Stirling Carpenter

Stirling Carpenter's AcademicInfluence.com Rankings

Stirling Carpenter

Medical

#2417

World Rank

#2841

Historical Rank

Neurology

#230

World Rank

#308

Historical Rank

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Stirling Carpenter's Published Works

Number of citations in a given year to any of this author's works

Total number of citations to an author for the works they published in a given year. This highlights publication of the most important work(s) by the author

Published Works

Neurologic sequelae of domoic acid intoxication due to the ingestion of contaminated mussels. (1990) (523)
Mutations in a gene encoding a novel protein tyrosine phosphatase cause progressive myoclonus epilepsy (1998) (479)
Strikingly different clinicopathological phenotypes determined by progranulin-mutation dosage. (2012) (414)
Proximal axonal enlargement in motor neuron disease (1968) (376)
The syndrome of systemic carnitine deficiency (1975) (369)
Clinical Phenotypes of Different MPZ (P0) Mutations May Include Charcot–Marie–Tooth Type 1B, Dejerine–Sottas, and Congenital Hypomyelination (1996) (367)
Expression of immunoreactive major histocompatibility complex products in human skeletal muscles (1988) (301)
Progressive myoclonus epilepsies: specific causes and diagnosis. (1986) (295)
Periventricular and subcortical nodular heterotopia. A study of 33 patients. (1995) (277)
Pathology of Skeletal Muscle (1984) (256)
Myopathy with thick filament (myosin) loss following prolonged paralysis with vecuronium during steroid treatment (1991) (246)
Dystrophin is expressed in mdx skeletal muscle fibers after normal myoblast implantation. (1989) (233)
Small‐caliber skeletal muscle fibers do not suffer necrosis in mdx mouse dystrophy (1988) (231)
Inclusion body myositis (1978) (230)
Dystrophin-deficient mdx muscle fibers are preferentially vulnerable to necrosis induced by experimental lengthening contractions (1990) (219)
Duchenne muscular dystrophy: plasma membrane loss initiates muscle cell necrosis unless it is repaired. (1979) (216)
ELECTRON MICROSCOPIC STUDIES ON THE VASCULAR PERMEABILITY AND THE MECHANISM OF DEMYELINATION IN EXPERIMENTAL ALLERGIC ENCEPHALOMYELITIS. (1965) (212)
Kufs' disease: a critical reappraisal. (1988) (210)
Temporal lobe epilepsy caused by domoic acid intoxication: Evidence for glutamate receptor–mediated excitotoxicity in humans (1995) (208)
Myoclonus epilepsy and ragged-red fibres (MERRF). 1. A clinical, pathological, biochemical, magnetic resonance spectrographic and positron emission tomographic study. (1989) (196)
Relationship between atrophy of the amygdala and ictal fear in temporal lobe epilepsy. (1994) (181)
Subacute necrotizing encephalomyelopathy. A review and a study of two families. (1971) (178)
The childhood type of dermatomyositis (1976) (176)
Experimental ischemic myopathy. (1974) (171)
Neurofibrillary axonal swellings and amyotrophic lateral sclerosis (1984) (165)
Localization and Quantitation of the Chromosome 6-Encoded Dystrophin-Related Protein in Normal and Pathological Human Muscle (1993) (146)
Small-caliber skeletal muscle fibers do not suffer deleterious consequences of dystrophic gene expression. (1986) (144)
Mitochondrial dysfunction in multiple symmetrical lipomatosis (1991) (139)
The Kearns-Shy syndrome. A multisystem disease with mitochondrial abnormality demonstrated in skeletal muscle and skin. (1973) (134)
Creutzfeldt‐Jakob disease presenting as isolated aphasia (1989) (133)
Experimental core-like lesions and nemaline rods. A correlative morphological and physiological study. (1972) (130)
In vivo muscle magnetic resonance spectroscopy in the clinical investigation of mitochondria1 disease (1991) (129)
Glucocorticoid excess induces preferential depletion of myosin in denervated skeletal muscle fibers (1987) (128)
Sweat gland duct cells in Lafora disease (1981) (127)
The ultrastructural characteristics of the abnormal cytosomes in Batten-Kufs' disease. (1977) (122)
Specific involvement of muscle, nerve, and skin in late infantile and juvenile amaurotic idiocy (1972) (120)
