, and failure to thrive in a young child. (2011) (1)
- Pulmonary interstitial Glycogenosis – a systematic analysis of new cases (2018) (1)
- Reply: glutathione inhalation treatments in cystic fibrosis: the interference of airway γ-glutamyltransferase. (2014) (1)
- [What to do if children cough for more than 4 weeks: diagnostic pathways and therapeutic options]. (2009) (1)
- 187. Degradation of surfactant protein A (SP-A) and other BAL proteins in patients with cystic fibrosis (1999) (1)
- AGE-DEPENDENT MATURATION OF β–ADRENOCEPTORS ON B– BUT NOT ON T–CELLS (1987) (0)
- 2 Behandlungsansätze in Standardsituationen (2013) (0)
- THE INTERLEUKIN 1 RECEPTOR LOCUS IS A GENETIC MODIFIER OF CYSTIC FIBROSIS (2017) (0)
- Whole lung lavage therapy (WLL) of pulmonary alveolar proteinosis (PAP): A global survey of current practices and procedures (2016) (0)
- Pulmonary haemorrhage (2021) (0)
- 41 Bronchitis plastica (2013) (0)
- 276* Long-term pulmonary outcome in cystic fibrosis (CF) is not adversely affected in CF associated liver disease treated with UDCA (2011) (0)
- Telomere gene mutations and associated childhood interstitial lung disease (chILD) (2023) (0)
- Surfactant lipid uptake and metabolism by neonatal and adult type II pneumocytes. (1999) (0)
- ABCA3 mutations disturb lipid homeostasis in alveolar epithelial cells (2013) (0)
- Neuroendocrine cell hyperplasia of infancy: is biopsy not needed? (2016) (0)
- ABCA3 Deficiency—Variant-Specific Response to Hydroxychloroquine (2023) (0)
- Old and novel surfactant protein C (SP-C) mutations in children (2011) (0)
- Quality standards for managing children and adolescents with bronchiectasis: an international consensus (2022) (0)
- 22 Palliative Care (2013) (0)
- Drug- and radiation-induced lung disease (2021) (0)
- Homooligomerization of the ABC-transporter 3 and its functional significance (2014) (0)
- Binding of dipalmitoyl-phosphatidylcholine liposomes to lung epithelial type II cells and other surfaces. (1997) (0)
- Bombesein Staining May Be A Useful Marker In Idiopathic Interstitial Pneumonias Other Than Nehi (2016) (0)
- An observational study of incident diagnoses of children’s diffuse parenchymal lung disease (ChILDEU) (2018) (0)
- [Causative relations between infections and allergies in obstructive respiratory tract diseases in childhood]. (1987) (0)
- 190 Long-term outcome after meconium ileus (2007) (0)
- SERIES ''MATRIX METALLOPROTEINASES IN LUNG HEALTH AND DISEASE'' Edited by J. Muller-Quernheim and O. Eickelberg Number 3 in this Series The role of matrix metalloproteinases in cystic fibrosis lung disease (2011) (0)
- Prevalence and characteristics of cystic lung lesions in children with interstitial lung diseases – a register-based study (2021) (0)
- Interstitial Lung Disease in Immunocompromised Children (2022) (0)
- [Surfactant homeostasis--principles for surfactant substitution therapy]. (1992) (0)
- Pulmonary alveolar proteinosis due to heterozygous mutation in OAS1: Treatment of a novel disease with whole lung lavages and stem cell transplantation (2019) (0)
- High sputum levels of gamma-glutamyltransferase are a contraindication to GSH inhalation therapies in cystic fibrosis (2016) (0)
- Reduced frequency of reactions in patients with cystic fibrosis and continuous treatment with oral cephalosporins (2008) (0)
- mouse lungs: its acceleration by reduction Removal of a dimeric form of surfactant protein C from (2015) (0)
- Homozygous mutation in ABCA3 Lipid-Transporter defect (EXON 9) and low level of surfactant protein C (2010) (0)
- Surfactant Metabolism Disorders: Two Cases With Different Findings (2016) (0)
- [Significance of basal TSH and free T3 as compared with an extended in vitro diagnosis in the understanding of functional disorders of the thyroid]. (1988) (0)
- Zelluläre Mechanismen interstitieller Lungenerkrankungen durch Mutationen im ABCA3-Transporter (2009) (0)
- Quantifying Functional Impairment of ABCA3 Variants Associated with Interstitial Lung Disease (2023) (0)
- Interstitial lung disease in children with aminoacyl-tRNA synthetase (ARSs) deficiencies (2023) (0)
