Patrick Niaudet
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Patrick Niaudet's Degrees
- PhD Molecular Biology University of California, San Francisco
- Doctorate Medicine Stanford University
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(Suggest an Edit or Addition)Patrick Niaudet's Published Works
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Total number of citations to an author for the works they published in a given year. This highlights publication of the most important work(s) by the author
Published Works
- NPHS2, encoding the glomerular protein podocin, is mutated in autosomal recessive steroid-resistant nephrotic syndrome (2000) (1379)
- Donor splice-site mutations in WT1 are responsible for Frasier syndrome (1997) (680)
- Strict blood-pressure control and progression of renal failure in children. (2009) (603)
- Genetics and outcome of atypical hemolytic uremic syndrome: a nationwide French series comparing children and adults. (2013) (575)
- The ciliary gene RPGRIP1L is mutated in cerebello-oculo-renal syndrome (Joubert syndrome type B) and Meckel syndrome (2007) (466)
- Acquired and genetic complement abnormalities play a critical role in dense deposit disease and other C3 glomerulopathies. (2012) (441)
- Differential impact of complement mutations on clinical characteristics in atypical hemolytic uremic syndrome. (2007) (400)
- Structure of the gene for congenital nephrotic syndrome of the finnish type (NPHS1) and characterization of mutations. (1999) (394)
- Heterozygous and homozygous factor h deficiencies associated with hemolytic uremic syndrome or membranoproliferative glomerulonephritis: report and genetic analysis of 16 cases. (2004) (386)
- NPHS2 mutation analysis shows genetic heterogeneity of steroid-resistant nephrotic syndrome and low post-transplant recurrence. (2004) (354)
- Anti-B-cell monoclonal antibodies in the treatment of severe B-cell lymphoproliferative syndrome following bone marrow and organ transplantation. (1991) (328)
- A mutant mitochondrial respiratory chain assembly protein causes complex III deficiency in patients with tubulopathy, encephalopathy and liver failure (2001) (297)
- Effect of plasma protein adsorption on protein excretion in kidney-transplant recipients with recurrent nephrotic syndrome (1994) (266)
- Methylprednisolone pulse therapy in the treatment of severe forms of Schönlein-Henoch purpura nephritis (1998) (262)
- Clinical features of anti-factor H autoantibody-associated hemolytic uremic syndrome. (2010) (250)
- Early angiotensin-converting enzyme inhibition in Alport syndrome delays renal failure and improves life expectancy. (2012) (249)
- Eculizumab for Atypical Hemolytic Uremic Syndrome Recurrence in Renal Transplantation (2012) (248)
- Incompletely penetrant PKD1 alleles suggest a role for gene dosage in cyst initiation in polycystic kidney disease. (2009) (243)
- Identification of constitutional WT1 mutations, in patients with isolated diffuse mesangial sclerosis, and analysis of genotype/phenotype correlations by use of a computerized mutation database. (1998) (237)
- KLHL3 mutations cause familial hyperkalemic hypertension by impairing ion transport in the distal nephron (2012) (232)
- Rituximab treatment for severe steroid- or cyclosporine-dependent nephrotic syndrome: a multicentric series of 22 cases (2008) (232)
- Eculizumab in severe Shiga-toxin-associated HUS. (2011) (209)
- Initial presentation of childhood-onset systemic lupus erythematosus: a French multicenter study. (2005) (207)
- Population Pharmacokinetics and Pharmacogenetics of Tacrolimus in De Novo Pediatric Kidney Transplant Recipients (2009) (178)
- Mutations in the human laminin β2 (LAMB2) gene and the associated phenotypic spectrum a (2010) (170)
- Timing and outcome of renal replacement therapy in patients with congenital malformations of the kidney and urinary tract. (2013) (168)
- H deficiency in two brothers with atypical dense intramembranous deposit disease. (1986) (168)
- The nephropathy associated with male pseudohermaphroditism and Wilms' tumor (Drash syndrome): a distinctive glomerular lesion--report of 10 cases. (1985) (168)
- Treatment of childhood steroid-resistant idiopathic nephrosis with a combination of cyclosporine and prednisone. French Society of Pediatric Nephrology. (1994) (164)
- WT1 and glomerular diseases (2006) (160)
- High NPHP1 and NPHP6 mutation rate in patients with Joubert syndrome and nephronophthisis: potential epistatic effect of NPHP6 and AHI1 mutations in patients with NPHP1 mutations. (2007) (158)
- Nephronophthisis (2008) (156)
- Mutations in the gene encoding the inwardly-rectifying renal potassium channel, ROMK, cause the antenatal variant of Bartter syndrome: evidence for genetic heterogeneity. International Collaborative Study Group for Bartter-like Syndromes. (1997) (156)
- Steroid-sensitive nephrotic syndrome: from childhood to adulthood. (2003) (152)
- Novel mutations in the thiazide-sensitive NaCl cotransporter gene in patients with Gitelman syndrome with predominant localization to the C-terminal domain. (1998) (148)
