W. King Engel
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(Suggest an Edit or Addition)W. King Engel's Published Works
Number of citations in a given year to any of this author's works
Total number of citations to an author for the works they published in a given year. This highlights publication of the most important work(s) by the author
Published Works
- Mammalian Motor Units: Physiological-Histochemical Correlation in Three Types in Cat Gastrocnemius (1971) (763)
- Rapid examination of muscle tissue (1963) (503)
- NEMALINE MYOPATHY. A NEW CONGENITAL MYOPATHY. (1963) (439)
- The histographic analysis of human muscle biopsies with regard to fiber types (1969) (372)
- Ocular motor abnormalities in hereditary cerebellar ataxia. (1976) (344)
- Slow saccades in spinocerebellar degeneration. (1976) (296)
- Chronic relapsing (Dysimmune) polyneuropathy: Pathogenesis and treatment (1981) (272)
- Vascular deposits of immunoglobulin and complement in idiopathic inflammatory myopathy. (1972) (268)
- Oculocraniosomatic Neuromuscular Disease With Ragged-Red Fibers: Histochemical and Ultrastructural Changes in Limb Muscles of a Group of Patients With Idiopathic Progressive External Ophthalmoplegia (1972) (261)
- Selective and nonselective susceptibility of muscle fiber types. A new approach to human neuromuscular diseases. (1970) (253)
- The histographic analysis of human muscle biopsies with regard to fiber types (1969) (236)
- Neuromuscular disease in primary hyperparathyroidism. (1974) (227)
- The histographic analysis of human muscle biopsies with regard to fiber types (1969) (215)
- “Type grouping” in skeletal muscles after experimental reinnervation (1968) (199)
- HISTOCHEMICAL STUDIES OF DENERVATED OR TENOTOMIZED CAT MUSCLE: ILLUSTRATING DIFFICULTIES IN RELATING EXPERIMENTAL ANIMAL CONDITIONS TO HUMAN NEUROMUSCULAR DISEASES (1966) (198)
- Adrenomyeloneuropathy: A probable variant of adrenoleukodystrophy I. Clinical and endocrinologic aspects (1977) (195)
- Correlative histochemical study of skeletal muscle after suprasegmental denervation, peripheral nerve section, and skeletal fixation (1968) (192)
- Frameshift and novel mutations in FUS in familial amyotrophic lateral sclerosis and ALS/dementia (2010) (192)
- EFFECT ON WEAKNESS AND SPASTICITY IN AMYOTROPHIC LATERAL SCLEROSIS OF THYROTROPIN-RELEASING HORMONE (1983) (183)
- MYASTHENIA GRAVIS: A SERUM FACTOR BLOCKING ACETYLCHOLINE RECEPTORS OF THE HUMAN NEUROMUSCULAR JUNCTION (1975) (178)
- Endoplasmic reticulum stress and unfolded protein response in inclusion body myositis muscle. (2004) (176)
- Duchenne Muscular Dystrophy: Functional Ischemia Reproduces Its Characteristic Lesions (1971) (168)
- Inclusion-body myositis (2006) (159)
- A new program for investigating adult human skeletal muscle grown aneurally in tissue culture (1975) (155)
- Polyneuropathy with monoclonal gammopathy: Studies of 11 patients (1981) (154)
- Immunoglobulin and complement deposits in nerves of patients with chronic relapsing polyneuropathy. (1980) (152)
- The histographic analysis of human muscle biopsies with regard to fiber types (1969) (149)
- Transfer of beta-amyloid precursor protein gene using adenovirus vector causes mitochondrial abnormalities in cultured normal human muscle. (1996) (148)
- THYMIC EPITHELIAL CELL CONTAINS ACETYLCHOLINE RECEPTOR (1977) (146)
- Light and electron microscopic localization of beta-amyloid protein in muscle biopsies of patients with inclusion-body myositis. (1992) (144)
- Tubular aggregates in type II muscle fibers: ultrastructural and histochemical correlation. (1970) (143)
- Inclusion‐Body Myositis: Newest Concepts of Pathogenesis and Relation to Aging and Alzheimer Disease (2001) (141)
- The essentiality of histo- and cytochemical studies of skeletal muscle in the investigation of neuromuscular disease (1962) (140)
- Impaired skeletal muscle maturation following neonatal neurectomy. (1968) (137)
- Twisted tubulofilaments of inclusion body myositis muscle resemble paired helical filaments of Alzheimer brain and contain hyperphosphorylated tau. (1994) (137)
- Cardiac manifestations in polymyositis. (1978) (135)
- Inclusion Body Myositis: A Degenerative Muscle Disease Associated with Intra‐Muscle Fiber Multi‐Protein Aggregates, Proteasome Inhibition, Endoplasmic Reticulum Stress and Decreased Lysosomal Degradation (2009) (132)
- β‐Amyloid precursor epitopes in muscle fibers of inclusion body myositis (1993) (130)
- Cytological localization of cholinesterase in developing chick embryo skeletal muscle. (1961) (128)
- Benefit from alternate-day prednisone in myasthenia gravis. (1972) (125)
- Inclusion-body myositis: muscle-fiber molecular pathology and possible pathogenic significance of its similarity to Alzheimer’s and Parkinson’s disease brains (2008) (124)
- Type I fiber hypotrophy and central nuclei. A rare congenital muscle abnormality with a possible experimental model. (1968) (123)
- Axonal Transport of Proteins in Experimental Neuropathies (1969) (117)
- Acetazolamide treatment of hypokalemic periodic paralysis. Prevention of attacks and improvement of persistent weakness. (1970) (116)
- Enhanced detection of Congo‐red‐positive amyloid deposits in muscle fibers of inclusion body myositis and brain of Alzheimer's disease using fluorescence technique (1993) (114)
- SCANNING FOR SOFT-TISSUE AMYLOID (1977) (111)
- Sporadic inclusion-body myositis and hereditary inclusion-body myopathies: current concepts of diagnosis and pathogenesis. (1998) (111)
- Muscle Target Fibres, a Newly Recognized Sign of Denervation (1961) (111)
- Clinical studies of a patient with pyruvate decarboxylase deficiency. (1971) (105)
- Proteasome inhibition and aggresome formation in sporadic inclusion-body myositis and in amyloid-beta precursor protein-overexpressing cultured human muscle fibers. (2005) (104)
- De novo neuromuscular junction formation on human muscle fibres cultured in monolayer and innervated by foetal rat spinal cord: Ultrastructural and ultrastructural-cytochemical studies (1987) (103)
- Inclusion-body myositis and myopathies: different etiologies, possibly similar pathogenic mechanisms (2002) (103)
- Collagen localization in normal and fibrotic human skeletal muscle. (1981) (103)
- Central core disease-an investigation of a rare muscle cell abnormality. (1961) (103)
- Neuromuscular disease in secondary hyperparathyroidism. (1975) (103)
- Histochemical investigation of fiber type ratios with the myofibrillar ATP-ase reaction in normal and denervated skeletal muscles of guinea pig. (1968) (102)
- Difference in Expression of Phosphorylated Tau Epitopes between Sporadic Inclusion‐body Myositis and Hereditary Inclusion‐body Myopathies (1996) (101)
- Myoclonic epilepsy and ragged‐red fibers with cytochrome oxidase deficiency: Neuropathology, biochemistry, and molecular genetics (1989) (100)
- An inherited disease similar to amyotrophic lateral sclerosis with a pattern of posterior column involvement. An intermediate form? (1959) (100)
- New advances in the understanding of sporadic inclusion‐body myositis and hereditary inclusion‐body myopathies (1995) (100)
- Experimental myopathy after microarterial embolization; comparison with childhood x-linked pseudohypertrophic muscular dystrophy. (1970) (99)
- Late-Onset Type of Skeletal-Muscle Phosphorylase Deficiency (1963) (98)
- beta-Amyloid precursor protein mRNA is increased in inclusion-body myositis muscle. (1993) (95)
- Immunolocalization of ubiquitin in muscle biopsies of patients with inclusion body myositis and oculopharyngeal muscular dystrophy (1991) (94)
- Impaired autophagy in sporadic inclusion-body myositis and in endoplasmic reticulum stress-provoked cultured human muscle fibers. (2010) (93)
- Inclusion-body myositis, a multifactorial muscle disease associated with aging: current concepts of pathogenesis (2007) (93)
- Thyrotropin‐Releasing Hormone Enhances Choline Acetyltransferase and Creatine Kinase in Cultured Spinal Ventral Horn Neurons (1984) (92)
- Atrophy of skeletal muscle in patients with Cushing's syndrome. (1970) (91)
- Oculocraniosomatic neuromuscular disease with "ragged-red" fibers. (1972) (91)
- Novel Immunolocalization of α‐Synuclein in Human Muscle of Inclusion‐Body Myositis, Regenerating and Necrotic Muscle Fibers, and at Neuromuscular Junctions (2000) (91)
- Human muscle cultured in monolayer and cocultured with fetal rat spinal cord: importance of dorsal root ganglia for achieving successful functional innervation (1987) (91)
- Neuronal trophic function. A new aspect demonstrated histochemically in developing soleus muscle. (1967) (89)
- Acetazolamide prophylaxis in hypokalemic periodic paralysis. (1968) (88)
- The hemostatic imbalance of plasma-exchange transfusion. (1979) (87)
- Muscle biopsies in neuromuscular diseases. (1967) (85)
- Proposed pathogenetic cascade of inclusion-body myositis: importance of amyloid-&bgr;, misfolded proteins, predisposing genes, and aging (2003) (84)
- A skeletal-muscle disorder associated with intermittent symptoms and a possible defect of lipid metabolism. (1970) (84)
- Sporadic inclusion-body myositis: A degenerative muscle disease associated with aging, impaired muscle protein homeostasis and abnormal mitophagy. (2015) (82)
- New advances in inclusion-body myositis. (1993) (81)
- Transformation of the Histochemical Profile of Skeletal Muscle by “Foreign” Innervation (1967) (80)
- Inclusion-body myositis (2006) (76)
- A histochemical-physiological correlation of frog skeletal muscle fibers. (1967) (75)
- Substance P in human cerebrospinal fluid (1980) (74)
- Tremor as a feature of chronic relapsing and dysgammaglobulinemic polyneuropathies. Incidence and management. (1984) (73)
- Human schwann cells in tissue culture: histochemical and ultrastructural studies. (1980) (73)
- Increase of nitric oxide synthases and nitrotyrosine in inclusion‐body myositis (1996) (73)
- Malignant hyperthermia and central core disease in a child with congenital dislocating hips. (1978) (72)
- ULTRASTRUCTURAL STUDY OF A PERIPHERAL NERVE BIOPSY IN REFSUM'S DISEASE (1969) (71)
- MY ASTHENIA GRAVIS: A NEW HYPOTHESIS OF THE PATHOGENESIS AND A NEW FORM OF TREATMENT (1971) (70)
- NEMALINE MYOPATHY; A SECOND CASE. (1964) (69)
- The fine structure of type II muscle fiber atrophy (1971) (69)
- LEUKÆMIA AND LOWER-MOTOR-NEURON DISEASE (1974) (68)
- Histochemical and contractile properties in the cross-innervated guinea pig soleus muscle. (1969) (68)
- Histochemistry of muscle in infantile spinal muscular atrophy (1963) (68)
- Increased Plasma Enzyme Concentrations in Rats with Functional Ischaemia of Muscle provide a Possible Model of Duchenne Muscular Dystrophy (1972) (68)
- Effects of acetazolamide on myotonia (1978) (67)
- Histochemistry of rat intrafusal muscle fibers and their motor innervation. (1978) (67)
- Pathogenic Considerations in Sporadic Inclusion-Body Myositis, a Degenerative Muscle Disease Associated With Aging and Abnormalities of Myoproteostasis (2012) (67)
- Amyloidosis with plasma cell dyscrasia. An overlooked caused of adult onset sensorimotor neuropathy. (1977) (66)
- βAPP gene transfer into cultured human muscle induces inclusion‐body myositis aspects (1997) (66)
- Refsum's disease--a recently characterized lipidosis involving the nervous system. Combined clinical staff conference at the National Institutes of Health. (1967) (65)
- Sporadic inclusion-body myositis and its similarities to Alzheimer disease brain. Recent approaches to diagnosis and pathogenesis, and relation to aging. (1998) (65)
- Neuropathy in Tangier disease. Alpha-Lipoprotein deficiency manifesting as familial recurrent neuropathy and intestinal lipid storage. (1967) (65)
- Sporadic inclusion-body myositis: conformational multifactorial ageing-related degenerative muscle disease associated with proteasomal and lysosomal inhibition, endoplasmic reticulum stress, and accumulation of amyloid-β42 oligomers and phosphorylated tau. (2011) (65)
- Prion protein is abnormally accumulated in inclusion‐body myositis (1993) (64)
- Mutant ubiquitin UBB+1 is accumulated in sporadic inclusion-body myositis muscle fibers (2004) (63)
- Abnormal accumulation of prion protein mRNA in muscle fibers of patients with sporadic inclusion-body myositis and hereditary inclusion-body myopathy. (1994) (63)
- Phytanic acid in patients with Refsum's syndrome and response to dietary treatment. (1970) (63)
- Sporadic inclusion-body myositis and hereditary inclusion-body myopathies: diseases of oxidative stress and aging? (1998) (63)
- Focal myopathic changes produced by electromyographic and hypodermic needles. "Needle myopathy". (1967) (62)
- Open-biopsy electromyography. I. Correlation of motor unit behavior with histochemical muscle fiber type in human limb muscle. (1972) (62)
- ALKALINE PHOSPHATASE-POSITIVE ABNORMAL MUSCLE FIBERS OF HUMANS (1970) (61)
- Light and electron microscopic immunolocalization of presenilin 1 in abnormal muscle fibers of patients with sporadic inclusion-body myositis and autosomal-recessive inclusion-body myopathy. (1998) (61)
- Histochemistry of motor neurons and interneurons in the cat lumbar spinal cord (1970) (61)
- CYTOLOGICAL LOCALIZATION OF CHOLINESTERASE IN CULTURED SKELETAL MUSCLE CELLS (1961) (60)
- Fiber‐type nomenclature of human skeletal muscle for histochemical purposes (1974) (60)
- Homocysteine‐induced endoplasmic reticulum protein (Herp) is up‐regulated in sporadic inclusion‐body myositis and in endoplasmic reticulum stress‐induced cultured human muscle fibers (2006) (59)
- Studies of plasma insulin in myotonic dystrophy. (1969) (59)
- Ultrastructural localization of calcium in normal and abnormal skeletal muscle. (1977) (59)
- beta-Amyloid precursor epitopes in muscle fibers of inclusion body myositis. (1993) (59)
- ABUNDANT NUCLEAR RODS IN ADULT‐ONSET ROD DISEASE (1975) (58)
- ISOZYME HISTOCHEMISTRY: THE DISPLAY OF SELECTIVE LACTATE DEHYDROGENASE ISOZYMES IN SECTIONS OF SKELETAL MUSCLE (1964) (58)
- Intravenous treatment of hypokalemic periodic paralysis. (1983) (57)
- Histochemistry of the Myotonic Disorders (1966) (57)
- CSF “monoclonal” bands in chronic relapsing polyneuropathy (1980) (56)
- Reversal of the ATPase Reaction in Muscle Fibres By EDTA (1966) (56)
- Histochemical Phosphorylase Activity in Regenerating Muscle Fibers from Myophosphorylase-Deficient Patients (1972) (56)
- Expression of muscle-gene-specific isozymes of phosphorylase and creatine kinase in innervated cultured human muscle (1986) (56)
- Use of anti‐neurofilament antibody to identify paired‐helical filaments in inclusion‐body myositis (1996) (56)
- β-amyloid protein immunoreactivity in muscle of patients with inclusion-body myositis (1992) (56)
- Strong immunoreactivity of β-amyloid precursor protein, including the β-amyloid protein sequence, at human neuromuscular junctions (1992) (56)
- Immunocytochemical localization of ubiquitin in inclusion body myositis allows its light‐microscopic distinction from polymyositis (1992) (55)
- Adult-onset acid maltase deficiency. Morphologic and biochemical abnormalities reproduced in in cultured muscle. (1976) (55)
- MITOCHONDRIAL AGGREGATES IN MUSCLE DISEASE (1964) (55)
- Remarkable recovery of a steroid-responsive recurrent polyneuropathy. (1970) (54)
- Immunocytochemical localization of thymosin-α 1 in thymic epithelial cells of normal and myasthenia gravis patients and in thymic cultures (1981) (54)
- Serotonin and platelet function in Duchenne muscular dystrophy. (1973) (54)
- Assessment: Symptomatic Treatment for Muscle Cramps (An Evidence-Based Review): Report of the Therapeutics and Technology Assessment Subcommittee of The American Academy of Neurology (2010) (54)
- Impaired innervation of cultured human muscle overexpressing βAPP experimentally and genetically: relevance to inclusion‐body myopathies (1998) (53)
- Prion protein is strongly immunolocalized at the postsynaptic domain of human normal neuromuscular junctions (1993) (53)
- Immunocytochemical localization of desmin at human neuromuscular junctions (1990) (53)
- Distinct subtypes of type I fibers of human skeletal muscle (1975) (52)
- Glucose metabolism in five neuromuscular disorders (1968) (52)
- Brief, small, abundant motor‐unit action potentials (1975) (51)
- EFFECTS OF PHENAZINE METHOSULFATE IN HISTOCHEMISTRY (1964) (51)
- Endoplasmic reticulum stress induces myostatin precursor protein and NF-κB in cultured human muscle fibers: Relevance to inclusion body myositis (2007) (51)
- Immunolocalization of transcription factor NF-κB in inclusion-body myositis muscle and at normal human neuromuscular junctions (1998) (51)
- Histochemical Abnormalities of Skeletal Muscle in Patients with Acute Psychoses (1970) (50)
- Abnormalities in cultured muscle and peripheral nerve of a patient with adrenomyeloneuropathy. (1979) (49)
- Treatment of polyneuropathy in Waldenström's macroglobulinemia (1983) (48)
- Presence of BACE1 and BACE2 in muscle fibres of patients with sporadic inclusion-body myositis (2001) (48)
- Apolipoprotein E immunoreactive deposits in inclusion-body muscle diseases (1994) (48)
- Molecular pathology and pathogenesis of inclusion‐body myositis (2005) (48)
- Treatment of “permanent” muscle weakness in familial hypokalemic periodic paralysis (1983) (47)
- INTRAVENOUS IMMUNOGLOBULIN IN RELAPSING-REMITTING MULTIPLE SCLEROSIS: A DOSE-FINDING TRIAL (2009) (46)
- Systemic manifestations of gyrate atrophy of the choroid and retina. (1981) (46)
- HISTOCHEMISTRY AND CYTOCHEMISTRY OF EXPERIMENTALLY DENERVATED GUINEA PIG MUSCLE. I. HISTOCHEMISTRY. (1965) (46)
- Single‐fiber electromyography in neuromuscular disorders: Correlation of muscle histochemistry, single‐fiber electromyography, and clinical findings (1994) (45)
- Localization of technetium‐99m diphosphonate in acutely injured muscle (1977) (44)
- Pyruvate oxidation in neuromuscular diseases (1974) (44)
- Increased circulation of T lymphocytes bearing surface thymosin α1 in patients with myasthenia gravis (1983) (44)
- Three lipoprotein receptors and cholesterol in inclusion-body myositis muscle (2002) (44)
- Idiopathic inflammatory myopathies: inclusion‐body myositis, polymyositis, and dermatomyositis (1994) (43)
- NOGO is increased and binds to BACE1 in sporadic inclusion-body myositis and in AβPP-overexpressing cultured human muscle fibers (2007) (43)
- Ultrastructural and histochemical correlations of experimental muscle regeneration. (1970) (43)
- Novel demonstration of amyloid-β oligomers in sporadic inclusion-body myositis muscle fibers (2010) (43)
- Amyotrophic lateral sclerosis sera applied to cultured motor neurons. (1974) (43)
- Extrajunctional acetylcholine receptors. Alterations in human and experimental neuromuscular diseases. (1976) (42)
- Analog specificity of the thyrotropin-releasing hormone receptor in the central nervous system: possible clinical implications. (1985) (42)
- The skeletal muscle binding site of antistriated muscle antibody in myasthenia gravis: an electron microscopic immunohistochemical study using peroxidase conjugated antibody fragments. (1973) (42)
- Guidelines for the diagnosis and treatment of chronic inflammatory demyelinating polyneuropathy (2003) (42)
- The molecular mechanism of the inherited phosphofructokinase deficiency associated with hemolysis and myopathy. (1980) (41)
- Immunolocalization of Nitric Oxide Synthases at the Postsynaptic Domain of Human and Rat Neuromuscular Junctions—Light and Electron Microscopic Studies (1997) (41)
- Cardiac findings in Charcot-Marie-Tooth disease. A prospective study of 68 patients. (1979) (41)
- ALTERNATE-DAY PREDNISONE IN A PATIENT WITH MYASTHENIA GRAVIS (1970) (41)
- Does Overexpression of βAPP in Aging Muscle Have a Pathogenic Role and a Relevance to Alzheimer’s Disease? : Clues from Inclusion Body Myositis, Cultured Human Muscle, and Transgenic Mice (1998) (41)
- Fourteen Newly Recognized Proteins at the Human Neuromuscular Junctions‐and Their Nonjunctional Accumulation in Inclusion‐Body Myositisa a (1998) (40)
- Myostatin is increased and complexes with amyloid-β within sporadic inclusion-body myositis muscle fibers (2005) (40)
- Luminescent Conjugated Oligothiophenes for Sensitive Fluorescent Assignment of Protein Inclusion Bodies (2013) (40)
- ULTRASTRUCTURAL DEVELOPMENT OF EXPLANTED HUMAN SKELETAL MUSCLE IN TISSUE CULTURE (1972) (39)
- BACE1 and BACE2 in pathologic and normal human muscle (2003) (39)
- POLYMYOSITIS: REMARKABLE RESPONSE TO TOTAL BODY IRRADIATION (1981) (39)
- Histochemistry and acetylcholine receptor distribution in normal and denervated monkey extraocular muscles (1978) (39)
- In AβPP‐overexpressing cultured human muscle fibers proteasome inhibition enhances phosphorylation of AβPP751 and GSK3β activation: effects mitigated by lithium and apparently relevant to sporadic inclusion‐body myositis (2010) (38)
- Histochemical abnormalities of skeletal muscle in acutely psychotic patients. II. (1970) (38)
- Thyrotropin‐releasing hormone enhances motor neuron–evoked contractions of cultured human muscle (1985) (38)
- Association of active extracellular signal-regulated protein kinase with paired helical filaments of inclusion-body myositis muscle suggests its role in inclusion-body myositis tau phosphorylation. (2000) (36)
- Left ventricular relaxation, mitral valve prolapse, and intracardiac conduction in myotonia atrophica: assessment by digitized echocardiography and noninvasive His bundle recording. (1982) (35)
- MYASTHENIA GRAVIS, CORTICOSTEROIDS, ANTICHOLINESTERASES (1976) (35)
- Reincarnation in cultured muscle of mitochondrial abnormalities. Two patients with epilepsy and lactic acidosis. (1978) (35)
- Families with myotonic dystrophy with and without cardiac involvement. (1983) (35)
- 99mTc‐diphosphonate uptake in skeletal muscle (1975) (34)
- Localization of survival motor neuron protein in human apoptotic-like and regenerating muscle fibers, and neuromuscular junctions. (1999) (34)
- Ultrastructural demonstration of calcium in retina, retinal pigment epithelium and choroid. (1977) (34)
- ABNORMAL IMMUNOGLOBULIN BANDS IN CEREBROSPINAL FLUID IN MYASTHENIA GRAVIS (1978) (34)
- The acetylcholine receptor in normal and pathologic states (1976) (33)
- Laser Doppler blood flow studies during open muscle biopsy in patients with neuromuscular diseases (1983) (33)
- Single cholinergic receptor channel currents in cultured human muscle (1982) (32)
- MYOGLOBINÆMIA IN DUCHENNE MUSCULAR DYSTROPHY PATIENTS AND CARRIERS: A NEW ADJUNCT TO CARRIER DETECTION (1978) (32)
- The Motor Unit (1973) (31)
- Asynchronous regulation of muscle specific isozymes of creatine kinase, glycogen phosphorylase, lactic dehydrogenase and phosphoglycerate mutase in innervated and non-innervated cultured human muscle (1988) (31)
- Histochemical and Functional Correlations in Anterior Horn Neurons of the Cat Spinal Cord (1971) (31)
- Subacute sclerosing panencephalitis in only one of identical twins. (1972) (31)
- Adverse interaction between steroid hormones and anticholinesterase drugs (1974) (31)
- Modification by L-dopa of a case of progressive supranuclear palsy. With evidence of defective cerebral dopamine metabolism. (1970) (31)
- Moebius syndrome (1970) (30)
- Long‐Term Treatment with Glucocorticoids Increases Synthesis and Stability of Junctional Acetylcholine Receptors on Innervated Cultured Human Muscle (1993) (30)
- IMMUNOPEROXIDASE LOCALIZATION OF ALPHA BUNGAROTOXIN: A NEW APPROACH TO MYASTHENIA GRAVIS * (1976) (30)
- Endoplasmic reticulum stress induces myostatin precursor protein and NF-kappaB in cultured human muscle fibers: relevance to inclusion body myositis. (2007) (30)
- X-linked recessive congenital muscle fiber hypotrophy with central nuclei: abnormalities of growth and adenylate cyclase in muscle tissue cultures. (1979) (30)
- AN ATTEMPT AT HISTOCHEMICAL LOCALIZATION OF MYOGLOBIN IN SKELETAL MUSCLE BY THE BENZIDINE-PEROXIDASE REACTION (1961) (30)
- Increased BACE1 mRNA and noncoding BACE1-antisense transcript in sporadic inclusion-body myositis muscle fibers—Possibly caused by endoplasmic reticulum stress (2010) (29)
- Leukoencephalopathy in Oculocraniosomatic Neuromuscular Disease With Ragged-Red Fibers: Mitochondrial Abnormalities Demonstrated by Computerized Tomography (1978) (29)
- AβPP-overexpression and proteasome inhibition increase αB-crystallin in cultured human muscle: Relevance to inclusion-body myositis (2006) (29)
- Influence of TRH and TRH Analogues RGH‐2202 and DN‐1417 on Cultured Ventral Spinal Cord Neurons a (1989) (29)
- Amyotrophic lateral sclerosis. A study of central monoamine metabolism and therapeutic trial of levodopa. (1971) (29)
- Nitric oxide-induced oxidative stress in autosomal recessive and dominant inclusion-body myopathies. (1998) (29)
- The histologic diagnosis of neuromuscular diseases: a review of 79 biopsies. (1966) (28)
- Histoenzymatic profile of human muscle cultured in monolayer and innervated de novo by fetal rat spinal cord (1988) (28)
- Muscle-type phosphorylase activity present in muscle cells cultured from three patients with myophosphorylase deficiency. (1977) (28)
- DENERVATION OF MUSCLE IN MYASTHENIA GRAVIS. ROPORT OF A PATIENT WITH MYASTHENIA GRAVIS FOR 47 YEARS AND HISTOCHEMICAL SIGNS OF DENERVATION. (1964) (28)
- Redox factor-1 in muscle biopsies of patients with inclusion-body myositis (2000) (28)
- Hereditary sensory neuropathy. Association with increased synthesis of immunoglobulin A. (1974) (27)
- In sporadic inclusion body myositis muscle fibres TDP‐43‐positive inclusions are less frequent and robust than p62 inclusions, and are not associated with paired helical filaments (2011) (27)
- Immunocytochemical localization of ubiquitin at human neuromuscular junctions (1992) (27)
- Paired helical filaments of inclusion-body myositis muscle contain RNA and survival motor neuron protein. (2000) (27)
- AXONAL TRANSPORT TO AND FROM THE MOTOR NERVE ENDING * (1976) (27)
- Nearly fatal muscle carnitine deficiency with full recovery after replacement therapy (1983) (27)
- Hemopexin metabolism in patients with altered serum levels. (1983) (27)
- In inclusion-body myositis muscle fibers Parkinson-associated DJ-1 is increased and oxidized. (2008) (27)
- Differences in catecholamine-sensitive adenylate cyclase and beta-adrenergic receptor binding between fast-twitch and slow-twitch skeletal muscle membranes. (1979) (27)
- Myotonic lid lag in hypokalaemic periodic paralysis (1967) (26)
- In vitro characterization of skeletal muscle beta-adrenergic receptors coupled to adenylate cyclase. (1979) (26)
- Glucocorticoid increases acetylcholinesterase and organization of the postsynaptic membrane in innervated cultured human muscle (1992) (26)
- Myofibril formation in cultured skeletal muscle cells studied with antimyosin fluorescent antibody (1960) (26)
- Increased expression of Noga-A in ALS muscle biopsies is not unique for this disease. (2006) (26)
- Erythrocyte shape in Duchenne muscular dystrophy (1976) (26)
- Nuclear inclusions in innervated cultured muscle fibers from patients with oculopharyngeal muscular dystrophy (1989) (25)
- Lipid composition of erythrocytes. Findings in Duchenne's muscular dystrophy and myotonic atrophy. (1979) (25)
- Ultrastructural demonstration and analytical application of extrajunctional receptors of denervated human and rat skeletal muscle fibres (1975) (25)
- Demonstration of 2′,3′‐Cyclic Nucleotide 3′‐Phosphohydrolase in Cultured Human Schwann Cells (1982) (25)
- Nitro blue tetrazolium (1966) (25)
- Parkin and its association with alpha-synuclein and AbetaPP in inclusion-body myositis and AbetaPP-overexpressing cultured human muscle fibers. (2006) (25)
- IDENTIFICATION OF HUMAN THYMIC EPITHELIAL CELLS WITH ANTIBODIES TO THYMOSIN α1, IN MYASTHENIA GRAVIS * (1981) (24)
- Developmental expression of the muscle-specific isozyme of phosphoglycerate mutase in human muscle cultured in monolayer and innervated by fetal rat spinal cord (1987) (24)
- Decreased SIRT1 deacetylase activity in sporadic inclusion-body myositis muscle fibers (2010) (24)
- Amyloid in hereditary amyloid polyneuropathy is related to prealbumin. (1981) (23)
- FACTORS INFLUENCING THE CELL TYPE OF BRAIN TUMORS INDUCED IN DOGS BY SCHMIDT‐RUPPIN ROUS SARCOMA VIRUS (1972) (23)
- Reversible ocular myasthenia gravis or mitochondrial myopathy from statins? (2003) (23)
- Thymosin alpha 1 in myasthenia gravis. (1980) (23)
- Adenylate cyclase system of human skeletal muscle: Subcellular distribution and general properties (1978) (23)
- Muscle carnitine deficiency (1983) (23)
- Familial adult-onset proximal spinal muscular atrophy. Report of a family with type II hyperlipoproteinemia. (1970) (23)
- In vitro analysis of the general properties and junctional receptor characteristics of skeletal muscle membranes. Isolation, purification, and partial characterization of sarcolemmal fragments. (1974) (23)
- Subacute sclerosing panencephalitis. Spontaneous improvement in a patient with elevated measles antibody in blood and spinal fluid. (1968) (23)
- Electrophysiologic properties of aneurally cultured muscle from patients with myotonic muscular atrophy (1983) (23)
- Chaperone‐mediated autophagy components are upregulated in sporadic inclusion‐body myositis muscle fibres (2013) (23)
- Catecholamines and indoleamines in patients with Duchenne muscular dystrophy. (1972) (22)
- In vitro studies of skeletal muscle membranes characterization of a phosphorylated intermediate of sarcolemmal (Na+ + K+)ATPase (1976) (22)
- DEPENDENCY OF HISTOCHEMICAL PHOSPHORYLASE STAINING ON AMOUNT OF CELLULAR GLYCOGEN (1972) (22)
- Serotonin-induced muscle weakness. (1974) (22)
- Serum creatine kinase BB and MM concentrations determined by radioimmunoassay in neuromuscular disorders (1980) (22)
- Strong immunoreactivity of α1 co-localizes with β-amyloid protein and ubiquitin in vacuolated muscle fibers of inclusion-body myositis (2004) (22)
- Abnormalities of aneural and innervated cultured muscle fibers from patients with myotonic atrophy (dystrophy). (1990) (21)
- A skeletal muscle disorder associated with intermittent symptoms and a possible defect of lipid metabolism. (1969) (21)
- SPLENIC AND TOTAL‐BODY IRRADIATION TREATMENT OF MY ASTHENIA GRAVIS (1981) (21)
- SUBCELLULAR ANALYSIS OF THE MOLECULAR FORMS OF ACETYLCHOLINESTERASE IN RAT SKELETAL MUSCLE (1978) (21)
- Nature of amyloid deposits in hypernephroma. Immunocytochemical studies in 2 cases associated with amyloid polyneuropathy. (1984) (21)
- Strong immunoreactivity of alpha 1-antichymotrypsin co-localizes with beta-amyloid protein and ubiquitin in vacuolated muscle fibers of inclusion-body myositis. (1993) (20)
- Erythrocyte survival in Duchenne muscular dystrophy (1977) (20)
- Adenosine Triphosphatase of Sarcoplasmic Reticulum Triads and Sarcolemma identified histochemically (1963) (20)
- Thyrotoxic periodic paralysis. (1969) (19)
- A critique of the "myopathic" electromyogram. (1970) (19)
- Cyclin-dependent kinase 5 colocalizes with phosphorylated tau in human inclusion-body myositis paired-helical filaments and may play a role in tau phosphorylation (2000) (19)
- CSF viral antibodies. Evaluation in amyotrophic lateral sclerosis and late-onset postpoliomyelitis progressive muscular atrophy. (1979) (19)
- Cystatin C colocalizes with amyloid-beta and coimmunoprecipitates with amyloid-beta precursor protein in sporadic inclusion-body myositis muscles. (2003) (19)
- Does overexpression of betaAPP in aging muscle have a pathogenic role and a relevance to Alzheimer's disease? Clues from inclusion body myositis, cultured human muscle, and transgenic mice. (1998) (19)
- CYTOLOGICAL LOCALIZATION OF GLYCOGEN IN CULTURED SKELETAL MUSCLE (1961) (19)
- ELECTRICAL PROPERTIES OF HUMAN MUSCLE CULTURED IN MONOLAYER ANEURALLY AND CO-CULTURED WITH FETAL RAT SPINAL CORD (1990) (19)
- Remote effects of focal cancer on the neuromuscular system. (1976) (19)
- Analogs of thyrotropin-releasing hormone: hypotheses relating receptor binding to net excitation of spinal lower motor neurons. (1986) (19)
- Letters to the editor: A technique of fiber selection from human muscle tissue cultures for histochemical-electronmicroscopic studies. (1975) (19)
- POLYINOSINIC-POLYCYTIDYLIC ACID TREATMENT OF NEUROPATHY (1978) (19)
- Expression of muscle-type phosphorylase in innervated and aneural cultured muscle of patients with myophosphorylase deficiency. (1993) (19)
- Expression of β-Amyloid Precursor Protein Gene Is Developmentally Regulated in Human Muscle Fibers in Vivo and in Vitro (1994) (19)
- beta-Amyloid protein immunoreactivity in muscle of patients with inclusion-body myositis. (1992) (19)
- Expression of Nogo‐A in human muscle fibers is not specific for amyotrophic lateral sclerosis (2007) (18)
- Effects of experimental spinal cord transection on substance P receptors: A quantitative autoradiography study (1990) (18)
- Fibroblast growth factor, epidermal growth factor and insulin exert a neuronal-like influence on acetylcholine receptors in aneurally cultured human muscle (1985) (18)
- LIGHT‐CORED DENSE PARTICLES IN MITOCHONDRIA OF A PATIENT WITH SKELETAL MUSCLE AND MYOCARDIAL DISEASE (1976) (18)
- Activation of the Unfolded Protein Response in Sporadic Inclusion-Body Myositis but Not in Hereditary GNE Inclusion-Body Myopathy (2015) (18)
- Phosphate and parathyroid disorders associated with the syndrome of amyotrophic lateral sclerosis. (1982) (18)
- CSF from amyotrophic lateral sclerosis patients applied to motor neurons in culture fails to alter neuron‐specific enolase (1981) (18)
- Calcium metabolism in amyotrophic lateral sclerosis. (1977) (18)
- Acetylcholine receptors of aneurally cultured human and animal muscle (1977) (18)
- The Oxidation of β-Hydroxybutyric Acid by Small Quantities of Type-pure Red and White Skeletal Muscle (1971) (18)
- Newest pathogenetic considerations in inclusion-body myositis: Possible role amyloid-β, cholesterol, relation to aging and to alzheimer’s disease (2002) (17)
- MB-creatine phosphokinase isoenzyme elevation not diagnostic of myocardial infarction. (1977) (17)
- Dagen des oordeels. Pathokinetic mechanisms and molecular messengers (a dramatic view). (1979) (17)
- CHEMOCYTOLOGY OF STRIATED ANNULETS AND SARCOPLASMIC MASSES IN MYOTONIC DYSTROPHY (1962) (17)
- Myostatin and its precursor protein are increased in the skeletal muscle of patients with Type-II muscle fibre atrophy. (2008) (16)
- Transthyretin Val122Ile, accumulated Aβ, and inclusion-body myositis aspects in cultured muscle (2003) (16)
- Adenylate cyclase system of human skeletal muscle (1978) (16)
- Correlation of motor-unit behavior with histochemical myofiber type in humans by open-biopsy electromyography. (1973) (16)
- Serum immunoglobulin and complement (C3) levels (1973) (16)
- THE ELECTRON PROBE IN ENZYME HISTOCHEMISTRY (1968) (16)
- Myostatin precursor protein is increased and associates with amyloid‐β precursor protein in inclusion‐body myositis culture model (2007) (16)
- Activation of the γ-secretase complex and presence of γ-secretase-activating protein may contribute to Aβ42 production in sporadic inclusion-body myositis muscle fibers (2012) (15)
- The effect of pharmacologic acetylcholine receptor on fibrillation and myotonia in rat skeletal muscle. (1978) (15)
- Direct Correlation of Physiological and Histochemical Characteristics in Motor Units of Cat Triceps Surae Muscle (1973) (15)
- MYASTHENIA GRAVIS: RELATIONSHIP BETWEEN SERUM FACTOR BLOCKING ACETYLCHOLINE RECEPTORS AND ANTI-STRIATED-MUSCLE ANTIBODY (1975) (15)
- Elevations of hemopexin levels in neuromuscular disease. (1978) (15)
- Neuromuscular blockade with anti‐axoplasmic antibodies (1977) (15)
- AbetaPP-overexpression and proteasome inhibition increase alphaB-crystallin in cultured human muscle: relevance to inclusion-body myositis. (2006) (14)
- Protein abnormalities in neuromuscular diseases--Part 2. (1966) (14)
- Sporadic inclusion-body myositis: a proposed key pathogenetic role of the abnormalities of the ubiquitin-proteasome system, and protein misfolding and aggregation. (2005) (14)
- Severe occult juvenile myasthenia gravis responsive to long-term corticosteroid therapy. (1968) (14)
- Antibodies to nucleic acids in myasthenia gravis. (1976) (14)
- Letter: Leukaemia and lower-motor-neuron disease. (1974) (14)
- Metastatic Leydig cell tumor with sarcomatoid differentiation. (1999) (14)
- Morphologic and immunologic studies in experimental autoimmune myasthenia gravis and myasthenia gravis (1977) (14)
- The essentiality of histo‐ and cytochemical studies of skeletal muscle in the investigation of neuromuscular disease (1962) (14)
- Novel demonstration of conformationally modified tau in sporadic inclusion-body myositis muscle fibers (2011) (14)
- The effects of single‐dose alternate‐day prednisone therapy on the immunological status of patients with neuromuscular diseases (1978) (14)
- Focal lesions of muscle in peripheral vascular disease (1977) (14)
- Use of phenazine methosulfate in enzyme histochemistry of human muscle biopsies (1966) (13)
- Sodium phenylbutyrate reverses lysosomal dysfunction and decreases amyloid-β42 in an in vitro-model of inclusion-body myositis (2014) (13)
- Stokes-Adams syndrome and atrial arrhythmias as the presenting symptoms of myotonic dystrophy, with response to electrocardioversion. (1966) (12)
- Dysferlin is a newly identified binding partner of AβPP and it co-aggregates with amyloid-β42 within sporadic inclusion-body myositis (s-IBM) muscle fibers (2013) (12)
- Unicorns, dragons, polymyositis, and other mythical beasts (2004) (12)
- Effects of electrical stimulation and tetrodotoxin paralysis on expression of muscle-specific isozymes of four enzymes in aneurally cultured embryonic rat muscle (1987) (12)
- Electrophysiologic and histochemical observations in five patients with muscle phosphorylase deficiency (MPD). (1977) (12)
- Myotonia--a different point of view. (1971) (12)
- Effect of heme administration on hemopexin metabolism in the rhesus monkey. (1982) (12)
- Central Core Disease: A Myofibrillary and Mitochondrial Abnormality of Muscle: Combined Clinical Staff Conference of the National Institutes of Health (1962) (12)
- DETECTION OF ATYPICAL CHOLINESTERASE BY ELECTROPHORESIS. (1965) (12)
- Histochemical Differentiation of Motor Neurones and Interneurones in the Anterior Horn of the Cat Spinal Cord (1970) (12)
- Expression of beta-amyloid precursor protein gene is developmentally regulated in human muscle fibers in vivo and in vitro. (1994) (12)
- 14 – Total Body Irradiation in the Treatment of Intractable Polymyositis and Dermatomyositis (1988) (11)
- Insulin Enhances Development of Functional Voltage‐Dependent Ca2+ Channels in Aneurally Cultured Human Muscle (1987) (11)
- Extrajunctional acetylcholine receptors on myogenously de=innervated muscle fibers. (1976) (11)
- Calf muscle hypertrophy, complex repetitive discharges and spinal stenosis. (1993) (11)
- Blood-to-cerebrospinal fluid barrier for cyclic adenosine monophosphate in man. (1977) (11)
- A search for antibodies to neuronal nuclei in the serum of patients with myasthenia gravis (1974) (10)
- Therapeutic Trial in Amyotrophic Lateral Sclerosis: Lack of Benefit With Pancreatic Extract and DL-Alpha Tocopherol in 12 Patients (1969) (10)
- Effect of lactate infusions on patients with myasthenia gravis (1974) (10)
- Autosomal dominant syndrome of lipid neuromyopathy with normal carnitine (1985) (10)
- Amyotrophic lateral sclerosis: metabolism of central monoamines and treatment with L-dopa. (1971) (10)
- Paralysis of Innervated Cultured Human Muscle Fibers Affects Enzymes Differentially (1990) (10)
- Extracellular Cyclic Nucleotide Metabolism in the Human Central Nervous System (1980) (10)
- Myopathic changes produced by local trauma. (1969) (10)
- Autoradiographic visualization of beta-adrenergic receptors in normal and denervated skeletal muscle. (1979) (10)
- Effect of acetazolamide on myotonia. (1977) (10)
- Therapeutic trial in amyotrophic lateral sclerosis. (1969) (10)
- Myosin isoenzymes in cultured human muscle. (1982) (10)
- High‐dose TRH Treatment of Neuromuscular Diseases: Summary of Mechanisms and Critique of Clinical Studies a (1989) (9)
- Leukoencephalopathy in oculocraniosomatic neuromuscular disease with ragged-red fibers. Mitochondrial abnormalities demonstrated by computerized tomography. (1979) (9)
- Long-term plasmapheresis therapy is effective and safe in children with chronic relapsing dysimmune polyneuropathy. (1990) (9)
- Alpha 1‐antichymotrypsin is strongly immunolocalized at normal human and rat neuromuscular junctions (1994) (9)
- Expression of muscle-specific isozymes of phosphorylase and creatine kinase in human muscle fibers cultured aneurally in serum-free, hormonally/chemically enriched medium (1990) (9)
- Cultured inclusion-body myositis muscle fibers do not accumulate β-amyloid precursor protein and can be innervated (1999) (9)
- Lysosomal abnormalities in cultured schwann cells from a patient with peripheral neuropathy and continuous muscle fiber activity (1981) (9)
- Kinetic analysis of thyrotropin-releasing hormone binding in the central nervous system: evidence for receptor desensitization (1987) (9)
- Lack of Usefulness of DN‐1417 for Characterization of a CNS Receptor for Thyrotropin‐Releasing Hormone (1987) (9)
- Cyclic nucleotide metabolism in neuromuscular disease. (1976) (9)
- Subtypes of histochemical type I muscle fibers (1976) (9)
- Tropomodulin is highly concentrated at the postsynaptic domain of human and rat neuromuscular junctions. (1993) (8)
- Histochemical Patterns in Single Peripheral Nerve Fibers: A Rapid Method for Identifying the Schwann Cell and Axonal Cytoplasm (1968) (8)
- Heredopathia atactica polyneuritiformis (Refsum's Disease): a second trial of dietary therapy in two patients. (1971) (8)
- Accumulation of CK-MM is impaired in innervated and contracting cultured muscle fibers of Duchenne muscular dystrophy patients. (1987) (8)
- Protein abnormalities in neuromuscular diseases. I. (1966) (8)
- Adrenomyeloneuropathy: increased accumulation of very long chain fatty acid in cultured skeletal muscle. (1980) (8)
- Muscle lesions in myasthenia gravis. Discussion. (1966) (8)
- Poly ICLC in the treatment of postinfectious demyelinating encephalomyelitis. (1981) (8)
- Different degradation rates of junctional and extrajunctional acetylcholine receptors of human muscle cultured in monolayer and innervated by fetal rat spinal cord neurons (1992) (7)
- Depletion of serum hemopexin in fulminant rhabdomyolysis. Evidence for an interaction of hemopexin with myoglobin-derived heme. (1978) (7)
- Drugs blocking the muscle-damaging effects of 5-HT and noradrenaline in aorta-ligatured rats (1975) (7)
- An improved method of preparing Schmidt-Ruppin Rous sarcoma virus for brain tumor induction in mammals. (1970) (7)
- Overlooked Avian Oncornavirus in Cultured Muscle--Functionally Significant? (1976) (7)
- High-dose TRH treatment of neuromuscular diseases: summary of mechanisms and critique of clinical studies. Summary of section IX. (1989) (6)
- Muscle Aging, Inclusion-Body Myositis and Myopathies: Askanas/Muscle Aging, Inclusion-Body Myositis and Myopathies (2012) (6)
- "Myopathic EMG"--nonesuch animal. (1973) (6)
- Intravenous immunoglobulin G is remarkably beneficial in chronic immune dysschwannian/dysneuronal polyneuropathy, diabetes-2 neuropathy, and potentially in severe acute respiratory syndrome. (2003) (6)
- Does Overexpression of b APP in Aging Muscle Have a Pathogenic Role and a Relevance to Alzheimer’s Disease? Clues from Inclusion Body Myositis, Cultured Human Muscle, and Transgenic Mice (1998) (6)
- Decreased spinal cord cGMP in murine (wobbler) spontaneous lower motor neuron degeneration. (1978) (6)
- Cerebrospinal fluid norepinephrine and free γ-aminobutyric acid in amyotrophic lateral sclerosis (1980) (6)
- Adrenomyeloneuropathy (1977) (6)
- 4 Genetically Determined Myopathies (1965) (6)
- Classification of neuromuscular disorders. (1971) (6)
- Novel cytoplasmic immunolocalization of RNA polymerase II in inclusion-body myositis muscle (2001) (6)
- Unicorns, dragons, polymyositis, and other mythical beasts. Authors' reply (2004) (5)
- Distinct histochemical subtypes of type I fibers of human skeletal muscle. (1975) (5)
- Strong immunoreactivity of beta-amyloid precursor protein, including the beta-amyloid protein sequence, at human neuromuscular junctions. (1992) (5)
- Role of immunoglobulin light chains in the pathogenesis of amyloid polyneuropathy associated with occult plasma-cell dyscrasia. (1979) (5)
- Adverse interaction between corticosteroid hormones and anticholinesterase drugs. (1973) (5)
- Pathogenesis of Sporadic Inclusion‐Body Myositis: Role of Aging and Muscle‐Fiber Degeneration, and Accumulation of the Same Proteins as in Alzheimer and Parkinson Brains (2011) (5)
- Cyclic nucleotide metabolism in neurological disease. (1976) (4)
- Phthalazinol, thrombocytopenia, and amyotrophic lateral sclerosis. (1980) (4)
- NEURONAL RNA METABOLISM IN INFANTILE SPINAL MUSCULAR ATROPHY (WERDNIG‐HOFFMANN'S DISEASE) STUDIED BY RADIOAUTOGRAPHY: A NEW TECHNIC IX THE INVESTIGATION OF NEUROLOGICAL DISEASE (1967) (4)
- Biochemical and morphological effects of 20,25-diazacholesterol on cultured muscle cells. (1982) (4)
- Quantification of acute phase reactants after muscle biopsy. (1982) (4)
- Adult-onset acid maltase deficiency. Electrophysiological properties of aneurally cultured muscle. (1984) (4)
- Prolonged response to edrophonium in myasthenia gravis. (1975) (4)
- Third International Congress of Histochemistry and Cytochemistry (1968) (4)
- Diagnostic histochemistry and clinical-pathological testings as molecular pathways to pathogenesis and treatment of the ageing neuromuscular system: a personal view. (2015) (4)
- The influence of muscle contractile activity versus neural factors on morphologic properties of innervated cultured human muscle (1992) (4)
- T.P.2 01 Longer-term (>3 months) IVIG treatment to optimize clinical benefit and cellular protection usually requires an individualized adjustable schedule – not fixed regimentation (2006) (3)
- Polyneuropathy in type 2 diabetes mellitus (2001) (3)
- The skeletal muscle binding site of anti striated muscle antibody an ultrastructural study using peroxidase conjugated antibody (1973) (3)
- Acetazolamide Treatment of Hypokalemic Periodic Paralysis (2020) (3)
- Neoplasia in patients with amyotrophic lateral sclerosis. (1964) (3)
- Effect of prednisone therapy on cerebrospinal fluid immunoglobulins and lymphocytes in chronic idiopathic relapsing polyneuropathy (CIRPN) and other neuromuscular disorders. (1977) (3)
- New organotypic model to culture the entire fetal rat spinal cord (1993) (3)
- G.P.17.07 Fever-responsive dysschwannian neuropathy (FRDN): Interferon-alpha 2a (Iα) treatment has produced remarkable recovery from total quadriplegia, the benefit now persisting 4years beyond the 14years of therapy (2007) (3)
- Letter: Acupuncture myopathy? (Remembrance of things passed). (1974) (3)
- G.P.17.06 Late-onset rod myopathy with monoclonal immunoglobulin can be treatable with IVIG (2007) (3)
- Vascular deposits of immunoglobulin and complement in inflammatory myopathy. (1971) (3)
- Mechanisms of muscle injury in idiopathic inflammatory myopathy. (1973) (3)
- Oral immunosuppression for multiple sclerosis (1992) (3)
- Autoradiographic localization of substance P receptors in rat spinal cord: effects of experimental spinal transection. (1987) (3)
- Novel identification of aggresomes in sporadic inclusion-body myositis (s-IBM) muscle fibers suggests that inhibition of 26S/20S proteasome and misfolded proteins play a pathogenic role (2003) (3)
- G.P.2 01 Alpha-synuclein and parkin are novel proteins accumulated in ragged red fibers (2006) (3)
- Trophic factors for cultured lower motor neurons. (1991) (3)
- Alternate-dy prednisone in a patient with myasthenia gravis. (1970) (3)
- Cells of neural crest origin as possible models to investigate thyrotropin releasing hormone action in the central nervous system (1985) (2)
- Leptomeres in cultured human muscle (1978) (2)
- Histochemical classification of anterior horn neurons. (1970) (2)
- Measurement of metabolic activities in small samples of muscle. (1970) (2)
- A sequential study of denervation - ultrastructural immunoperoxidase localization of alpha-bungarotoxin. (1975) (2)
- Abnormality of cultured muscle and Schwann's cells in familial lipid neuromyopathy. Muscle corrected by neural influence. (1984) (2)
- Analysis of eye movements in members of a family with late-onset, dominantly inherited cerebellar ataxia. (1975) (2)
- Chick muscle in tissue culture: The ubiquity of viral infection (1975) (2)
- Comprar Muscle Aging, Inclusion-Body Myositis And Myopathies | Valerie Askanas | 9781405196468 | Wiley (2012) (2)
- Idiopathic inflammatory myopathy. Failure to detect hepatitis B antigen in serum and muscle. (1973) (2)
- Multiplicity of muscle changes postulated from motoneuron abnormalities. (1972) (2)
- G.P.4.14 In ALS, viral-dysmetabolic mechanisms acting via neuronal-nurturing cells (NNCs) could portend replacement therapy and should be sought by multi-tissue screening for rev-transcriptase (RT) and viral tracks (2008) (2)
- Prednisone-responsive limb-girdle syndrome: a special disorder? (1987) (2)
- G.O.6 “Pseudo-Lupus”, benign neutropenia, and other probably non-worrisome blood-component changes due to IVIG treatment (2006) (2)
- Dihydropyridine‐sensitive Ca2+ channel in aneurally cultured human muscles Relationship between high‐affinity binding site and inhibition of calcium uptake (1988) (2)
- Technetium-99m diphosphonate uptake in skeletal muscle: a quantitative index of acute damage. Scientific report (1975) (2)
- A MODEL OF DEFECTS IN MUSCLE GLYCOGENOLYSIS/GLYCOLYSIS (GG/Gly): 19 (1977) (2)
- THE MANY CAUSES OF "IDIOPATHIC " SCOLIOSIS (1975) (1)
- Proteasome abnormalities participate in the pathogenesis of sporadic inclusion body myositis (s-IBM) (2004) (1)
- Workshop 18: Inclusion‐Body Myositis: Newest Advances (1994) (1)
- Aging of the Human Neuromuscular System: Clinical Considerations (2011) (1)
- Muscle biopsy uses and limitations. (1967) (1)
- Ponderous-purse disease. (1978) (1)
- New histochemical technique for the demonstration of adenyl cyclase (AC) in nervous tissue and muscle. (1976) (1)
- G.O.2 In sporadic inclusion-body myositis (s-IBM) muscle fibers, Parkinson-disease-associated DJ-1 is oxidized and might play a novel pathogenic role (2007) (1)
- Short Communication Light and Electron Microscopic Localization of ,B-amyloid Protein in Muscle Biopsies of Patients with Inclusion-body Myositis (2007) (1)
- G.P.13.15 In sporadic inclusion-body myositis muscle-fiber (s-IBM) cytoplasm, cytochrome C aggregates with α-synuclein and amyloid-β precursor protein (AβPP), but does not activate caspase-3 (2007) (1)
- PAPERS READ BY TITLE Morphologic Changes of Peripheral Muscle in Progressive Disabilities of Ocular Motility (1970) (1)
- HTLV-I-associated myelopathy. (1990) (1)
- RNA metabolism in relation to amyotrophic lateral sclerosis. (1991) (1)
- Novel expression of dysferlin in recently denervated and apoptoid human muscle fibers (2003) (1)
- Amyloid polyneuropathy--a plasma cell dyscrasia with abnormal circulating immunoglobulins. (1976) (1)
- Autoradiographic Visualization of $-Adrenergic Receptors in Normal and Denervated Skeletal Muscle (1979) (1)
- HIGH EXCITABILITY AND REMAINED SLOW CALCIUM REPOLARIZATION COMPONENTS OF ACTION POTENTIALS IN CULTURED HUMAN PARAMYOTONIA CONGENITA MUSCLE CELLS (1990) (1)
- Antibodies to L-type calcium channels in amyotrophic lateral sclerosis. (1993) (1)
- Tissue nonspecificity of antinuclear antibodies in myasthenia gravis (1974) (1)
- Histochemistry of Motoneurons Innervating Slow and Fast Motor Units1 (1973) (1)
- Aging of the Human Neuromuscular System: Pathological Aspects (2011) (1)
- G.P.2 02 In cultured human muscle fibers (CHMFs) amyloid-β precursor protein (AβPP) and proteasome inhibition increase αB-crystallin (αBC). Relevance to sporadic inclusion-body myositis (s-IBM) (2006) (1)
- Axonal Protein Flow in Experimental Neuropathies (1970) (1)
- Correlated virological and ultrastructural study of Schmidt-Ruppin Rous sarcoma virus-induced dog brain tumors. (1971) (1)
- Molecular pathogenesis and treatment of immunemediated neuropathies (2007) (1)
- 7 Muscle Biopsy (1965) (1)
- Toxic role of long chain fatty acids in muscle carnitine deficiency and other long chain fatty acid endodissolutions dietary long chain fatty acid restriction associated with dramatic long term improvement (1986) (1)
- The essentiality of histo- and cytochemical studies of skeletal muscle in the investigation of neuromuscular disease (2011) (1)
- Investigative approach to the muscular dystrophies. (1977) (1)
- Myopathies associated with systemic diseases. (1971) (1)
- Current Concepts of Myopathies (1965) (1)
- The effects of high-single-dose alternate-day prednisone on the immunological status of patients with neuromuscular diseases. (1975) (1)
- Limb-girdle muscular dystrophy. (1971) (1)
- G.P.3.16 In skeletal muscle of patients with type-II fiber atrophy, myostatin (MSTN) and myostatin precursor protein (MSTN-PP) are both increased (2007) (1)
- ABNORMALITIES OF THE SERINE PROTEASES CHYMO-TRYPSIN (CT) AND CATHEPSIN G AND THEIR INHIBITOR (SERPIN) α1,-ANTI-CHYMOTRYPSIN (α1,-ACT) IN MUSCLE BIOPSIES OF INCLUSION-BODY MYOSITIS (IBM) (1993) (1)
- DISCUSSION (1966) (1)
- Sporadic inclusion-body myositis as a conformational disorder: Novel role of misfolded proteins and proteasome inhibition in sporadic inclusion-body myositis pathogenesis (2004) (1)
- Commentary (1998) (0)
- Histochemical patterns in single peripheral nerve fibers. (1968) (0)
- Alzheimer disease (AD) and inclusion-body myositis (IBM) ; Do the remarkable cytochemical similarities indicate similarities of molecular pathogenesis? (2000) (0)
- DISCUSSION (1976) (0)
- Localization of 99m sub T c Diphosphonate in Acutely Injured Muscle: Relationship to Muscle Calcium Deposition. (1976) (0)
- I-1. Diagnosis and long-term treatment of “untreatable” neuromuscular patients, an update. (2009) (0)
- Nature of Amyloid Deposits in Hypernephroma Immunocytochemical Studies Amyloid Polyneuropathy Immu-in 2 Cases Associated With (2007) (0)
- Pathologic Diagnostic Criteria of Sporadic Inclusion‐Bodyc Myositis and Hereditary Inclusion‐Body Myopathy Muscle Biopsies (2011) (0)
- Wartenberg wheel-and-flair reaction--a prickly problem. (1992) (0)
- [Neuronal RNA metabolism in infantile spinal muscular atrophy (Werdnig-Hoffmann disease), studied with the use of radioautography: a new technic in the examination of neurological diseases]. (1967) (0)
- A Further Fond Farewell to Shy and Drager (1997) (0)
- Remarkable recoveryofasteroid-responsi ve recurrent polyneuropathy (1970) (0)
- Letter: The many causes of "idiopathic" scoliosis. (1975) (0)
- MYOPATHIES ASSOCIATED WITH OTHER DISEASES. (1965) (0)
- Proteasome inhibition induces aggresome formation in a culture model of inclusion-body myositis (IBM) (2005) (0)
- Molecular mechanisms of treatment of dysimmune and visal neuromuscolar diseases (1992) (0)
- Acid maltase deficiency: reincarnation in cultured muscle fibers of the typical morphological and biochemical defects. (1976) (0)
- Myotonic lidlaginhypokalaemic periodic paralysis (1967) (0)
- [New theory on the pathogenesis of Duchenne's pseudo-hypertrophic muscular dystrophy]. (1971) (0)
- Abolish boxing. (1982) (0)
- Novel pathogenic aspects of myostatin and therapeutic potential in human neuromuscular diseases (2007) (0)
- Aging of the Human Neuromuscular System: Patient Vignettes (2011) (0)
- More on diagnosis of amyloidosis. (1983) (0)
- Localization of /sup 99m/Tc diphosphonate in acutely injured muscle: relationship to muscle calcium deposition. Scientific report (1976) (0)
- Infiltration and tendon rupture (2001) (0)
- PROGRESSIVE MUSCULAR ATROPHY AUTOANTIBODIES BIND TO LOWER MOTORNEURONS (1996) (0)
- Focal lesions of muscle in peripheral vascular disease: their comparison with Duchenne muscular dystrophy. (1976) (0)
- SERA OF PATIENTS WITH LOWER MOTORNEURON (LMN) DEGENERATION BIND TO SURFACE PROTEOGLYCAN OF LMN (1993) (0)
- Molecular pathogenesis and prospects of treatment of inclusion-body myositis (2007) (0)
- GENETICALLY DETERMINES MYOPATHIES. (1965) (0)
- Down-regulation of thyrotropin-releasing hormone (TRH) receptors in spinal cord after transection as revealed by quantitative autoradiography (2004) (0)
- Disorders of the immunoglobulin A system in hereditary sensory neuropathy. (1973) (0)
- Basic concepts in the understanding of epilepsy. (1954) (0)
- A CLINICAL APPROACH TO THE MYOPATHIES. (1965) (0)
- Hyperparathyroid Neuromuscular Disease. (1973) (0)
- PHENOTYPIC MOLECULAR SIMILARITIES BETWEEN INCLUSION-BODY MYOSITIS (IBM) MUSCLE AND ALZHEIMER AND PRION-DISEASE BRAIN (1996) (0)
- Role of endoplasmic reticulum stress in muscle diseases (2007) (0)
- Cerebrospinal fluid oligocional proteins in amyotrophic lateral sclerosis. (1979) (0)
- 2 Sporadic inclusion-body myositis: A degenerative muscle disease 3 associated with aging, impaired muscle protein homeostasis and (2014) (0)
- XII CONGRESS OF MEDITERRANEAN SOCIETY OF MYOLOGY Naples, Italy - May 18-20, 2015 Program (Summary) (2015) (0)
- DISCUSSION (1976) (0)
- THE ELECTRON PROBE IN ENZYME HISTOCHEMISTRY (1968) (0)
- Isoenzymes of creatine phosphokinase determined by acrylamide gel electrophoresis. (1968) (0)
- Age-dependent requirements of cultured spinal cord neurons. (1988) (0)
- FOCAL LOSS OF CROSS-STRIATIONS (FLCS) IN FOUR SIBLINGS: AN AUTOSOMAL-RECESSIVE GENETIC DISORDER, WITH FATALITY FOLLOWING SCOLIOSIS SURGERY (1996) (0)
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