- Hypersensitivity Pneumonitis In Children In Germany: Still A Long Way To State Of The Art Diagnosis And Treatment (2010) (0)
- Autoimmune PAP (aPAP) in children (2022) (0)
- Presenting Respiratory Disease in Niemann-Pick Type-C2 Is Caused by Pulmonary Alveolar Proteinosis (PAP) with Defective Surfactant. (2009) (0)
- Targeted massive parallel sequencing for genetic diagnosis of neonatal/infantile pulmonary hypertension (2016) (0)
- ABCA3 mutations influence the stress level and immunological function of lung epithelial A549 cells (2010) (0)
- Treating Resistant Bacteria S. aureus, P. aeruginosa, and Others (2017) (0)
- 261 Continous treatment with ursodeoxycholic acid (UDCA) for 15 years (2006) (0)
- Analysis of children’s diffuse parenchymal lung disease from the European Management Platform for Childhood Interstitial Lung Diseases: Frequency of disease categories and treatments used (2017) (0)
- 38 Alpha-1-Antitrypsin-Mangel (2013) (0)
- Clinical features of four children with pulmonary alveolar proteinosis (2014) (0)
- The triple function of the ABC transporter ABCA3 in the secretion of lung surfactant lamellar bodies, milk fat globules and platelet granules (2009) (0)
- Satellite-derived data on greenness and access to green spaces are related to children ' s health indicators (2015) (0)
- [Secretion of surfactant from type II pneumocytes. Protracted maturation of the secretory process--role of purinergic stimulation]. (1995) (0)
- Surfactant dysfunction and alveolar proteinosis (2013) (0)
- Assessment of fibrosis in lung biopsies from the European childhood interstitial lung disease (chILD) registry (2020) (0)
- Functional analysis of ABCA3 in phosphatidylcholine metabolism (2018) (0)
- Functional analysis of the ABCA3-transporter with fluorescent labeled phosphatidylcholine (2015) (0)
- 186 Long-term outcome of different strategies following the first isolation of Pseudomonas aeruginosa (2006) (0)
- Additional file 1: of Whole lung lavage therapy for pulmonary alveolar proteinosis: a global survey of current practices and procedures (2016) (0)
- For Peer Review Whole lung lavage in infants and children with pulmonary alveolar proteinosis (2011) (0)
- Probe the transport function of ABCA3 by metabolic labelling of choline phospholipids (2020) (0)
- Estimating the Effect of Nintedanib on Forced Vital Capacity in Children and Adolescents With Fibrosing Interstitial Lung Disease: Extrapolation Using a Bayesian Borrowing Approach (2023) (0)
- Biallelic variants in the calpain regulatory subunit, CAPNS1, cause pulmonary arterial hypertension (2023) (0)
- WS18.2 Persistent elevation of antibodies against Pseudomonas aeruginosa following successful eradication (2012) (0)
- Familial Interstitial Lung Disease And ABCA3 Gene GLY964ASP Mutation (2011) (0)
- Calmodulin Antagonist and Calcium lonophore Modulation of ATP-Stimulated Surfactant Phosphatidylcholine Secretion in Rat Type II Pneumocytes (1994) (0)
- Surfactant dysfunction syndromes and pulmonary alveolar proteinosis (2021) (0)
- In-vitro inhibition of neutrophil elastase activity by inhaled antibiotics used in cystic fibrosis patients (2009) (0)
- Childhood interstitial lung disease: A diagnostic challenge (2015) (0)
- Studies on the adenosine A2 receptor mediating pulmonary surfactant phosphatidylcholine secretion in primary cultures of type II pneumocytes isolated from adult rats (1990) (0)
- European pulmonary alveolar proteinosis network (EuPAPNet): Results from biomarkers´ investigation (2014) (0)
- Surfactant therapy in the newborn: Known facts and open questions (1993) (0)
- Installation of a Multidisciplinary team (MDT) review board for children´s interstitial lung disease (ILD) (2017) (0)
- Current Practice of Drug Treatment In Children with ILD: First Insights From The Child-Eu Registry (2016) (0)
- The genetics of interstitial lung diseases due to surfactant dysfunction disorders in children (2008) (0)
- Aerosolized liposomal cyclosporine A for treatment of progressive allograft dysfunction following lung transplantation (2013) (0)
- P083 Inhaled anti-pseudomonal therapy in patients with cystic fibrosis (2018) (0)