- Biosynthesis of Paf-acether (platelet-activating factor). VII. Precursors of Paf-acether and acetyl-transferase activity in human leukocytes. (1984) (148)
- NPHS 2 , encoding the glomerular protein podocin , is mutated in autosomal recessive steroid-resistant nephrotic syndrome (2000) (146)
- Multiple OXPHOS Deficiency in the Liver, Kidney, Heart, and Skeletal Muscle of Patients With Methylmalonic Aciduria and Propionic Aciduria (2009) (143)
- Cysteamine therapy delays the progression of nephropathic cystinosis in late adolescents and adults. (2012) (143)
- Nephropathic cystinosis: an international consensus document. (2014) (137)
- Phenotype-genotype correlation in antenatal and neonatal variants of Bartter syndrome. (2009) (136)
- Early-childhood membranous nephropathy due to cationic bovine serum albumin. (2011) (134)
- The risk of recurrence of hemolytic uremic syndrome after renal transplantation in children (2003) (133)
- Cyclosporine in the treatment of idiopathic nephrosis. (1994) (132)
- Mapping a gene (SRN1) to chromosome 1q25-q31 in idiopathic nephrotic syndrome confirms a distinct entity of autosomal recessive nephrosis. (1995) (132)
- Efficacy and safety of Oxalobacter formigenes to reduce urinary oxalate in primary hyperoxaluria. (2011) (132)
- Rituximab therapy for childhood-onset systemic lupus erythematosus. (2006) (123)
- Genotype-phenotype correlations in non-Finnish congenital nephrotic syndrome. (2010) (121)
- LONG-TERM SOCIAL OUTCOME OF CHILDREN AFTER KIDNEY TRANSPLANTATION (2004) (121)
- Nephrin mutations can cause childhood-onset steroid-resistant nephrotic syndrome. (2008) (121)
- Overall Neutralization of Complement Factor H by Autoantibodies in the Acute Phase of the Autoimmune Form of Atypical Hemolytic Uremic Syndrome (2012) (107)
- WT1 and PAX-2 podocyte expression in Denys-Drash syndrome and isolated diffuse mesangial sclerosis. (1999) (107)
- Long-term follow-up of ifosfamide renal toxicity in children treated for malignant mesenchymal tumors: an International Society of Pediatric Oncology report. (1991) (105)
- PAX2 mutations in oligomeganephronia. (2001) (105)
- Long-term evaluation of Ifosfamide-related nephrotoxicity in children. (2009) (101)
- Low incidence of SARS-CoV-2, risk factors of mortality and the course of illness in the French national cohort of dialysis patients (2020) (97)
- Genetic forms of nephrotic syndrome (2004) (92)
- WT1 splice-site mutations are rarely associated with primary steroid-resistant focal and segmental glomerulosclerosis. (2000) (92)
- Renal transplantation in children with augmentation cystoplasty: long-term results. (1998) (87)
- Intravenous cyclosporine therapy in recurrent nephrotic syndrome after renal transplantation in children (2003) (86)
- The same mutation affecting the splicing of WT1 gene is present on Frasier syndrome patients with or without Wilms' tumor (1999) (85)
- KLHL3 mutations cause familial hyperkalemic hypertension by impairing ion transport in the distal nephron (2012) (84)
- Mutations in the vasopressin V2 receptor and aquaporin-2 genes in 12 families with congenital nephrogenic diabetes insipidus. (1997) (84)
- Truncation of C-mip (Tc-mip), a New Proximal Signaling Protein, Induces c-maf Th2 Transcription Factor and Cytoskeleton Reorganization (2003) (83)
- The kidney in mitochondrial cytopathies. (1997) (83)
- Recurrence of nephrotic syndrome after transplantation in a mixed population of children and adults: course of glomerular lesions and value of the Columbia classification of histological variants of focal and segmental glomerulosclerosis (FSGS). (2010) (82)
- Hair and skin disorders as signs of mitochondrial disease. (1999) (81)
- Development of human renal function: reference intervals for 10 biochemical markers in fetal urine. (1996) (80)
- Renal Transplantation Under Prophylactic Eculizumab in Atypical Hemolytic Uremic Syndrome With CFH/CFHR1 Hybrid Protein (2012) (78)
- Idiopathic Nephrotic Syndrome in Children: Clinical Aspects (2016) (77)
- Comparison between pre- and posttreatment renal biopsies in children receiving ciclosporine for idiopathic nephrosis. (1994) (77)
- Cyclosporin therapy in patients with Alport syndrome (2007) (74)
- Acute lymphoblastic leukaemia associated antigen—II. Isolation and partial characterisation (1978) (73)
- Different inactivating mutations of the mineralocorticoid receptor in fourteen families affected by type I pseudohypoaldosteronism. (2003) (72)
- A randomized controlled crossover trial with delayed-release cysteamine bitartrate in nephropathic cystinosis: effectiveness on white blood cell cystine levels and comparison of safety. (2012) (72)
- Lupus Anticoagulant-Hypoprothrombinemia Syndrome: Report of 8 Cases and Review of the Literature (2012) (72)
- Alterations of protein metabolism by metabolic acidosis in children with chronic renal failure. (2000) (71)
- Percutaneous transluminal angioplasty of renal artery stenosis in children (1998) (71)
- Long-term outcome in methylmalonic aciduria: a series of 30 French patients. (2009) (70)
- Impairment of lung diffusion capacity in Schönlein-Henoch purpura. (1992) (69)
- Prognosis of autosomal dominant polycystic kidney disease diagnosed in utero or at birth (2007) (69)
- Treatment of lupus nephritis in children. (2000) (68)
- Comparison of cyclosporin and chlorambucil in the treatment of steroid-dependent idiopathic nephrotic syndrome: a multicentre randomized controlled trial (2004) (68)
- Transcriptional and Post-Transcriptional Alterations of I κBα in Active Minimal-Change Nephrotic Syndrome (2001) (68)
- Long term results of liver-kidney transplantation in children with primary hyperoxaluria (2001) (64)
- Thymic function in NZB mice. II. Regulatory influence of a circulating thymic factor on antibody production against polyvinylpyrrolidone in NZB mice. (1976) (64)
- Glomerular Lesions in Patients With Sickle Cell Disease (2010) (63)
- Population Pharmacokinetics and Pharmacogenetics of Mycophenolic Acid Following Administration of Mycophenolate Mofetil in De Novo Pediatric Renal‐Transplant Patients (2010) (62)
- In vivo confocal microscopy and anterior segment optical coherence tomography analysis of the cornea in nephropathic cystinosis. (2009) (59)
- Observations of a large Dent disease cohort. (2016) (58)
- Differences in effect of isoproterenol stimulation on levels of cyclic AMP in human B and T lymphocytes (1976) (58)
- Mutation Update of the CLCN5 Gene Responsible for Dent Disease 1 (2015) (56)
- Mycophenolate mofetil for steroid-dependent nephrotic syndrome: a phase II Bayesian trial (2012) (56)
- Pulse cyclophosphamide therapy and clinical remission in atypical hemolytic uremic syndrome with anti-complement factor H autoantibodies. (2010) (56)
- Nutritional and metabolic studies in children on continuous ambulatory peritoneal dialysis. (1983) (55)
- de Toni-Fanconi-Debré syndrome with Leigh syndrome revealing severe muscle cytochrome c oxidase deficiency. (1988) (55)
- Everolimus in pediatric de nova renal transplant patients1 (2003) (55)
- A specific glomerular lesion of the graft: allograft glomerulopathy. (1993) (55)
- Hemolytic Uremic Syndrome: New Developments in Pathogenesis and Treatment (2011) (54)
- Deletion of mitochondrial DNA in patient with chronic tubulointerstitial nephritis. (1995) (54)
- Deletion of the mitochondrial DNA in a case of de Toni-Debré-Fanconi syndrome and Pearson syndrome (1994) (54)
- Neurological involvement in a child with atypical hemolytic uremic syndrome (2010) (53)
- Long-term outcome of children with steroid-sensitive idiopathic nephrotic syndrome. (2009) (53)
- Treatment of idiopathic nephrotic syndrome with cyclosporin A in children. (1991) (53)
- A randomised Phase I/II trial to evaluate the efficacy and safety of orally administered Oxalobacter formigenes to treat primary hyperoxaluria (2017) (53)
- A randomized clinical trial indicates that levamisole increases the time to relapse in children with steroid-sensitive idiopathic nephrotic syndrome. (2017) (53)
- Primary IgA nephropathies in children: prognosis and treatment. (1993) (51)
- A rational dosing algorithm for basiliximab (Simulect) in pediatric renal transplantation based on pharmacokinetic-dynamic evaluations1 (2002) (50)
- A controlled study of deflazacort in the treatment of idiopathic nephrotic syndrome (1997) (50)
- A new gel formulation of topical cysteamine for the treatment of corneal cystine crystals in cystinosis: the Cystadrops OCT-1 study. (2014) (50)
- Renovascular hypertension and vascular anomalies in Alagille syndrome (1998) (49)
- Mitochondrial disorders and the kidney (1998) (49)
- Renal Granulomatous sarcoidosis in childhood: a report of 11 cases and a review of the literature (1999) (48)
- Non-immunologic mechanisms of calcineurin inhibitors explain its antiproteinuric effects in genetic glomerulopathies (2010) (47)
- Acute kidney injury complicating nephrotic syndrome of minimal change disease. (2018) (47)
- Effect of hydrochlorothiazide on urinary calcium excretion in dent disease: an uncontrolled trial. (2008) (46)
- Hydration measurement by bioimpedance spectroscopy and blood pressure management in children on hemodialysis (2013) (44)
- [Transmission of nephrotic syndrome to two neonates. Spontaneous regression]. (1991) (44)
- Determinants of eGFR at start of renal replacement therapy in paediatric patients. (2010) (42)
- Urological complications after renal transplantation using ureteroureteral anastomosis in children. (2001) (41)
- Complement factor H deficiency and posttransplantation glomerulonephritis with isolated C3 deposits. (2008) (41)
- Successful kidney transplantation of immunized patients after desensitization with normal human polyclonal immunoglobulins. (1995) (41)
- Cystinosin is a melanosomal protein that regulates melanin synthesis (2012) (40)
- Treatment of Idiopathic Nephrotic Syndrome with Levamisole (1984) (40)
- Treatment and outcome of congenital nephrotic syndrome (2019) (39)
- Management of oxalosis. (1996) (39)
- Haemolytic uraemic syndrome and pulmonary hypertension in a patient with methionine synthase deficiency (1999) (39)
- Preventive treatment of vascular thrombosis after kidney transplantation in children with low molecular weight heparin. (1991) (39)
- Respiratory chain deficiency presenting as congenital nephrotic syndrome (2005) (38)
- Multicenter trial of everolimus in pediatric renal transplant recipients: Results at three year (2008) (38)
- Podocin and nephrotic syndrome: implications for the clinician. (2004) (37)
- Clinical features and management of arterial hypertension in children with Williams-Beuren syndrome. (2010) (37)
- A multicenter, open-label, pharmacokinetic/pharmacodynamic safety, and tolerability study of basiliximab (Simulect) in pediatric de novo renal transplant recipients (2002) (37)
- Nephrotic syndrome in children. (1993) (37)
- Age-Dependent Risk of Graft Failure in Young Kidney Transplant Recipients (2017) (36)
- Renal involvement in mitochondrial cytopathies (1996) (36)
- Small intestinal transplantation in a child using cyclosporine. (1988) (36)
- Kidney transplantation in children: results of 383 grafts performed at Enfants Malades Hospital from 1973 to 1984. (1987) (35)
- Quality of Life is Improved and Kidney Function Preserved in Patients with Nephropathic Cystinosis Treated for 2 Years with Delayed-Release Cysteamine Bitartrate (2014) (35)
- Long-term remission of atypical HUS with anti-factor H antibodies after cyclophosphamide pulses (2013) (34)
- Renal transplantation in 4 patients with methylmalonic aciduria: a cell therapy for metabolic disease. (2013) (34)
- Side effects of levamisole in children with nephrosis (1994) (34)
- Software and database for the analysis of mutations in the human WT1 gene (1998) (33)
- Treatment of lupus nephritis in children (2000) (33)
- Long‐term results of combined liver‐kidney transplantation for primary hyperoxaluria type 1: The French Experience (2014) (33)
- Haemolytic uraemic syndrome: prognostic factors in children over 3 years of age (1995) (32)
- Transcriptional and post-transcriptional alterations of IkappaBalpha in active minimal-change nephrotic syndrome. (2001) (32)
- Tubulopathy and pancytopaenia with normal pancreatic function: a variant of Pearson syndrome. (2009) (31)
- Cyclosporin in the treatment of idiopathic nephrotic syndrome in children (1987) (31)
- Peanut Agglutinin (1978) (31)
- Clinical and genetic heterogeneity in familial steroid-sensitive nephrotic syndrome (2018) (30)
- Living donor kidney transplantation in patients with hereditary nephropathies (2010) (28)
- Improvement of Renal Function in Pediatric Heart Transplant Recipients Treated with Low-Dose Calcineurin Inhibitor and Mycophenolate Mofetil (2005) (28)
- Allo-immune membranous nephropathy and recombinant aryl sulfatase replacement therapy: a need for tolerance induction therapy. (2014) (28)
- Liver hepatoblastoma and multiple OXPHOS deficiency in the follow-up of a patient with methylmalonic aciduria. (2008) (28)
- Cyclosporine in the therapy of steroid-resistant idiopathic nephrotic syndrome. (1997) (28)
- Renal failure from mitochondrial cytopathies. (1997) (27)
- Non-immunological risk factors in paediatric renal transplantation (1993) (26)
- High NPHP 1 and NPHP 6 Mutation Rate in Patients with Joubert Syndrome and Nephronophthisis : Potential Epistatic Effect of NPHP 6 and AHI 1 Mutations in Patients with NPHP 1 Mutations (2007) (26)
- Pediatric en bloc kidney transplantation into pediatric recipients: The French experience (2012) (25)
- Clinicopathologic correlations in severe forms of Henoch-Schönlein purpura nephritis based on repeat biopsies. (1984) (25)
- Surface markers and electron microscopy of human blood L cells: a comparison with T and B lymphocytes. (1978) (25)
- Congenital disorders of glycosylation type I: a rare but new cause of hyperechoic kidneys in infants and children due to early microcystic changes (2006) (25)
- X‐linked hypohidrotic ectodermal dysplasia and t(X;12) in a female (1989) (25)
- Long-term results of renal transplantation in children with the prune-belly syndrome. (1997) (24)
- Recurrence of de novo membranous glomerulonephritis on renal grafts. (1994) (24)
- Therapeutic approach to focal and segmental glomerulosclerosis recurrence in kidney transplant recipients. (2010) (24)
- Schönlein-Henoch purpura nephritis: pronostic factors and therapy. (1994) (23)
- Diabetes mellitus in patients with infantile cystinosis after renal transplantation (1999) (23)
- Diffuse arterial calcified elastopathy--a new cause of renovascular hypertension in children. (1985) (22)
- High-resolution mapping of the gene for cystinosis, using combined biochemical and linkage analysis. (1996) (22)
- Cyclosporine and childhood idiopathic nephrosis. (1988) (22)
- Safety and tolerability of cyclosporin A (Sandimmun®) in idiopathic nephrotic syndrome (1991) (21)
- Kidney involvement in mitochondrial disorders. (1995) (21)
- Genetics of the nephrotic syndrome. (2000) (21)
- In vivo reflectance confocal microscopy of the skin: a noninvasive means of assessing body cystine accumulation in infantile cystinosis. (2013) (20)
- An international cohort study spanning five decades assessed outcomes of nephropathic cystinosis. (2021) (20)
- Postransplant lymphoproliferative disease following renal transplantation: a multicenter retrospective study of 41 cases observed between 1992 and 1996. French Speaking Transplantation Workshop. (1998) (20)
- Nephrogenic diabetes insipidus: clinical and pathophysiological aspects. (1984) (20)
- The IgE humoral response in OKT3-treated patients. Incidence and fine specificity. (1996) (19)
- Duration of action of a chimeric interleukin-2 receptor monoclonal antibody, basiliximab, in pediatric kidney transplant recipients. (2000) (19)
- Population pharmacokinetics and pharmacodynamics of cysteamine in nephropathic cystinosis patients (2011) (19)
- Optimal Use of Sandimmun® in Nephrotic Syndrome (1992) (19)
- Sclerosing encapsulating peritonitis in children. (1987) (19)
- Outcome of children with acute renal failure. (1985) (19)
- Treatment of childhood steroid-resistant idiopathic nephrotic syndrome. (1998) (18)
- Nephrotic syndrome in Kawasaki disease: a report of three cases (2012) (18)
- Renal function and histology in children after small bowel transplantation (2013) (18)
- WT1, renal development, and glomerulopathies. (1999) (17)
- Treatment of severe childhood nephrosis. (1988) (17)
- High serum levels of a non-(1–84) parathyroid hormone (PTH) fragment in pediatric haemodialysis patients (2001) (17)
- Growth in boys with idiopathic nephrotic syndrome on long-term cyclosporin and steroid treatment (2009) (17)
- Pediatric nephrology, seventh edition (2015) (17)
- Excellent long-term outcome of renal transplantation in cystinosis patients (2015) (17)
- [Bacterial complications of nephrotic syndrome in children]. (1995) (17)
- Family Outbreak of Shiga Toxin–producing Escherichia coli O123:H–, France, 2009 (2010) (16)
- Pretransplant blood transfusions with cyclosporine in pediatric renal transplantation (2000) (16)
- Familial hyperkalemic hypertension (Gordon syndrome): evidence for phenotypic variability in a study of 7 families. (2001) (16)
- Altered Oxidative Metabolism, Motility, and Adherence in Phagocytic Cells from Cystinotic Children (1985) (16)
- A pharmacokinetic study of Neoral in childhood steroid-dependent nephrotic syndrome (2001) (15)
- Protein Losses During Peritoneal Dialysis in Children (1985) (15)
- Glucocorticoid pharmacokinetics and growth retardation in children with renal transplants (2004) (15)
- Schönlein-Henoch purpura nephritis (1996) (13)
- Chronic renal failure after Puumala virus infection (1999) (13)
- Serial renal biopsies in children with idiopathic nephrosis receiving cyclosporin. (1995) (13)
- Comparison of three low-nitrogen diets containing essential amino acids and their alpha analogues for severely uremic children. (1983) (13)
- Multicentric Kaposi's sarcoma in a 5-year-old human immunodeficiency virus-negative renal allograft recipient. (1992) (13)
- Anti-OKT3 response following prophylactic treatment in paediatric kidney transplant recipients (1993) (12)
- Nephrotic syndrome: Rituximab in childhood steroid-dependent nephrotic syndrome (2013) (12)
- Renal tubular disorders of electrolyte regulation in children (2015) (12)
- [Renal involvement in autoimmune enteropathies]. (1993) (12)
- One-year routine renal transplant biopsies in children (2001) (12)
- Prophylactic OKT3 monoclonal antibody versus antilymphocyte globulins: a prospective, randomized study in 148 first cadaver kidney grafts. (1993) (12)
- Renal involvement in juvenile chronic arthritis: clinical and pathologic features. (1987) (12)
- [Acute renal insufficiency in Kawasaki disease]. (1993) (11)
- Original article Comparison of cyclosporin and chlorambucil in the treatment of steroid-dependent idiopathic nephrotic syndrome: a multicentre randomized controlled trial (1992) (11)
- Systemic Lupus Erythematosus (2009) (11)
- Nephrogenic Diabetes insipidus in Children (1985) (11)
- Diversity of cell surface polypeptides that are recognized by heteroantisera to human T cells. (1980) (11)
- Thymic function in nzb mice. I. Duration of thymic function in new zealand black (nzb) mice. (1976) (10)
- [Value of cyclosporine in the treatment of the recurrence of nephrosis after renal transplantation]. (1996) (10)
- ANCA-associated glomerulonephritis in systemic-onset juvenile idiopathic arthritis. (2012) (10)
- Crescentic glomerulonephritis in juvenile chronic arthritis. (1996) (10)
- Presymptomatic diagnosis of familial steroid-resistant riephrotic syndrome (1996) (10)
- Molecular identification of human T-lymphocyte antigens defined by the OKT5 and OKT8 monoclonal antibodies. (1982) (10)
- Steady-state pharmacokinetics of cyclosporine in renal transplant patients: does an influence of age or body weight exist? (1994) (10)
- Lung manifestations in MPO‐ANCA associated vasculitides in children (2014) (10)
- Steroid-resistant idiopathic nephrotic syndrome and ciclosporin. French Club of Pediatric Nephrology. (1991) (10)
- OP0064 Joint EULAR/ERA-EDTA recommendations for the management of adult and pediatric lupus nephritis (2013) (9)
- Loss of Ultrafiltration and Peritoneal Membrane Alterations in Children on CAPD (1985) (9)
- Papillary stones with Randall's plaques in children: clinicobiological features and outcome. (2012) (9)
- Nitrogen mustard therapy in idiopathic nephrotic syndrome of childhood. (1985) (9)
- CONVERSION FROM AZATHIOPRINE TO MYCOPHENOLATE MOFETIL IN PEDIATRIC RENAL TRANSPLANT RECIPIENTS (1999) (8)
- Triple therapy including cyclosporine A versus conventional regimen--a randomized prospective study in pediatric kidney transplantation. (1987) (8)
- Immunoglobulin-producing cells in cultured human peripheral blood lymphocytes. Modulation by accessory cells and enhancing effect of polyacrylamide beads. (1980) (8)
- Lupus érythémateux disséminé chez l'enfant : recommandations concernant les examens à effectuer lors de l'évaluation initiale et du suivi Guidelines about investigations to be performed at the diagnosis and during the follow-up of childhood-onset systemic lupus erythematosus (2004) (8)
- Causes of death in pediatric systemic lupus erythematosus. (2009) (8)
- Fanconi syndrome and severe polyuria: an uncommon clinicobiological presentation of a Gitelman syndrome (2014) (8)
- Ciliopathies A reference for clinicians (2014) (7)
- Risk of primary disease recurrence in pediatric renal transplantation. (1999) (7)
- [Cardiovascular impact of end-stage renal insufficiency in children undergoing hemodialysis]. (2000) (7)
- [Renal involvement in mitochondrial cytopathies]. (1996) (6)
- [Prevention of vascular thromboses after renal transplantation using low molecular weight heparin]. (1991) (6)
- Serological status of cytomegalovirus and outcome of renal transplantation. (1983) (6)
- Liver transplantation in children with inherited metabolic disorders. (1995) (6)
- Congenital nephrotic syndrome: commentary (2001) (6)
- Treatment of idiopathic nephrotic syndrome with cyclosporin in children. Preliminary results of growth data in long-term use. (1992) (6)
- Management of steroid-responsive nephrotic syndrome (2000) (6)
- [Immunosuppressive treatment]. (2011) (6)
- Mutations in the gene encoding the inwardly-rectifying renal potassium channel, ROMK, cause the antenatal variant of Bartter syndrome: evidence for genetic heterogeneity (2019) (6)
- Enteric-coated mycophenolate sodium in de novo pediatric renal transplant patients (2009) (6)
- Hemolytic-uremic syndrome: hereditary forms and forms associated with hereditary diseases. (2000) (6)
- Early failures of kidney transplantation: a study of 70 cases from 801 consecutive grafts performed in children and adolescents. (1993) (6)
- Loss of graft by chronic rejection in a series of pediatric kidney transplantation: predictive value of biopsy. (1998) (6)
- Alteration of lung diffusion capacity in IgA nephropathy. (1996) (5)
- Comprar Pediatric Nephrology | Avner, Ellis D. | 9783540763277 | Springer (2009) (5)
- In vitro characteristics on human lymphocyte functions of a new immunomodulatory agent, a cyclic peptide, cyclomunine. (1980) (5)
- PREGNANCY AND GLOMERULONEPHRITIS (1989) (5)
- The levamisole study in steroid sensitive idiopathic nephrotic syndrome (SSINS): inclusion completed (2012) (5)
- Utility of genetic screening in children with nephrotic syndrome presenting during the first year of life (2007) (5)
- Renal histology and response to cyclosporine in childhood idiopathic nephrotic syndrome (1998) (5)
- [Analgesia with oxygen-nitrous oxide mixture during percutaneous renal biopsy in children]. (2001) (5)
- Primary IgA nephropathies in children. (1990) (5)
- Treatment of acute rejection crisis by antilymphocyte globulins: a randomized prospective study in pediatric kidney transplantation. (1987) (5)
- [Congenital and infantile nephrotic syndrome]. (2005) (5)
- Mutations in the vasopressin V2 receptor and aquaporin-2 genes in twelve families with congenital nephrogenic diabetes insipidus. (1998) (5)
- Dominant polycystic kidney disease in childhood: report of 22 cases. (1989) (5)
- Modification of peritoneal ultrafiltration capacity in children undergoing peritoneal dialysis. (1985) (4)
- [Nephropathy of rheumatoid purpura]. (1989) (4)
- Early Conversion of Calcineurin Inhibitor to Everolimus in De Novo Paediatric Renal Transplant Recipients and Its Impact on Efficacy and Renal Function; Design of An Open-Label, Randomised, Multi-Centre Study: 1573 (2012) (4)
- [Lipoid nephrosis in childhood]. (2003) (4)
- Mutations in BCS1, a mitochondrial respiratory chain assembly gene, are responsible for complex III deficiency in patients with tubulopathy, encephalopathy and liver failure. (2001) (4)
- Complications of nephrotic syndrome in children (2015) (4)
- [Hemolytic anemia after kidney transplantation]. (1994) (4)
- Pediatric Nephrology (1981) (4)
- A 10-year-old girl was found to have asymptomatic proteinuria upon routine urinary screening at school. (2000) (4)
- Stimulation of thymic humoral function by cyclomunine, a cyclic peptide, in mice (1980) (4)
- [Renal transplantation in children under five years of age. Experience at the Hopital des Enfants-Malades]. (1993) (4)
- Update and outcome of renal transplant patients with human immunodeficiency virus. The Groupe Cooperatif de Transplantation de I'lle de France. (1991) (3)
- Immunological factors in organ transplantation (2004) (3)
- [Course of renal lesions in disseminated lupus erythematosus]. (1991) (3)
- RET proto-oncogene: role in kidney development and molecular pathology. (1998) (3)
- Tumor cell line characterization of a malignant histiocytosis transplanted into nude mice (2004) (3)
- Cyclosporin in the Therapy of Idiopathic Nephrotic Syndrome in Children (1989) (3)
- Renal transplantation in childhood (2005) (3)
- Intra‐ and postoperative adverse events in children with nephrotic syndrome requiring surgery under general anesthesia (2012) (2)
- [Hemolytic and uremic syndrome in the child]. (2008) (2)
- Oliguria, facial oedema and severe dyspnoea. (1989) (2)
- [Proteinuria (in adults and children). Diagnostic orientation]. (1997) (2)
- Activation of Human T Lymphocytes by Soluble Protein A (1985) (2)
- [Diabetes induced by corticoids in 6 children after renal transplantation]. (1984) (2)
- [Characterization of the NPH2 gene, coding for the glomerular protein podocin, implicated in a familial form of cortico-resistant nephrotic syndrome transmitted as an autosomal recessive]. (2002) (2)
- Pregnancy and glomerulonephritis. (1989) (2)
- Comparison of two protein diets in infants with chronic renal failure (1995) (2)
- ESPN-WINS : European working group on idiopathic nephrotic syndrome (2009) (2)
- Congenital/infantile nephrotic syndrome with diffuse mesangial sclerosis: relationship with Drash syndrome. (1989) (2)
- Association between 25(OH) vitamin D and graft survival in renal transplanted children (2020) (2)
- Loss of Ultrafiltration and Sclerosing Encapsulating Peritonitis in Children Undergoing CAPD/CCPD (1987) (2)
- Proteinuria plus positive hepatitis B surface antigen test. (1990) (2)
- [A comparative trial of OKT3 and antilymphocyte serum in the preventive treatment of rejection after kidney transplantation in children]. (1990) (2)
- Nephron number and primary hypertension. (2003) (2)
- [Prospective study of cytomegalovirus infections in 211 children with kidney transplants]. (1983) (1)
- Renal Involvement in Children with Systemic Lupus Erythematosus (2015) (1)
- CHAPTER 11 – Nephritic Syndrome (2008) (1)
- Donor-Specific Blood Transfusion and Renal Graft Survival: A 3-Year Experience in Pediatrics (1984) (1)
- [Intrafamilial renal transplantation in children after donor blood transfusions]. (1985) (1)
- Mutational analyses in Gitelman syndrome (1996) (1)
- FC067: Long-Term Outcome of Childhood Onset Idiopathic Nephrotic Syndrome (2022) (1)
- [Social, occupational, familial outcome in patients treated since childhood by dialysis and/or kidney transplantation]. (1996) (1)
- Blood transfusions under cyclosporine coverage before renal transplantation in children. (1995) (1)
- Congenital Nephrotic Syndrome (2012) (1)
- Austrian Syndrome Associated with Pandemic (H1N1) 2009 in Child (2019) (1)
- [Recent considerations on systemic lupus erythematosus (author's transl)]. (1981) (1)
- What is the risk that I will transmit nephrotic syndrome to my children, Doctor? (2010) (1)
- [Disseminated lupus erythematosus in children: guidelines about investigations during the initial evaluation and follow-up]. (2004) (1)
- Denys-Drash syndrome (2004) (1)
- Outcome of infantile nephropathic cystinosis depends on early intervention, not genotype: A multicenter sibling cohort study (2022) (1)
- Renal involvement in mitochondrial cytopathies. (1996) (1)
- Primary hyperoxaluria Author : Professor (2004) (1)
- How to manage a child with steroid-responsive nephrotic syndrome when dose of prednisolone is reduced or when placed on high-dose alternate day steroids. (1992) (1)
- Congenital and infantle nephrotic syndrome (2006) (1)
- Thymic Function in NZB Mice (1976) (1)
- [Nephrotic syndromes. Physiopathology, diagnosis, clinical course and treatment of lipoid nephrosis]. (1993) (1)
- [Ganglioneuroblastoma and ulcerative colitis. Chance association]. (1974) (1)
- [Idiopathic nephrosis (minimal glomerular lesions, segmental and focal hyalinosis)]. (1991) (1)
- Increased monocyte-dependent suppression of polyclonal activation of B lymphocytes from cystinotic children (1991) (1)
- 301 Nephrotic Syndrome in Children (2012) (1)
- [A prospective study of Cytomegalovirus infections in 211 children with renal transplants]. (1983) (1)
- Altered Leukotriene Generation in Leukocytes from Cystinotic Children (1994) (1)
- Absence of correlation between genotype and the severity of diffuse mesangial sclerosis in Denys-Drash syndrome. (2000) (1)
- [Children and adolescents with ESRD]. (2012) (1)
- [Study of pulmonary lymphocyte populations obtained by alveolar lavage]. (1980) (1)
- Autosomal recessive polycystic kidney disease Author : Professor (2004) (0)
- [Non anti-HLA antibodies and early irreversible rejection after kidney transplantation in children]. (1992) (0)
- Clinicopathological quiz. Wilms' tumour with renal failure due to diffuse mesangial sclerosis. (1987) (0)
- A PROSPECTIVE TRIAL OF INTRAVENOUS IMMUNOGLOBULINS (IVIg) FOR THE TRANSPLANTATION OF IMMUNIZED PATIENTS.: Abstract# 666 (2000) (0)
- Somatostatin Secretion in Children on CAPD and CCPD (1985) (0)
- Renée Habib (1924–2009) (2010) (0)
- Ask the expert (2004) (0)
- Subject Index, Vol. 57, 1991 (1991) (0)
- LONG TERM OUTCOME OF KIDNEY TRANSPLANTED CHILDREN: 11 TO 27 YEARS LATER.: Abstract# 636 (2000) (0)
- [Rheumatoid purpura in children and adults. Diagnosis, prognosis]. (2001) (0)
- Idiopathic nephrotic syndrome (2018) (0)
- CMV infection after kidney transplantation in children. (1996) (0)
- FP820AGE DEPENDANT RISK OF GRAFT FAILURE IN YOUNG KIDNEY TRANSPLANT RECIPIENTS (2015) (0)
- Annual Meeting of the French Society of Pediatric Nephrology (2001) (0)
- [History of pediatric nephrology in France]. (2023) (0)
- Nail-patella syndrome (2004) (0)
- Congenital nephrotic syndrome, Finnish type (2004) (0)
- [Recent considerations on systemic lupus erythematosus (author's transl)]. (1981) (0)
- Primary focal segmental glomerulosclerosis (2018) (0)
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- [Viral hepatitis with bone marrow depression in children. Apropos of 5 cases]. (1973) (0)
- In Memoriam: Professor Renée Habib 1924–2009 (2010) (0)
- Guidelines for the use of Sandimmun in nephrotic syndrome (1992) (0)
- SFRP CO-07 – Syndrome hémolytique et urémique atypique à anticorps anti-facteur H : Efficacité du cyclophosphamide (2014) (0)
- Ciclosporine Treatment of Childhood Idiopathic Neprhosis (1989) (0)
- Acute Kidney Failure and Minimal Change Disease (2018) (0)
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- [Captopril treatment of arterial hypertension in children after renal transplantation]. (1984) (0)
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- SP702A PRAGMATIC TRIAL OF DELAYED-RELEASE CYSTEAMINE BITARTRATE IN CHILDREN LESS THAN 6 YEARS OLD WITH CYSTINOSIS (2016) (0)
- Immunosuppressive treatment in childhood idiopathic nephrosis. (1989) (0)
- Transcriptional and Post-Transcriptional Alterations of I k B a in Active Minimal-Change Nephrotic Syndrome (2001) (0)
- Alteration oflungdiffusion capacity inIgA nephropathy (1996) (0)
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- Autosomal recessive polycystic kidney disease (2020) (0)
- [Immunosuppressive agents]. (1980) (0)
- Pediatric Nephrology (2012) (0)
- Clinical quiz. Diagnosis of pseudomembranous colitis secondary to C. difficile toxin. (1998) (0)
- New Therapies for the Treatment of Idiopathic Nephrotic Syndrome (1991) (0)
- Sandimmun in other etiologies of nephrotic syndrome (1992) (0)
- Pathogenesis of proteinuria in minimal change disease and focal segmental glomerulosclerosis (2018) (0)
- [Is nephrotoxicity of cyclosporine ineluctable?]. (1994) (0)
- Partial androgen receptor deficiency and mixed gonadal dysgenesis in Drash syndrome (2004) (0)
- [Genetics and nephrotic syndrome]. (1998) (0)
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- High-Resolution Mapping oftheGeneforCystinosis, Using Combined Biochemical andLinkage Analysis (1996) (0)
- Relapsing nephrotic syndrome (1993) (0)
- [Hepatic and renal transplantation in the treatment of type I hyperoxaluria]. (1991) (0)
- Minimal change disease (2018) (0)
- Detection of antilineage specific leucocyte antibodies by a quantitative immunocytometry method in sera from candidates for renal allografts. (1995) (0)
- Hemolytic-Uremic Syndrome in Children. (2022) (0)
- Zuber AJT 2012 (2013) (0)
- Cyclosporine in the treatment of idiopathic nephrosis. (1995) (0)
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- Clinicopathological quiz (1987) (0)
- Keywords Congenital nephrotic syndrome · Diffuse mesangial sclerosis · WT1 gene · Genetic counselling (2001) (0)
- Traitement antiprotéinurique d'un syndrome néphrotique congénital par l'association captopril et indométacine (1997) (0)
- Creation Date : October 2001 Update : May 2004 1 Member of the European editorial committee of Orphanet encyclopedia 2 Service de néphrologie pédiatrique (2004) (0)
- Clinical quiz (1998) (0)
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- [Results of kidney transplantation in children. Apropos of 213 grafts]. (1982) (0)
- Full Review Nephropathic cystinosis: an international consensus document (2014) (0)
- Long-term evaluation of ifosfamide-related nephrotoxicity in children: The French experience (2007) (0)
- OC062: Fetal hyperechogenic kidneys: causes and long term outcome in 43 cases (2003) (0)
- Truncation of cMip ( Tc-mip ) , a new proximal signaling protein , induces c-maf-dependent Th 2 pathway and cytoskeleton reorganization (2018) (0)
- CICLOSPORIN USE IN PEDIATRIC RENAL TRANSPLANTATION EXPERIENCE WITH 50 PATIENTS (1986) (0)
- [Exploration of immunity in man. Application to immune deficiencies]. (1980) (0)
- [Alpha-1-antitrypsin deficiency and renal involvement]. (1985) (0)
- [Blood transfusions and kidney transplantation]. (1992) (0)
- In memoriam: Professor Renée Habib 1924 - 2009 (2010) (0)
- MP691DELAYED RELEASE CYSTEAMINE IN NEPHROPATHIC CYSTINOSIS PATIENTS AFTER RENAL TRANSPLANT: A SUBGROUP ANALYSIS (2016) (0)
- Renal fine-needle aspiration cytology in transplanted children. (1988) (0)
- Congenital nephrotic syndrome , Finnish type Author : Professor (2004) (0)
- Results of Second Renal Transplantation in Pediatric Patients (1997) (0)
- Clinical features of anti-FH auto antibodies-associated HUS: A typical onset but an atypical outcome (2010) (0)
- Nephrotic Syndrome: Classification and Evaluation (2021) (0)
- Systemic-onset juvenile rheumatoid arthritis and ANCA-associated glomerulonephritis (2008) (0)
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