Cardiac myxoma (1976) (118)
Chronic inflammatory demyelinating polyneuropathy (CIDP) in diabetics (1996) (118)
Injury of neck as cause of vertebral artery thrombosis. (1961) (116)
Loss and renewal of thick myofilaments in glucocorticoid‐treated rat soleus after denervation and reinnervation (1992) (115)
Cathepsin F mutations cause Type B Kufs disease, an adult-onset neuronal ceroid lipofuscinosis. (2013) (107)
Late‐onset mitochondrial myopathy (1995) (103)
Glycogen branching enzyme deficiency in adult polyglucosan body disease (1993) (100)
Myopathy caused by a deficiency of Ca2+‐adenosine triphosphatase in sarcoplasmic reticulum (Brody's disease) (1986) (100)
A new concept of childhood nemaline myopathy. (1971) (92)
Giant axonal neuropathy. A clinically and morphologically distinct neurological disease. (1974) (89)
Identification of retinoyl complexes as the autofluorescent component of the neuronal storage material in Batten disease (1977) (89)
'Onion bulb' formations in the central and peripheral nervous system in association with multiple sclerosis and hypertrophic polyneuropathy. (1977) (88)
Lectin histochemistry of human skeletal muscle. (1981) (86)
Action myoclonus-renal failure syndrome: characterization of a unique cerebro-renal disorder. (2004) (85)
A pathologic basis for Kleine-Levin syndrome. (1982) (81)
Combined central and peripheral myelinopathy (1987) (77)
The neurotoxins 2,5‐hexanedione and acrylamide promote aggregation of intermediate filaments in cultured fibroblasts (1983) (77)
Hereditary motor and sensory neuropathy with agenesis of the corpus callosum (2003) (76)
Lafora disease. (2016) (72)
Clinical spectrum of mitochondrial DNA mutation at base pair 8344 (1991) (67)
Type I muscle fibre atrophy and central nuclei. A rare familial neuromuscular disease. (1970) (65)
An ultrastructural study of an acute fatal case of the Guillain-Barré syndrome. (1972) (63)
The adult form of acid maltase (α‐1,4‐glucosidase) deficiency (1977) (60)
Lafora's disease (1974) (59)
Time Course of Cerebral Blood Flow and Histological Outcome After Focal Cerebral Ischemia in Rats (1992) (58)
A type of juvenile cerebromacular degeneration characterized by granular osmiophilic deposits. (1973) (58)
Familial inclusion body myositis among Kurdish-Iranian Jews. (1991) (58)
Diffuse craniospinal seeding from a benign fourth ventricle choroid plexus papilloma. Case report. (1998) (57)
Familial infantile cerebellar atrophy associated with retinal degeneration. (1966) (54)
Segmental Necrosis and Its Demarcation in Experimental Micropuncture Injury of Skeletal Muscle Fibers (1989) (54)
Age-Related Conversion of Dystrophin-Negative to -Positive Fiber Segments of Skeletal but not Cardiac Muscle Fibers in Heterozygote mdx Mice (1990) (53)
Pathology of the inflammatory myopathies. (1993) (52)
Dystrophin is localized to the plasma membrane of human skeletal muscle fibers by electron‐microscopic cytochemical study (1990) (52)
Necrosis of capillaries in denervation atrophy of human skeletal muscle (1982) (52)
Conspicuous accumulation of a single-stranded DNA binding protein in skeletal muscle fibers in inclusion body myositis. (1994) (52)
The motor unit profile of the rat soleus in experimental myopathy and reinnervation (1974) (52)
Familial myopathy with changes resembling inclusion body myositis and periventricular leucoencephalopathy. A new syndrome. (1988) (52)
The effect of muscle hyper- and hypoactivity upon fibre diameters of intact and regenerating nerves. (1973) (50)
THE EFFECT OF VINCRISTINE ON SKELETAL MUSCLE IN THE RAT: A Correlative Histochemical, Ultrastructural and Chemical Study (1972) (49)
Experimental mitochondrial myopathy produced by in vivo uncoupling of oxidative phosphorylation (1975) (47)
Fatal infantile glycogen storage disease (1981) (46)
SANDO: Two novel mutations in POLG1 gene (2006) (45)
The clinical consequences of X-chromosome inactivation: Duchenne muscular dystrophy in one of monozygotic twins (1987) (45)
Genetic locus heterogeneity in Lafora's progressive myoclonus epilepsy (1999) (41)
Vacuolar myelopathy in transgenic mice expressing human immunodeficiency virus type 1 proteins under the regulation of the myelin basic protein gene promoter (1996) (40)
The major inflammatory myopathies of unknown cause. (1981) (40)
Hexosaminidase-A deficiency presenting as atypical juvenile-onset spinal muscular atrophy. (1985) (39)
Juvenile dystonic lipidosis (1977) (39)
Action myoclonus-renal failure syndrome: a previously unrecognized neurological disorder unmasked by advances in nephrology. (1986) (38)
Progressive dystonia with bilateral putaminal hypodensities. (1987) (38)
Infantile myotonic dystrophy (1973) (37)
Glucocorticoids and immunosup pressants do not change the prevalence of necrosis and regeneration in mdx skeletal muscles (1991) (37)
Adult onset motor neuronopathy in the juvenile type of hexosaminidase A and B deficiency (1988) (37)
Morphological diagnosis and misdiagnosis in Batten-Kufs disease. (1988) (37)
Major Alteration of the Pathological Phenotype in Gamma Irradiated mdx Soleus Muscles (1991) (36)
Pathological involvement of primary sensory neurons in Werdnig-Hoffmann disease (1978) (36)
Letter to the editor: Subtypes of the histochemical type I muscle fibers. (1975) (34)
Virus‐like filaments and phospholipid accumulation in skeletal muscle (1970) (34)
Metabolic and Histological Reversibility of Thiamine Deficiency (1983) (34)
Inclusion Body Myositis, a Review (1996) (34)
Simulation of Brain Death from Fulminant De-efferentation (2003) (34)
Vacuolation of Muscle Fibers Near Sarcolemmal Breaks Represents T-Tubule Dilatation Secondary to Enhanced Sodium Pump Activity (1988) (33)
Immunocytochemical studies of intermediate filament aggregates and their relationship to microtubules in cultured skin fibroblasts from patients with giant axonal neuropathy. (1983) (32)
CENTRAL NERVOUS SYSTEM EFFECTS OF LASER RADIATION. (1965) (32)
In vivo magnetic resonance spectroscopy of brain and muscle in a type of mitochondrial encephalomyopathy (MERRF) (1991) (32)
Neurofilament subunit–related proteins in neuronal intranuclear inclusions (1984) (32)
Kufs disease: clinical features and forms. (1988) (31)
Neurological sequelae of domoic acid intoxication. (1990) (31)
A peculiar polysaccharide accumulation in muscle in a case of cardioskeletal myopathy (1969) (30)
Cylindrical spirals in human skeletal muscle (1979) (30)
The Pathological Diagnosis of Specific Inflammatory Myopathies (1991) (29)
Subacute skeletal myopathy induced by 2,4‐dichlorophenoxyacetate in rats and guinea pigs (1978) (29)
Muscle pain associated with tubular aggregates and structures resembling cylindrical spirals (1989) (29)
Prevention of skeletal muscle fiber necrosis in hamster dystrophy (1982) (28)
Correlative multidisciplinary approach to the study of mitochondrial encephalomyopathies. (1991) (27)
Three familial midline malformtion syndromes of the central nervous system: agenesis of the corpus callosum and anterior horn-cell disease; agenesis of cerebellar vermis; and atrophy of the cerebellar vermis. (1975) (25)
Diagnosis and misdiagnosis of adult neuronal ceroid lipofuscinosis (Kufs disease) (2016) (25)
The Ramsay Hunt syndrome is no longer a useful diagnostic category (1989) (24)
Congenital inflammatory myopathy (1990) (24)
Hereditary sensory neuropathy (1985) (24)
Hypophysectomy mitigates skeletal muscle fiber damage in hamster dystrophy (1985) (23)
A hypothesis for the pathogenesis of amyotrophic lateral sclerosis. (1988) (23)
The Newfoundland aggregate of neuronal ceroid-lipofuscinosis. (1988) (22)
Rud syndrome: congenital ichthyosis, hypogonadism, mental retardation, retinitis pigmentosa and hypertrophic polyneuropathy. (1982) (21)
Inhibition of myosatellite cell proliferation by gamma irradiation does not prevent the age-related increase of the number of dystrophin-positive fibers in soleus muscles of mdx female heterozygote mice. (1991) (21)
Adult-onset leukodystrophy with axonal spheroids (2010) (21)
Kufs disease due to mutation of CLN6: clinical, pathological and molecular genetic features (2018) (20)
New observations in reducing body myopathy (1985) (20)
Metachromatic leukodystrophy: Multiple nonfunctional and pseudodeficiency alleles in a pedigree: Problems with diagnosis and counseling (1993) (20)
Ultrastructural findings in lafora disease (1981) (20)
Lysosomal storage in human skeletal muscle. (1986) (20)
Syndrome of systemic carnitine deficiency: Clinical, morphologic, biochemical, and pathophysiologic features (2011) (20)
Multiple peripheral nerve entrapments. An unusual phenotypical variant of the Hunter syndrome (mucopolysaccharidosis II) in a family. (1974) (20)
Prenatal axonal dystrophy and osteopetrosis. (1973) (19)
A histochemical study of oxidative enzymes in the nervous system of vitamin E‐deficient rats (1965) (19)
Reserpine induced alteration of physiological properties and histochemical fiber types in rat skeletal muscle (1975) (18)
Myopathy with trabecular muscle fibers (1999) (18)
Skeletal Muscle Pathology (1984) (17)
Sweat gland vacuoles in Unverricht‐Lundborg disease (1994) (16)
Myopathy with hexagonally cross‐linked tubular arrays: A new autosomal dominant or sporadic congenital myopathy (1999) (16)
An experimental morphometric study of neutral lipid accumulation in skeletal muscles (1981) (16)
Reinnervation is followed by necrosis in previously denervated skeletal muscles of dystrophic hamsters (1983) (15)
Histopathological evidence of Fabry disease in a female patient with left ventricular noncompaction. (2014) (15)
Familial myopathy with conspicuous depletion of mitochondria in muscle fibers: a morphologically distinct disease (1995) (14)
Mitochondrial Encephalomyopathies: A Solution to the Enigma of the Ramsay Hunt Syndrome (1987) (13)
Cerebral Vein Thrombosis due to Hereditary Antithrombin III Deficiency (1993) (12)
The human neuropathology of encephalopathic mussel toxin poisoning. (1990) (12)
Progressive myoclonus epilepsy in young adults with neuropathologic features of Alzheimer's disease (1997) (11)
Skin biopsy for diagnosis of hereditary neurologic metabolic disease. (1987) (11)
Calcium paradox in skeletal muscles: Physiologic and microscopic observations (1986) (11)
Antiepileptic drug myopathy (1994) (10)
“Killer” cell activity in Duchenne muscular dystrophy (1986) (9)
The Pathology of the Andermann Syndrome (1994) (8)
Subacute enlarging cerebral hematoma from amyloid angiopathy: case report. (1995) (8)
Morphological Diagnostic and Pathological Considerations (2011) (7)
Atypical inclusion body progressive myoclonus epilepsy (1986) (6)
10 – Resin Histology and Electron Microscopy in Inflammatory Myopathies (1988) (6)
The effects of muscle hyper- and hypoactivity upon fiber diameters of intact and regenerating nerves. (1973) (5)
Primary Bilateral Thalamic Astrocytoma Presenting With Head Tremor, Ataxia, and Dementia (2010) (5)
Familial multiple peripheral nerve entrapments--an unusual manifestation of a peripheral neuropathy. (1973) (5)
Variant Creutzfeldt–Jakob disease: the first confirmed case from Portugal shows early onset, long duration and unusual pathology (2009) (5)
A novel type of familial proximal axonal dystrophy: three cases and a review of the axonal dystrophies. (2012) (4)
Type 2 GM1 gangliosidosis and neuronal ceroid lipofuscinosis (1982) (4)
Calcium-induced damage of skeletal muscle fibers is markedly reduced by calcium channel blockers (2004) (4)
ADULT POLYGLUCOSAN BODY AXONOPATHY - A DISTINCT CHRONIC NEUROLOGICAL DISEASE (1978) (4)
Maturational arrest. (1976) (4)
Effects of lidocaine on the lysosomes of cultured skin fibroblasts. (1982) (3)
Muscle Biopsy for Diagnosis of Neuromuscular and Metabolic Diseases (2015) (3)
Virus like filaments and phospholipid accumulations in a case of chronic myopathy. (1971) (3)
Sporadic Creutzfeldt-Jakob Disease Causing a 2-Years Slowly Progressive Isolated Dementia (2009) (3)
The motor unit profile in two experimental chronic myopathies (1975) (3)
Regeneration of skeletal muscle fibers after necrosis. (1990) (2)
PERIPHERAL NERVE PATHOLOGY IN THE SYNDROME OF AGENESIS OF THE CORPUS CALLOSUM WITH PERIPHERAL NEUROPATHY (1985) (2)
Teaching NeuroImages: Neuropathy caused by Mycobacterium leprae (2011) (2)
Granulomatous infectious disease in an immunosuppressed patient: a case report with radiological and pathological correlation. (2009) (2)
A distinctive type of infantile inflammatory myopathy with abnormal myonuclei (1996) (2)
Neuroaxonal dystrophy and osteopetrosis (1978) (2)
Histopathological evidence of Fabry disease in a female patient with left ventricular noncompaction (2014) (2)
The Ultrastructure of Demyelination in a Case of Acute Guillain-Barré Syndrome (1970) (2)
A chronic myopathy with coated vesicles and tubular masses (1992) (2)
Cortical Metabolic Dysfunction in a Mitochondrial Encephalomyopathy (MERRF) Demonstrated by Positron Emission Tomography (1987) (2)
In Memoriam: Morrison H. Finlayson, M.B. Ch.B., F.R.C.P. (C) (1929-1982) (1983) (1)
Retinitis pigmentosa in Lafora disease: Expanding findings of progressive myoclonic epilepsy (2016) (1)
Letters to the editor (1991) (1)
George Karpati O.C., C.Q., M.D., FRCPC, FRS (C) 1934–2009 (2009) (1)
Variant Creutzfeldt-Jakob [corrected] disease: the second case in Portugal and in the same geographical region. (2008) (1)
Case report SANDO: Two novel mutations in POLG1 gene (2006) (0)
Jakob-Creutzfeldt Disease Presenting as Isolated Aphasia (1987) (0)
Infantile neuroaxonal dystrophy with urinary oligosaccharide excretion not due to defective α-N- acetylgalactosaminidase activity (1994) (0)
LUXOL FAST BLUE DISTINGUISHES LIPOFUSCIN FROM THE STORAGE DEPOSITS OF TYPICAL LATE INFANTILE AND JUVENILE BATTENʼS DISEASE: 260 (1990) (0)
Mitochondrial myopathy in primary biliary cirrhosis an antibody mediated mitochondrial cytopathy (1988) (0)
Expression of immunoreactive major histocompatibility complex determinants in normal and pathological human muscles (1987) (0)
THE CURVILINEAR BODIES OF LATE INFANTILE BATTENʼS DISEASE-ISOLATION AND CHEMICAL AND ULTRASTRUCTURAL CHARACTERIZATION: 90 (1976) (0)
Tracer and marker techniques in the microscopic study of skeletal muscles. (1981) (0)
Late-onset seizures and dementia in MELAS syndrome (1992) (0)
Experimental vincristine myopathy--a histochemical, ultrastructural and biochemical study. (1971) (0)
[Myositis with inclusion bodies]. (1989) (0)
Prominent T-Tubule Dilatation in Muscle Fibers Near Sarcolemmal Breaks: An In Vitro Model (1987) (0)
144. Lectin Cytochemistry of Spinal Cord and Roots. (1982) (0)
145 HOW NECROSIS IS DEMARCATED IN SKELETAL MUSCLE FIBERS AFTER EXPERIMENTAL MICROPUNCTURE INJURY (1984) (0)
Central and peripheral demyelinization (1988) (0)
Familial Adult-onset Motor Neuronopathy Due to a β-Locus Hexosaminidase Mutation (1987) (0)
Familial Inclusion Body Myopathy with Periventricular Leukodystrophy: A Newly Recognized Syndrome (1987) (0)
Focal myositis with neurogenic atrophy: A case report. (2018) (0)
Nervous Tissue, Non-Neural Components of (2003) (0)
Central nervous system Ä ^ effects of laser radiation 1 copy ~ WPW COPY DDC r ? f ^ r ? nnnr ? (0)
Histology and histopathology of the nervous system. Edited by Webb Haymaker and Raymond Adams, 2 vol, 2,597 pp, illus, Charles C. Thomas, Springfield, Illinois, 1982. $295.00 (1983) (0)
Unusual Evolution and Computerized Tomographic Appearance of a Gliosarcoma (1994) (0)
Neuroaxonal dystrohpy and osteopetrosis. (1978) (0)
Autosomal dominant Kufs` disease: Clinical heterogeneity in nine families, and exclusion of linkage to CLN1 and CLN3 markers in a large American kindred (1994) (0)
What happens to capillaries in de nervated muscles (1980) (0)
Expression of Immunoreactive Class 1 Major Histocompatibility Complex (MHC) Determinants in Pathologic Human Skeletal Muscle Fibers (1987) (0)
Primary bilateral thalamic astrocytoma presenting with head tremor, ataxia, and dementia. (2010) (0)

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What Schools Are Affiliated With Stirling Carpenter?

Stirling Carpenter is affiliated with the following schools:

McGill University

Stirling Carpenter's Academic­Influence.com Rankings

Why Is Stirling Carpenter Influential?

Stirling Carpenter's Published Works

Published Works

What Schools Are Affiliated With Stirling Carpenter?

Stirling Carpenter's AcademicInfluence.com Rankings