- SURFACTANTPROTEINB DEFICIENCYCAUSEDBYANOVELMUTATION INVOLVINGMULTIPLEEXONSOFTHESP-B GENE* (2008) (0)
- Relationship of cardiac performance, free energy of ATP-hydrolysis and energy requirementof ion-transport processes under hypoxic steady state conditions* (1984) (0)
- inflammatory cell-derived oxidants in cystic fibrosis Glutathione aerosol suppresses lung epithelial surface (2015) (0)
- [Acute dyspnea in childhood. Croup or foreign body--bronchiolitis or asthma?]. (2003) (0)
- Febrile illness in high-risk children: a prospective, international observational study (2022) (0)
- Interstitial pneumonia and pulmonary alveolar proteinosis in a full-term baby with a de novo heterozygote SFTPC mutation (2004) (0)
- Children’s interstital lung diseases (chILD) – an area of unmet educational need? (2021) (0)
- “European network for translational research in children’s and adult interstitial lung disease”. A COST Action to keep working (2017) (0)
- 157 Long-term impact of fungi on pediatric cystic fibrosis lung disease (2014) (0)
- Lung clearance index in alpha-1-antitrypsin deficiency - A follow up (2016) (0)
- OR.5. Decreased Pulmonary CD4+CD25Hi T-Cells and Foxp3 mRNA Levels in Children with Allergic Asthma (2006) (0)
- Rescue of mutant ABCA3 by small molecular correctors (2017) (0)
- Mucosal antimicrobial peptides accumulate in airway mucins (2006) (0)
- 166 DEVELOPMENT CHANGES IN THE RESPONSE OF TYPE II CELLS TO PHOSPHATIDYLCHOLINE (PC) SECRETAGOGUES (1991) (0)
- Lung disease caused by non-null ABCA3 mutations: long-term follow-up (2018) (0)
- 4.7 Serum, Plasma, Urin (2011) (0)
- Changes in total IgE levels predict pulmonary outcome in cystic fibrosis related allergic bronchopulmonary aspergillosis (2016) (0)
- Early onset and familiar Interstitial lung disease: Diagnose molecularly and systematically explore treatment with hydroxychloroquine (2019) (0)
- Potentiation of A 2 Purinoceptor-Stimulated Surfactant Phospholipid Secretion in Primary Cultures of Rat Type II Pneumocytes (0)
- Autoimmune pulmonary alveolar proteinosis in children (2022) (0)
- Retrospective analysis of treatment with Ivacaftor/Lumacaftor in patients with cystic fibrosis at the Munich Cystic Fibrosis Centers (2018) (0)
- Alveolarproteinose – Update in Deutschland (2008) (0)
- Role Of Alpha1-Antitrypsin (AAT) In Cystic Fibrosis-Associated Endoplasmic Reticulum (ER) Stress (2010) (0)
- 8.1 Allergologie (2011) (0)
- Bactericidal activity of human cystic fibrosis macrophages against Pseudomonas aeruginosa (2011) (0)
- Correction to: Febrile illness in high-risk children: a prospective, international observational study (2023) (0)
- Chemokine Responsiveness in Chronic Chemokine Receptor Expression and Infiltrated Neutrophils Acquire Novel (2008) (0)
- Phenotypic spectrum in recessive STING-associated vasculopathy with onset in infancy: Four novel cases and analysis of previously reported cases (2022) (0)
- Incidence and prevalence of children’s diffuse lung disease in Spain (2021) (0)
- ' s response to reviews Title : Assessment of Surfactant Protein A ( SPA ) dependent agglutination (2010) (0)
- 1 Differenzialdiagnose vor Differenzialtherapie (2013) (0)
- Interstitial Lung Disease in Childhood: Current Status of Diagnosis and Management (2017) (0)
- Developmental lung vascular disorders - clinics and genetics (2016) (0)
- Bronchiolitis obliterans (2005) (0)
- Study Design of a Phase III, Randomized, Placebo-Controlled Trial of Nintedanib in Children and Adolescents with Clinically Significant Fibrosing Interstitial Lung Disease (ILD) (2020) (0)
- Extracellular GSTO1 – an as yet poorly explored player in redox regulation, inflammation and autoimmunity. (2023) (0)
- Cellular mechanisms of interstitial lung disease in children caused by mutations of the ABCA3-transporter (2010) (0)
- Author response for "Expanding the phenotypic spectrum of FINCA syndrome beyond infancy" (2021) (0)
- Liposomal Amphotericin B formulation and its pharmakokinetics in the treatment of fungal infections (1997) (0)
This paper list is powered by the following services:
What Schools Are Affiliated With Matthias Griese?
Matthias Griese is affiliated with the following schools:
